Results 41 to 50 of about 1,204 (194)
A 32‐Year‐Old Man With an Cardiomyopathy
ABSTRACT Scleredema is a sclerosing dermatosis of unknown etiology, characterized by non‐punctate, weakly infiltrated skin thickening and swelling, which can lead to the development of cardiomyopathy. Scleredema‐associated cardiomyopathy is at present poorly understood.
Yuting Zou, Shan Li, Tong Chen, Yi Li
wiley +1 more source
Macroglobulinemia de Waldenströn: comunicación de un caso
La macroglobulinemia de Waldenström (MW) es una rara neoplasia hematológica, caracterizada por la proliferación linfoplasmocitaria, con producción monoclonal de inmunoglobulina M (IgM) e infiltración medular.
Franco Romaní +3 more
doaj
Chronic inflammatory demyelinating polyneuropathy is an autoimmune disorder causing demyelination, leading to distal weakness, sensory loss, and autonomic dysfunction. Immune activation triggers macrophage‐mediated myelin damage and conduction failure.
Ayesha Khan +11 more
wiley +1 more source
Perfil proteinogramico en sueros de pollos [PDF]
El presente trabajo de investigación, nos permitirá conocer los valores normales de proteínas séricas en los pollos de engorde de crianza comercial. El determinar los valores normales de las proteínas que constituyen el suero de las aves, en el caso ...
Muñante Acevedo, Luis Gustavo
core +1 more source
Compresión del plexo lumbosacro por plasmocitoma: mieloma múltiple de cadenas ligeras tipo lambda
Se presenta el caso de una mujer de 51 años que desarrolló paraparesia y una masa abdominal palpable más pérdida de peso en el lapso de cuatro meses. La masa destruía la 5ª vértebra lumbar y se extendía a los tejidos blandos adyacentes. En suero se halló
Oscar G. Pamo +2 more
doaj
Integrating Gaucher disease (GD) into mainstream hematological curriculum training
HemaSphere, Volume 10, Issue 10, October 2026.
Colm Bradley +3 more
wiley +1 more source
Low Dose Pegylated Interferon Alpha as a First‐Line Treatment for Necrobiotic Xanthogranuloma
ABSTRACT Necrobiotic xanthogranuloma (NXG) is a rare, progressive granulomatous disorder frequently associated with monoclonal gammopathy, particularly monoclonal gammopathy of undetermined significance (MGUS). It typically presents with indurated to ulcerative yellowish plaques or nodules, often with ocular involvement.
Ishana Dixit +2 more
wiley +1 more source
Neurological Peculiarities of POEMS Syndrome: Experience From a Brazilian University Center
ABSTRACT Aim Polyneuropathy, organomegaly, endocrinopathy, monoclonal protein, and skin changes (POEMS) syndrome is a rare paraneoplastic syndrome associated with significant neurologic morbidity. Better understanding of the manifestations of this disease is crucial to early diagnosis and improvement of prognosis.
Renan Fabri Rosenstein +5 more
wiley +1 more source
Objective: Sjögren disease (SjD) is a systemic autoimmune disease characterized by increased risk of B-cell non-Hodgkin lymphoma. Although cryoglobulinemia and serum monoclonal component (MC) are well-recognized paraproteinemias in SjD, no large-scale ...
Cipriani P. +19 more
core +1 more source
ABSTRACT Background and Aims Monoclonal gammopathy of undetermined significance (MGUS) occurs in some patients with chronic inflammatory demyelinating polyneuropathy (CIDP), but its impact on clinical phenotype and treatment response remains unclear.
R. van Veen +16 more
wiley +1 more source

