Results 21 to 30 of about 1,068 (155)
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma.
Danielle Machado da Silva +4 more
doaj +1 more source
Recurrence of membranoproliferative glomerulonephritis (MPGN) is seen in 1965% cases of postrenal transplant resulting in graft loss in up to 35-50% of cases.
Umesh Lingaraj +5 more
doaj +1 more source
Diffuse plane normolipemic xanthomatosis (DPNX) is a rare, non-inherited disease that is often associated with systemic diseases, mainly malignant hematological (especially multiple myeloma) or lymph proliferative disorders.
Aristóteles Rosmaninho +4 more
doaj +1 more source
ESCLEREDEMA DE BUSCHKE – A propósito de um caso clínico
RESUMO: O Escleredema de Buschke (EB) é uma doença rara do tecido conjuntivo, de etiologia desconhecida, caracterizada por espessamento e endurecimento da pele, geralmente localizado nas regiões proximais e posteriores do tronco e pescoço.
Jorge Henriques +3 more
doaj +1 more source
Clinical observation of monoclonal fibrillary glomerulonephritis
Monoclonal gammopathy of renal significance is a condition caused by the proliferation of a clone of B-lymphocytes or plasma cells that does not reach the criteria required for the initiation of treatment for oncohematological indications, but is ...
T. A. Garkusha +2 more
doaj +1 more source
La nefropatía de las gammapatías monoclonales es debida, principalmente, al depósito de cadenas ligeras. Las enfermedades renales paraproteinémicas son lesiones asociadas con depósitos de inmunoglobulinas intactas o fragmentos de inmunoglobulinas ...
Jorge de Jesús Cantillo +2 more
doaj +1 more source
Bone Marrow Pathology in Cold Agglutinin‐Mediated Autoimmune Hemolytic Anemia: A Study of 56 Cases
ABSTRACT Cold agglutinin disease (CAD) is a rare form of autoimmune hemolytic anemia (AIHA). CAD occurs in the context of a small clonal B‐cell lymphoproliferation restricted to blood and/or bone marrow (BM), without overt or extramedullary lymphoma. The WHO‐HAEM5 introduced a description of the CAD‐associated lymphoproliferative disorder (CAD‐LPD) in ...
Anne‐Marie L. Becking +6 more
wiley +1 more source
El compromiso renal por cadenas ligeras es frecuente en el contexto de las gammapatías monoclonales, afectando los glomérulos o los túbulos renales y siendo el mieloma múltiple la causa más común; puede desarrollarse posterior a un trasplante renal por ...
John Fredy Nieto +7 more
doaj +1 more source
Chronic inflammatory demyelinating polyneuropathy is an autoimmune disorder causing demyelination, leading to distal weakness, sensory loss, and autonomic dysfunction. Immune activation triggers macrophage‐mediated myelin damage and conduction failure.
Ayesha Khan +11 more
wiley +1 more source
Low Dose Pegylated Interferon Alpha as a First‐Line Treatment for Necrobiotic Xanthogranuloma
ABSTRACT Necrobiotic xanthogranuloma (NXG) is a rare, progressive granulomatous disorder frequently associated with monoclonal gammopathy, particularly monoclonal gammopathy of undetermined significance (MGUS). It typically presents with indurated to ulcerative yellowish plaques or nodules, often with ocular involvement.
Ishana Dixit +2 more
wiley +1 more source

