Results 21 to 30 of about 1,204 (194)

LINFOMA LINFOPLASMACÍTICO SECRETOR DE IGG/KAPPA EVOLUINDO COM ANEMIA HEMOLÍTICA E INSUFICIÊNCIA RENAL

open access: yesHematology, Transfusion and Cell Therapy, 2021
Relato de caso: Paciente, sexo feminino, 43 anos, sem comorbidades, admitida na clínica cirúrgica do Hospital Jean Bitar (HJB) devido quadro de massa abdominal hipogástrica.
BLSA Lima   +9 more
doaj   +1 more source

Necrobiotic xanthogranuloma associated with smoldering multiple myeloma: satisfactory response to cyclophosphamide, dexamethasone, and thalidomide [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2019
: Necrobiotic xanthogranuloma is a rare chronic condition, belonging to the group C non-Langerhans cell histiocytoses, which is relevant due to the possibility of extracutaneous involvement and association with systemic diseases, particularly hematologic
Renan Bernardes de Mello   +1 more
doaj   +1 more source

Xantoma plano difuso normolipêmico idiopático com hiperesplenismo Diffuse plane idiopathic normolipemic xanthoma with hiperesplenism

open access: yesAnais Brasileiros de Dermatologia, 2010
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma.
Danielle Machado da Silva   +4 more
doaj   +1 more source

Are African primary physicians suspicious enough? Challenges of multiple myeloma diagnosis in Africa

open access: yesThe Egyptian Journal of Internal Medicine, 2021
Background Multiple myeloma is a hematological malignancy of plasma cells belonging to a spectrum of monoclonal protein-secreting disorders known as paraproteinemias.
Erick Thokerunga   +2 more
doaj   +1 more source

Diffuse plane xanthomatosis associated with monoclonal gammopathy Xantomatose plana difusa associada a gamopatia monoclonal

open access: yesAnais Brasileiros de Dermatologia, 2011
Diffuse plane normolipemic xanthomatosis (DPNX) is a rare, non-inherited disease that is often associated with systemic diseases, mainly malignant hematological (especially multiple myeloma) or lymph proliferative disorders.
Aristóteles Rosmaninho   +4 more
doaj   +1 more source

Recurrence of membranoproliferative glomerulonephritis post transplant – Is this mere recurrence of pattern or recurrence of disease?

open access: yesSaudi Journal of Kidney Diseases and Transplantation, 2019
Recurrence of membranoproliferative glomerulonephritis (MPGN) is seen in 1965% cases of postrenal transplant resulting in graft loss in up to 35-50% of cases.
Umesh Lingaraj   +5 more
doaj   +1 more source

Scleromyxedema without paraproteinemia

open access: yesInternational Journal of Dermatology, 2014
AbstractBackgroundScleromyxedema is a rare generalized form of lichen myxedematosus, a chronic cutaneous mucinosis of unknown etiology usually associated with a monoclonal gammopathy and underlying systemic disorders. It is characterized by the presence of lichenoid papules and diffuse indurations of the skin.
Abarzúa, Alvaro A.   +3 more
openaire   +3 more sources

Xantogranuloma necrobiótico solitário sem paraproteinemia Necrobiotic xanthogranuloma without paraproteinemia

open access: yesAnais Brasileiros de Dermatologia, 2008
O xantogranuloma necrobiótico é doença crônica granulomatosa e xantomatosa, caracterizada por pápulas e placas infiltradas, eritematosas e amareladas, preferencialmente localizadas na região periorbital.
Danielle Mazziero Macedo   +5 more
doaj   +1 more source

Clinical observation of monoclonal fibrillary glomerulonephritis

open access: yesВестник медицинского института «Реавиз»: Реабилитация, врач и здоровье
Monoclonal gammopathy of renal significance is a condition caused by the proliferation of a clone of B-lymphocytes or plasma cells that does not reach the criteria required for the initiation of treatment for oncohematological indications, but is ...
T. A. Garkusha   +2 more
doaj   +1 more source

Subcorneal Pustular Dermatosis, a Systematic Review and Pooled Analysis of a Rare and Underdiagnosed Disease

open access: yesJEADV Clinical Practice, EarlyView.
ABSTRACT Background Subcorneal pustular dermatosis (SPD), or Sneddon–Wilkinson disease, is a rare, relapsing pustular skin condition of unknown cause, characterised by subcorneal pustules. Objectives To summarise the demographic, clinical, histopathological, management and disease course of SPD.
Mason H. Crossman   +5 more
wiley   +1 more source

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