Identification of Monoclonal Immunoglobulins by Immunofixation Electrophoresis - Some Questions
In the series of 2413 paraproteins analyzed by immunoelectrophoresis during 30 years, doubled paraproteinemias were found 42 times, i.e. a frequence of 1.7%.
Miloš Tichý
doaj +1 more source
Spectacular skin nodules: Cutaneous necrobiotic xanthogranuloma without paraproteinemia
Necrobiotic xanthogranuloma (NXG) is a very rare, progressive variant of non-Langerhans cell histiocytosis. It is known to be associated with multisystem involvement and paraproteinemias.
Shimoni Kadakia +3 more
doaj +1 more source
Heavy-chain deposition disease associated with multiple myeloma: a case report [PDF]
Heavy-chain deposition disease (HCDD) is a rare disorder characterized by the deposition of monoclonal immunoglobulin. Due to the disease's rarity and diagnostic challenges, its prognosis is generally poor.
Young Rong Lee +5 more
doaj +1 more source
Scleromyxedema: clinical diagnosis and autopsy findings [PDF]
Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis.
Ana Carolina Bulhões Sala +5 more
doaj +1 more source
Scleromyxedema without paraproteinemia
AbstractBackgroundScleromyxedema is a rare generalized form of lichen myxedematosus, a chronic cutaneous mucinosis of unknown etiology usually associated with a monoclonal gammopathy and underlying systemic disorders. It is characterized by the presence of lichenoid papules and diffuse indurations of the skin.
Abarzúa, Alvaro A. +3 more
openaire +3 more sources
Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy
Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins +2 more
doaj +1 more source
Plasmaferese em neurologia análise crítica da indicação e protocolos
Por ser a plasmaferese método terapêutico moderno e seguro, ela é cada vez mais indicada em doenças ligadas etiopatogenicamente à imunologia. Propomo-nos analisar suas indicações no âmbito da neurologia. Discutimos e analisamos sua indicação em miastenia
José Carlos Brant Seggia, Paulo Abreu
doaj +1 more source
Relato de caso: Paciente, sexo feminino, 43 anos, sem comorbidades, admitida na clínica cirúrgica do Hospital Jean Bitar (HJB) devido quadro de massa abdominal hipogástrica.
BLSA Lima +9 more
doaj +1 more source
Necrobiotic xanthogranuloma associated with smoldering multiple myeloma: satisfactory response to cyclophosphamide, dexamethasone, and thalidomide [PDF]
: Necrobiotic xanthogranuloma is a rare chronic condition, belonging to the group C non-Langerhans cell histiocytoses, which is relevant due to the possibility of extracutaneous involvement and association with systemic diseases, particularly hematologic
Renan Bernardes de Mello +1 more
doaj +1 more source
Are African primary physicians suspicious enough? Challenges of multiple myeloma diagnosis in Africa
Background Multiple myeloma is a hematological malignancy of plasma cells belonging to a spectrum of monoclonal protein-secreting disorders known as paraproteinemias.
Erick Thokerunga +2 more
doaj +1 more source

