Results 11 to 20 of about 1,092 (158)

Anti-GD1b Disorder Presenting as Multiple Mononeuropathies. [PDF]

open access: yesClin Case Rep
ABSTRACT Isolated anti GD1b disorders are quite rare. They usually present with ophthalmoplegia, sensory ataxia, paraproteinemia, and elevated cold agglutinants. The response to immunosuppressant treatment does not seem to be very effective. We report a case of isolated mononeuropathies associated with isolated anti‐GD1b antibodies, without ataxia or ...
Eid K, Araoui R, Ismail R, Sawaya R.
europepmc   +2 more sources

Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy

open access: yesAnais Brasileiros de Dermatologia, 2004
Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins   +2 more
doaj   +1 more source

Paraproteinemia in a Child with Leukemia [PDF]

open access: yesBlood, 1970
Abstract A four-year-old boy was diagnosed as having lymphoblastic leukemia in January 1967. On immunosuppressive therapy he had several clinical remissions and relapses. In mid-1968 he entered a period of sustained clinical remission. At that time a monoclonal gammaglobulin peak appeared in the electrophoresis pattern of his serum.
K J, Lindqvist   +2 more
openaire   +2 more sources

Plasmaferese em neurologia análise crítica da indicação e protocolos

open access: yesArquivos de Neuro-Psiquiatria, 1992
Por ser a plasmaferese método terapêutico moderno e seguro, ela é cada vez mais indicada em doenças ligadas etiopatogenicamente à imunologia. Propomo-nos analisar suas indicações no âmbito da neurologia. Discutimos e analisamos sua indicação em miastenia
José Carlos Brant Seggia, Paulo Abreu
doaj   +1 more source

LINFOMA LINFOPLASMACÍTICO SECRETOR DE IGG/KAPPA EVOLUINDO COM ANEMIA HEMOLÍTICA E INSUFICIÊNCIA RENAL

open access: yesHematology, Transfusion and Cell Therapy, 2021
Relato de caso: Paciente, sexo feminino, 43 anos, sem comorbidades, admitida na clínica cirúrgica do Hospital Jean Bitar (HJB) devido quadro de massa abdominal hipogástrica.
BLSA Lima   +9 more
doaj   +1 more source

Necrobiotic xanthogranuloma associated with smoldering multiple myeloma: satisfactory response to cyclophosphamide, dexamethasone, and thalidomide [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2019
: Necrobiotic xanthogranuloma is a rare chronic condition, belonging to the group C non-Langerhans cell histiocytoses, which is relevant due to the possibility of extracutaneous involvement and association with systemic diseases, particularly hematologic
Renan Bernardes de Mello   +1 more
doaj   +1 more source

Are African primary physicians suspicious enough? Challenges of multiple myeloma diagnosis in Africa

open access: yesThe Egyptian Journal of Internal Medicine, 2021
Background Multiple myeloma is a hematological malignancy of plasma cells belonging to a spectrum of monoclonal protein-secreting disorders known as paraproteinemias.
Erick Thokerunga   +2 more
doaj   +1 more source

Xantoma plano difuso normolipêmico idiopático com hiperesplenismo Diffuse plane idiopathic normolipemic xanthoma with hiperesplenism

open access: yesAnais Brasileiros de Dermatologia, 2010
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma.
Danielle Machado da Silva   +4 more
doaj   +1 more source

Diffuse plane xanthomatosis associated with monoclonal gammopathy Xantomatose plana difusa associada a gamopatia monoclonal

open access: yesAnais Brasileiros de Dermatologia, 2011
Diffuse plane normolipemic xanthomatosis (DPNX) is a rare, non-inherited disease that is often associated with systemic diseases, mainly malignant hematological (especially multiple myeloma) or lymph proliferative disorders.
Aristóteles Rosmaninho   +4 more
doaj   +1 more source

Recurrence of membranoproliferative glomerulonephritis post transplant – Is this mere recurrence of pattern or recurrence of disease?

open access: yesSaudi Journal of Kidney Diseases and Transplantation, 2019
Recurrence of membranoproliferative glomerulonephritis (MPGN) is seen in 1965% cases of postrenal transplant resulting in graft loss in up to 35-50% of cases.
Umesh Lingaraj   +5 more
doaj   +1 more source

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