Results 11 to 20 of about 1,204 (194)

Plasmaferese em neurologia análise crítica da indicação e protocolos

open access: yesArquivos de Neuro-Psiquiatria, 1992
Por ser a plasmaferese método terapêutico moderno e seguro, ela é cada vez mais indicada em doenças ligadas etiopatogenicamente à imunologia. Propomo-nos analisar suas indicações no âmbito da neurologia. Discutimos e analisamos sua indicação em miastenia
José Carlos Brant Seggia, Paulo Abreu
doaj   +2 more sources

ESCLEREDEMA DE BUSCHKE – A propósito de um caso clínico

open access: yesGalicia Clínica, 2017
RESUMO: O Escleredema de Buschke (EB) é uma doença rara do tecido conjuntivo, de etiologia desconhecida, caracterizada por espessamento e endurecimento da pele, geralmente localizado nas regiões proximais e posteriores do tronco e pescoço.
Jorge Henriques   +3 more
doaj   +3 more sources

Familiality of benign and malignant paraproteinemias. A population-based cancer-registry study of multiple myeloma families [PDF]

open access: yesHaematologica, 2005
BACKGROUND AND OBJECTIVES: The occurrence of two or more cases of multiple myeloma (MM) in the same family has been reported from time to time. The current study is the first population- and cancer-registry-based survey to investigate familiality of ...
HM Ogmundsdottir   +6 more
doaj   +1 more source

Anti-GD1b Disorder Presenting as Multiple Mononeuropathies. [PDF]

open access: yesClin Case Rep
ABSTRACT Isolated anti GD1b disorders are quite rare. They usually present with ophthalmoplegia, sensory ataxia, paraproteinemia, and elevated cold agglutinants. The response to immunosuppressant treatment does not seem to be very effective. We report a case of isolated mononeuropathies associated with isolated anti‐GD1b antibodies, without ataxia or ...
Eid K, Araoui R, Ismail R, Sawaya R.
europepmc   +2 more sources

Usefulness of serum globulin levels for discriminating patients with monoclonal gammopathies/ paraproteinemias

open access: yes, 2021
Introduction and Aim: The confirmatory step in diagnosis of monoclonal gammopathies is bone marrow biopsy and presence of M-protein in serum protein electrophoresis.
Pawar, Neelam M., Hegde, Anupama
core   +1 more source

Heavy-chain deposition disease associated with multiple myeloma: a case report [PDF]

open access: yesKosin Medical Journal
Heavy-chain deposition disease (HCDD) is a rare disorder characterized by the deposition of monoclonal immunoglobulin. Due to the disease's rarity and diagnostic challenges, its prognosis is generally poor.
Young Rong Lee   +5 more
doaj   +1 more source

Scleromyxedema: clinical diagnosis and autopsy findings [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2016
Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis.
Ana Carolina Bulhões Sala   +5 more
doaj   +1 more source

Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy

open access: yesAnais Brasileiros de Dermatologia, 2004
Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins   +2 more
doaj   +1 more source

Paraproteinemias Associated with Autoimmune Diseases

open access: yes, 2022
Paraproteinemia is a frequent laboratory feature in the course of many organ specific or systemic autoimmune diseases. It can be persistent or transient. Autoimmune diseases are secondary to chronic activation of the immune system by antigenic stimuli on
Quartuccio L., De Vita S., Treppo E.
core   +1 more source

Paraproteinemia in a Child with Leukemia [PDF]

open access: yesBlood, 1970
Abstract A four-year-old boy was diagnosed as having lymphoblastic leukemia in January 1967. On immunosuppressive therapy he had several clinical remissions and relapses. In mid-1968 he entered a period of sustained clinical remission. At that time a monoclonal gammaglobulin peak appeared in the electrophoresis pattern of his serum.
K J, Lindqvist   +2 more
openaire   +2 more sources

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