Plasmaferese em neurologia análise crítica da indicação e protocolos [PDF]
Por ser a plasmaferese método terapêutico moderno e seguro, ela é cada vez mais indicada em doenças ligadas etiopatogenicamente à imunologia. Propomo-nos analisar suas indicações no âmbito da neurologia. Discutimos e analisamos sua indicação em miastenia
José Carlos Brant Seggia, Paulo Abreu
doaj +2 more sources
ESCLEREDEMA DE BUSCHKE – A propósito de um caso clínico [PDF]
RESUMO: O Escleredema de Buschke (EB) é uma doença rara do tecido conjuntivo, de etiologia desconhecida, caracterizada por espessamento e endurecimento da pele, geralmente localizado nas regiões proximais e posteriores do tronco e pescoço.
Jorge Henriques +3 more
doaj +4 more sources
Anti-GD1b Disorder Presenting as Multiple Mononeuropathies. [PDF]
ABSTRACT Isolated anti GD1b disorders are quite rare. They usually present with ophthalmoplegia, sensory ataxia, paraproteinemia, and elevated cold agglutinants. The response to immunosuppressant treatment does not seem to be very effective. We report a case of isolated mononeuropathies associated with isolated anti‐GD1b antibodies, without ataxia or ...
Eid K, Araoui R, Ismail R, Sawaya R.
europepmc +2 more sources
Illuminating Blurry Vision: Visualization of Corneal Protein Deposition With Immunofluorescence in Two Illustrative Case Reports. [PDF]
Background Monoclonal gammopathy of undetermined significance (MGUS) is an asymptomatic, premalignant disease with a progression rate of 0.5%–1% per year to multiple myeloma. It can rarely present with significant ocular symptoms in the context of crystalline keratopathy, necessitating medical and surgical interventions.
Zengin S +7 more
europepmc +2 more sources
Paraproteinemias Associated with Autoimmune Diseases [PDF]
Paraproteinemia is a frequent laboratory feature in the course of many organ specific or systemic autoimmune diseases. It can be persistent or transient. Autoimmune diseases are secondary to chronic activation of the immune system by antigenic stimuli on
Quartuccio L., De Vita S., Treppo E.
core +1 more source
Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy
Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins +2 more
doaj +1 more source
Paraproteinemia in a Child with Leukemia [PDF]
Abstract A four-year-old boy was diagnosed as having lymphoblastic leukemia in January 1967. On immunosuppressive therapy he had several clinical remissions and relapses. In mid-1968 he entered a period of sustained clinical remission. At that time a monoclonal gammaglobulin peak appeared in the electrophoresis pattern of his serum.
K J, Lindqvist +2 more
openaire +2 more sources
Relato de caso: Paciente, sexo feminino, 43 anos, sem comorbidades, admitida na clínica cirúrgica do Hospital Jean Bitar (HJB) devido quadro de massa abdominal hipogástrica.
BLSA Lima +9 more
doaj +1 more source
Necrobiotic xanthogranuloma associated with smoldering multiple myeloma: satisfactory response to cyclophosphamide, dexamethasone, and thalidomide [PDF]
: Necrobiotic xanthogranuloma is a rare chronic condition, belonging to the group C non-Langerhans cell histiocytoses, which is relevant due to the possibility of extracutaneous involvement and association with systemic diseases, particularly hematologic
Renan Bernardes de Mello +1 more
doaj +1 more source
Are African primary physicians suspicious enough? Challenges of multiple myeloma diagnosis in Africa
Background Multiple myeloma is a hematological malignancy of plasma cells belonging to a spectrum of monoclonal protein-secreting disorders known as paraproteinemias.
Erick Thokerunga +2 more
doaj +1 more source

