Bladder perivascular epithelioid cell tumor (PEComa): a case report and literature review
INTRODUCTION: Perivascular epithelioid cell tumors (PEComa) are a very uncommon mesenchymal cancer with uncertain malignant potential.MATERIALS AND METHODS: A computerized research on Pub Med was performed regarding bladder PEComa.
CERRUTO, Maria Angela +5 more
core +1 more source
Management and Outcomes of Uterine Smooth Muscle Tumour of Uncertain Malignant Potential (STUMP)
ABSTRACT Background Uterine smooth muscle tumours of uncertain malignant potential (STUMP) is a mesenchymal tumour which does not fulfil the criteria for leiomyoma, benign histological subtypes, or leiomyosarcoma. The risk factors for recurrence and the rates of recurrence vary amongst different studies; as a result, there are currently no consensus ...
Aaron Hey Yin Chan +3 more
wiley +1 more source
Sclerosing Perivascular Epithelioid Cell Tumor of the Lung: A Case Report with Cytologic Findings [PDF]
Benign perivascular epithelioid cell tumor (PEComa) of the lung is a rare benign neoplasm, a sclerosing variant of which is even rarer. We present a case of 51-year-old man who was diagnosed with benign sclerosing PEComa by percutaneous fine needle ...
Ha Yeon Kim +5 more
doaj +1 more source
Orbital Perivascular Epithelioid Cell Tumor in a Case of Tuberous Sclerosis
The aim of the study was to report a case of orbital perivascular epithelioid cell tumor (PEComa) in a known diagnosed patient of tuberous sclerosis and retinal astrocytic hamartoma.
Shaikha H Aljneibi +3 more
doaj +1 more source
Simultaneous diagnosis of liver PEComa in a family with known Li-Fraumeni syndrome: a case report.
Li-Fraumeni syndrome (LFS) is an autosomal dominant hereditary disease. It is associated with the loss of function of the p53 protein and an increased risk of malignant tumor development at early age.
Álvarez Álvarez, Rosa +5 more
core +1 more source
Psychosocial Impact of Sarcoma: Challenges and Adaptation, a Meta‐Synthesis
ABSTRACT Objectives Sarcoma is a rare and heterogeneous cancer frequently associated with significant psychosocial burden. This review aims to synthesise qualitative research to examine the psychosocial impact of sarcoma in adults, focusing on how individuals experience and make sense of disruption across diagnosis, treatment, recovery, and ...
R. Beghean +5 more
wiley +1 more source
TFE3 activation in a TSC1-altered malignant PEComa: challenging the dichotomy of the underlying pathogenic mechanisms [PDF]
Perivascular epithelioid cell tumors (PEComas) form a family of rare mesenchymal neoplasms that typically display myomelanocytic differentiation. Upregulation of mTOR signaling due the inactivation of TSC1/2 (Tuberous Sclerosis 1 and 2) is believed to be
Märdian, S. +50 more
core +1 more source
ABSTRACT Cancer cells rewire their metabolism to sustain a high proliferation rate. Sensing external cues is essential to match the metabolic fluxes of the cells to the external stimuli. As part of the glucose metabolism, the hexosamine biosynthesis pathway (HBP) is considered a nutrient‐sensing pathway. The HBP produces UDP‐GlcNAc, a key precursor for
Pegah Rahimizadeh +4 more
wiley +1 more source
Diagnostic pitfall of a rare variant of angiomyolipoma, epithelioid angiomyolipoma - a case report
Angiomyolipoma of the kidney is a common benign mesenchymal neoplasm of kidney. A rare variant, epithelioid angiomyolipoma, however, may show malignant behavior.
Michael Leonard Anthony +6 more
doaj +1 more source
A diminutive perivascular epithelioid cell tumor in the colon
Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal tumor. Some papers have reported that colonoscopy could be used to treat PEComa with a predominantly pedunculated polyp, whereas surgical intervention is often required for cases with ...
Naoki Sugimura +7 more
doaj +1 more source

