Results 101 to 110 of about 1,162 (183)
La pentalogía de Cantrell involucra defectos de la línea media abdominal supraumbilical, parte inferior del esternón, diafragma anterior, pericardio diafragmático y malformaciones congénitas intracardiacas (1, 2).
Carlos E Riaño +6 more
doaj
PENTALOGY OF CANTRELL: A CASE REPORT
Cantrell’s pentalogy is a rare developmental disorder occurring between the 14th and 18th day of embryonic life. Diagnosis is possible in the first trimester, when the rupturing of the continuity of the anterior chest cavity and abdominal walls is ...
Justyna Płusajska +4 more
doaj +1 more source
Divertículo ventricular en pentalogía de Cantrell: entidades infrecuentes, pero no aisladas [PDF]
Pentalogy of Cantrell is a rare entity characterized by a combination of alterations, among which the following stand out: defects of the pericardium, heart, diaphragm, lower third of sternum and abdominal wall.
Arias-Díaz, Antonio +5 more
core +1 more source
Anaesthesia and Pentalogy of Cantrell [PDF]
pected. The ET tube was replaced but there was no improvement. Further desaturation and bradycardia ensued. Although air entry was poor bilaterally it was thought to be worse on the right. The exomphalos made assessment of the epigastrium difficult and no hepar was palpable. With further deterioration, ongoing bradycardia and absent peripheral pulses a
openaire +1 more source
Asociación de ectopia cordis con pentalogía de Cantrell a partir de variantes en el gen ALDH1A2. [PDF]
Objetivo: Identificar la relación de variantes en el gen ALDH1A2 con la ectopia cordis descrita en los pacientes con pentalogía de Cantrell. Materiales y métodos: Según la declaración PRISMA, se realizó una búsqueda sistematizada de la literatura en ...
Jiménez-Müller, Hana +2 more
core +1 more source
Pentalogy of Cantrell with a double-outlet right ventricle: Prenatal Diagnosis, Delivery and Immediate Postnatal Surgical Repair / Pentalogia de Cantrell com um ventrículo direito de saída dupla: Diagnóstico Pré-Natal, Parto e Reparação Cirúrgica Pós-Natal Imediata [PDF]
A Pentalogia de Cantrell é uma doença congênita rara, havendo apenas cerca de 250 casos relatados. A síndrome consiste em uma variedade toracoabdominal de ectopia cordis, associada a cinco defeitos principais em: linha mediana anterior supraumbilical de ...
Bringel, Camilla Azevedo +5 more
core
En 1958, Cantrell describió un síndrome caracterizado por cinco defectos que incluyen: ectopia cordis, onfalocele, disrupción del esternón distal, diafragma anterior y pericardio diafragmático.
Hernán Cortés Y +1 more
doaj
Pentalogia de Cantrell: relato de caso Pentalogy of Cantrell: case report
Os autores descrevem o tratamento cirúrgico de um caso de pentalogia de Cantrell, rara anomalia congênita, caracterizada por defeitos da parede abdominal, terço inferior do esterno, diafragma, pericárdio e coração.The authors describe the surgical cure ...
Sheila Hazin +7 more
doaj
Pentalogía de Cantrell: reporte de un caso de padres consanguíneos [PDF]
Pentalogy of Cantrell is a syndrome evidencing five anomalies: a midline, upper abdominal wall abnormality; lower sternal defect; anterior diaphragmatic defect; diaphragmatic pericardial defect, and congenital abnormalities of the heart.
Barragán, Arelis +3 more
core +3 more sources

