Results 201 to 210 of about 29,850 (257)

Mitochondrial phosphoenolpyruvate carboxykinase deficiency

European Journal of Pediatrics, 1986
A 3-month-old girl presented with anorexia, failure to thrive and drowsiness. She was mildly icteric with hepatomegaly and peripheral oedema. Disordered liver function tests were associated with the biopsy appearances of a giant cell hepatitis and with a Fanconi syndrome. At the age of 16 weeks she collapsed with profound hypoglycaemia.
J V, Leonard   +3 more
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Phosphoenolpyruvate carboxykinase activity in invertebrates

Comparative Biochemistry and Physiology, 1964
Abstract 1. 1. The presence of P-enolpyruvate carboxykinase has been demonstrated in nine species of molluscs and one species of coelenterate. In most, the activity was considerably higher than in rat liver and in some of them the activity was much higher than in chicken liver. 2. 2.
J W, SIMPSON, J, AWAPARA
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Phosphoenolpyruvate carboxykinase from Fasciola hepatica

International Journal for Parasitology, 1982
Abstract Behm C. A. and Bryant C. 1982. Phosphoenolpyruvate carboxykinase from Fasciola hepatica. International Journal for Parasitology 12 : 271–278. The kinetic properties of a partially purified preparation of phosphoenolpyruvate carboxykinase (PEPCK) from F. hepatica were examined.
C A, Behm, C, Bryant
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Stereochemistry of phosphoenolpyruvate carboxylation catalyzed by phosphoenolpyruvate carboxykinase

Biochemistry, 1986
The stereochemistry of the carboxylation of phosphoenolpyruvate to yield oxalacetate, catalyzed by chicken liver phosphoenolpyruvate carboxykinase and by Ascaris muscle phosphoenolpyruvate carboxykinase, was determined. The substrate (Z)-3-fluorophosphoenolpyruvate was used for the stereochemical analysis.
S H, Hwang, T, Nowak
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TWO CASES OF PHOSPHOENOLPYRUVATE CARBOXYKINASE DEFICIENCY

Acta Paediatrica, 1976
ABSTRACT. Two children are described who suffered from hypoglycemia and liver impairment. Assays of gluconeogenic enzymes in liver samples taken immediately after death demonstrated a deficiency of phosphoenolpyruvate carboxykinase, a key enzyme of gluconeogenesis.
Hommes, F A   +4 more
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Inhibition of phosphoenolpyruvate carboxykinase by streptonigrin

Biochemical Pharmacology, 1982
Streptonigrin, an antibiotic with antineoplastic activity, inhibited rat liver phosphoenolpyruvate carboxykinase with an I50 of 0.3 microM when excess FeCl2 was present. No inhibition occurred in the absence of added metal ion. Inhibition was partial and noncompetitive versus ITP and oxalacetic acid.
M L, Merryfield, H A, Lardy
openaire   +2 more sources

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