Results 41 to 50 of about 2,012 (189)
Biliary atresia is a destructive, idiopathic, and inflammatory cholangiopathy that affects intra and extra-hepatic bile ducts leading to fibrosis and obliteration of the biliary tract and development of liver cirrhosis.
Evalyne Tukwasibwe +3 more
doaj +1 more source
Anomalies of Abdominal Organs in Polysplenia Syndrome: Multidetector Computed Tomography Findings
Polysplenia syndrome is a rare situs ambiguous anomaly associated with multiple spleens and anomalies of abdominal organs. Because most of the minor anomalies do not cause clinical symptoms, polysplenia syndrome is detected incidentally in the adults ...
Sungwon Kim, Yong Seok Lee, Jin-Hee Jung
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Polysplenia is a congenital condition characterized by the presence of multiple small accessory spleens with absent of primary spleen. While polysplenia may occur in isolation or may be present as part of Polysplenia syndrome.
Jayeshkumar Kanani +1 more
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Aortic pseudocoarctation associated with polysplenia/heterotaxy syndrome
Polysplenia/heterotaxy syndrome is a rare congenital disorder associated with a wide spectrum of anomalies in various organ systems. Although anomalies of the cardiovascular system are common in this syndrome, the authors report a rare case of ...
Ricardo Duarte, Humberto Morais
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Heterotaxy syndrome with left atrial isomerism and polysplenia is a unique entity: a case report
A state of a patient with heterotaxy syndrome with polysplenia was indiscriminately diagnosed through visualized estimation (computed tomography and pelviabdominal ultrasound) regardless of the pathological state.
Rana El-Helbawy +2 more
doaj +1 more source
Wandering Spleen, A Rare Cause of Acute Abdomen: A Case Report
ABSTRACT A wandering spleen (WS) is rare and often presents a diagnostic challenge to clinicians. We report a WS in a 16‐year‐old who presented with abdominal pain, vomiting, and peritonism. Imaging (ultrasound and CT scans), which usually facilitates a prompt diagnosis, was inconclusive, and the diagnosis was made by exploratory laparotomy.
John Kanyiri Yambah +7 more
wiley +1 more source
Non-cardiac issues in patients with heterotaxy syndrome
Management of complex congenital heart disease in patients with Heterotaxy syndrome (HS) has steadily improved. However, there is an insufficient appreciation of various non-cardiac issues that might impact the overall status of these patients.
Shyam S Kothari
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Anatomy, embryology, and imaging of situs ambiguous with polysplenia and left IVC
The situs ambiguous or heterotaxy syndrome is a type of syndrome that involves multiple visceral abnormalities, vascular ones and associated with left isomerism.
Rosa Montero-Macías, MD +4 more
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Fontan‐associated liver disease (FALD) is a frequent complication after Fontan surgery. Data from 1168 Fontan patients, including blood tests, imaging, and pathology, from high‐volume centers across Japan were used to develop diagnostic criteria for FALD and advanced FALD. The proposed diagnostic criteria accurately identified FALD in 86.8% of patients,
Tomomi Kogiso +4 more
wiley +1 more source
Malrotation and volvulus associated with heterotaxy syndrome
A 2-year-old boy with heterotaxy syndrome with associated polysplenia, ventricular septal defect, and malrotation of gut with volvulus is presented. There was delay in diagnosis due to the unusual plain abdominal radiography findings.
Santosh K Mahalik +2 more
doaj +1 more source

