Results 51 to 60 of about 1,849 (196)

Non-cardiac issues in patients with heterotaxy syndrome

Annals of Pediatric Cardiology, 2014
Management of complex congenital heart disease in patients with Heterotaxy syndrome (HS) has steadily improved. However, there is an insufficient appreciation of various non-cardiac issues that might impact the overall status of these patients.
Shyam S Kothari
doaj   +1 more source

Incidental Diagnosis of Situs Inversus Totalis in a 45‐Year‐Old Male Who Presented With Acute Asthma Exacerbation: A Case Report and Brief Literature Review

Clinical Case Reports, Volume 13, Issue 11, November 2025.
ABSTRACT Incidental situs inversus totalis (SIT) requires thorough anatomical mapping to exclude associated syndromes (e.g., Kartagener) and congenital anomalies. Early identification, patient education on mirrored anatomy, and multidisciplinary coordination are essential to prevent iatrogenic errors during future interventions, even in asymptomatic ...
Ragasa Getachew Bayisa, Lensa Million Baharu, Mohammed Mecha Abafogi, Yosef Bekele Bonsa, Mohammed Kedir Shukri, Tamirat Godebo Woyimo   +5 more
wiley   +1 more source

Malrotation and volvulus associated with heterotaxy syndrome

Journal of Indian Association of Pediatric Surgeons, 2012
A 2-year-old boy with heterotaxy syndrome with associated polysplenia, ventricular septal defect, and malrotation of gut with volvulus is presented. There was delay in diagnosis due to the unusual plain abdominal radiography findings.
Santosh K Mahalik, Sanat Khanna, Prema Menon   +2 more
doaj   +1 more source

Heterotaxy syndrome with left atrial isomerism and polysplenia is a unique entity: a case report

Egyptian Journal of Chest Disease and Tuberculosis, 2021
A state of a patient with heterotaxy syndrome with polysplenia was indiscriminately diagnosed through visualized estimation (computed tomography and pelviabdominal ultrasound) regardless of the pathological state.
Rana El-Helbawy, Ibrahim Elmahalawy, Mohammed A Agha   +2 more
doaj   +1 more source

Wandering Spleen, A Rare Cause of Acute Abdomen: A Case Report

Clinical Case Reports, Volume 13, Issue 10, October 2025.
ABSTRACT A wandering spleen (WS) is rare and often presents a diagnostic challenge to clinicians. We report a WS in a 16‐year‐old who presented with abdominal pain, vomiting, and peritonism. Imaging (ultrasound and CT scans), which usually facilitates a prompt diagnosis, was inconclusive, and the diagnosis was made by exploratory laparotomy.
John Kanyiri Yambah, Kojo Amanfo Ninson, Abdul Samed Sulemana, Richardson Edwin Annan, Vishnu Nene Limon Abayateye, Gifty Aba Donkor, Moses Dokurugu, Ninnang Tobias   +7 more
wiley   +1 more source

Preduodenal Portal Vein And Polysplenia: A Case Report and Review Of Literature

, 2022
Preduodenal portal vein (PDPV) is a rare anomaly in which the portal vein courses anterior to the second part of the duodenum. PDPV is often associated with other congenital anomalies such as polysplenia, malrotation and pancreatic anomalies.
Bamberger, P. Kurt, Qatanani, Anas, Malat, Jaclyn, McCarley, Saudia M   +3 more
core   +2 more sources

Polysplenia syndrome in adulthood: A case report of incidental discovery

Radiology Case Reports
The Polysplenia Syndrome (PSS) is a form of heterotaxy, a rare congenital anomaly with an estimated incidence of 1 in 250,000 live births, first described by Helwig in 1929.
Jihane El Houssni, Sanae Jellal, Ismail Neftah, Fariss Dehayni, Siham El Haddad, Nazik Allali, Latifa Chat   +6 more
doaj   +1 more source

Polysplenia with situs inversus totalis, azygos continuation of the inferior vena cava, and duplication of the superior vena cava in a healthy adult: A case report

Radiology Case Reports
Polysplenia syndrome is an embryological disorder whereby the usual left-right asymmetry of thoracic and abdominal viscera fails to develop. It is a rare entity, estimated to occur at a frequency of 1 in 40,000, and is often associated with cardiac and ...
Rahman Ladak, HBSc, William Magnuson, MD
doaj   +1 more source

Polysplenia Syndrome With Persistent Left Superior Vena Cava: Case Report and Review of the Literature

Global Pediatric Health, 2022
Polysplenia syndrome is an uncommon condition associating several splenic nodules (sometimes polylobed spleen and cases of normal spleen have been described) with a number of malformations that appear between the fourth and sixth week of embryonic ...
El Houss Salma MD, Amsiguine Najwa MD, Tantaoui Mehdi MD, Allali Nazik PhD, Chat Latifa PhD, El Haddad Siham PhD   +5 more
doaj   +1 more source

Liver transplantation in children with biliary atresia and polysplenia syndrome.

, 1991
Biliary atresia is the most common indication for orthotopic liver transplantation (OLT) in children. The polysplenia syndrome anomalies, which occur in approximately 10% of children with biliary atresia, may represent special difficulties at liver ...
Claus, D., Otte, Jean-Bernard, Falchetti, D, Clapuyt, Philippe, de Ville de Goyet, J, de Carvalho, F B, De Hemptinne, Bernard   +6 more
core   +1 more source