Porphyria Cutanea Tarda Presenting as Erythema-multiforme Like Lesions
Journal of Nepal Health Research Council, 2019 Porphyria cutaneatarda, is the most common type of porphyria.It is characterized by defective uroporphyrinogen III decarboxylase enzyme.It presents with erosion, bulla with milia formation and sometimes with hypertrichosis and abnormal pigmentation ...
Niraj Parajuli +2 more
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A Propos D'une Forme Nerveuse Pure A Evolution Cyclique De Porphyrie Aigue [PDF]
Acta Medica Iranica, 1959 A case of acute porphyria with polynevrite is described. Evidence of porphyria has been formed in other members of the family.
Gharib, Zamani
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Przegląd Dermatologiczny, 2019 Porphyria cutanea tarda belongs to the group of porphyrias. Porphyria is a heme disorder caused by an acquired or congenital defect of hepatic enzymes. This consequently leads to the accumulation of porphyrins in various organs.
Marcela Nowak +3 more
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Sporadic porphyria cutanea tarda due to haemochromatosis [PDF]
, 2006 Haemochromatosis is a hereditary iron-overload syndrome caused by increased intestinal iron absorption and characterised by accumulation of potentially toxic iron in the tissues.
Dees, A., Geus, H.R.H. (Hilde) de
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Ferritin accumulation and uroporphyrin crystal formation in hepatocytes of C57BL/10 mice: A time-course study [PDF]
, 1993 To establish the time-sequence relationship between ferritin accumulation and uroporphyrin crystal formation in livers of C57BL/10 mice, a biochemical, morphological and morphometrical study was performed.
Bruijn, W.C. (Wim) de +5 more
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Acute Intermittent Porphyria: Flaccid Quadriplegia and Encephalopathy due to Posterior Reversible Encephalopathy Syndrome (PRES) [PDF]
Liaquat National Journal of Primary CareA deficiency of the enzyme HMB Hydroxymethylbilane synthase function, also known as porphobilinogen deaminase, leads to the emergence of acute intermittent porphyria (AIP). AIP is an uncommon form of hepatic porphyria inherited in an autosomal dominant
Saba Zaidi +2 more
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Fibulin-1 is a marker for arterial extracellular matrix alterations in type 2 diabetes [PDF]
, 2011 Extracellular matrix alterations are important elements in the arterial changes seen in diabetes, being associated with increased vascular stiffness and the development of cardiovascular diseases.
Aagard, Jan +16 more
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Porphyria: What Is It and Who Should Be Evaluated?
Rambam Maimonides Medical Journal, 2018 The porphyrias are a group of rare metabolic disorders, inherited or acquired, along the heme biosynthetic pathway, which could manifest with neurovisceral and/or cutaneous symptoms, depending on the defective enzyme.
Yonatan Edel, Rivka Mamet
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Suspicious minds : the dramatisation of paranoia in Victorian poetry : a thesis presented in partial fulfilment of the requirements for the degree of Master of Arts in English at Massey University [PDF]
, 1999 This thesis contains readings of a number of Victorian poems by Alfred Tennyson, Robert Browning and Dante Gabriel Rossetti which dramatise paranoia and jealousy.
Frost, Sarah Lee
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