Results 11 to 20 of about 1,679 (231)
Hepatology, EarlyView., 2022 Natural history of liver disease in a large international cohort of children with Alagille syndrome: Results from the GALA study. Abstract Background and Aims Alagille syndrome (ALGS) is a multisystem disorder, characterized by cholestasis. Existing outcome data are largely derived from tertiary centers, and real‐world data are lacking.
Shannon M. Vandriel +93 more
wiley +1 more source
Hepatic Artery Aneurysm Rupture After Double-Balloon Endoscopy in Biliary Atresia. [PDF]
United European Gastroenterol JUnited European Gastroenterology Journal, Volume 13, Issue 3, Page 491-493, April 2025.
Yokoyama S +3 more
europepmc +2 more sources
Long‐term clinical and socioeconomic outcomes of children with biliary atresia
JGH Open, Volume 7, Issue 12, Page 841-847, December 2023., 2023 With improved medical facilities, more children of biliary atresia are surviving with their native livers and require lifelong follow‐up by adult services for better outcome. Abstract Background Biliary atresia (BA) is rare liver disease of unknown etiology, and is a major indication for liver transplant (LT).
Javaid Sadiq +8 more
wiley +1 more source
Acta Paediatrica, Volume 112, Issue 10, Page 2210-2217, October 2023., 2023 Abstract Aim The gut–liver axis may contribute to pathophysiology of cholestatic liver disorders like biliary atresia (BA) by bacterial translocation (BT). Toll‐like receptors (TLR) are pattern recognition receptors known to activate innate immunity and secretion of inflammatory cytokines.
Nimish Godbole +5 more
wiley +1 more source
대한영상의학회지, 2022 Biliary atresia is a progressive, idiopathic, obliterative disease of the extrahepatic biliary tree that presents with biliary obstruction in the neonatal period. It is the most common indication for liver transplantation in children.
Tae Yeon Jeon
doaj +1 more source
The Value of Hepatic Scintigraphy in the Diagnosis of Biliary Atresia
Frontiers in Pediatrics, 2022 IntroductionBiliary Atresia (BA) requires prompt diagnosis and surgical intervention to optimize its outcome. The aim of this study was to evaluate the accuracy of EHIDA in distinguishing between BA and other causes of cholestatic jaundice.MethodsThis ...
Wing Ki Chan +2 more
doaj +1 more source
Type 3 of progressive familial intrahepatic cholestasis (PFIC‐3): Case report
Clinical Case Reports, Volume 11, Issue 4, April 2023., 2023 Abstract Genetic testing should always be advised in both parents and children of families with progressive familial intrahepatic cholestasis as early detection will provide more options to a better qualitative life.
Mohammad Badr Almoshantaf +4 more
wiley +1 more source
Journal of Indian Association of Pediatric Surgeons, 2019 A search on PubMed and Web of Science revealed scarcity of the literature on anomalies of hepatic artery or portal vein and the presence of arterioportal fistula in biliary atresia; although, it has long-lasting implications for both the patient and the ...
Prabudh Goel +3 more
doaj +1 more source
MiR-100 rs1834306 A>G Increases Biliary Atresia Risk in Southern Han Chinese Children
BioMed Research International, Volume 2023, Issue 1, 2023., 2023 Background. Biliary atresia (BA) is a type of severe cholestatic childhood disease that may have a genetic component. miR-100 plays a key role in regulating cell apoptosis, proliferation, and inflammatory reactions. A single‐nucleotide polymorphism in miR-100 has been proven to modulate susceptibility to various diseases. Methods.
Jiaming Chang +9 more
wiley +1 more source
Biliary Lipid Excretion After Hepatic Portoenterostomy
Annals of Surgery, 1976 Since 1974, 16 consecutive infants with biliary atresia have been treated by hepatic portoenterostomy employing an exteriorized Roux-en-Y intestinal segment (Miluliez). Simultaneous, sequential analyses of bile pigments and lipids in serum and biliary drainage were performed.
J R, Lilly, N B, Javitt
openaire +3 more sources