Results 71 to 80 of about 748,768 (294)

Spinal stenosis: A summary and review [PDF]

, 1993
A review of the etiology, clinical, radiological and laboratory presentation, differential diagnosis and management of spinal stenosis is presented.
Walker, B.F.
core  

Combination Chemotherapy in Severe Pulmonary Vein Stenosis—A Case Series

, 2023
Pulmonary vein stenosis results from a proliferative process that leads to the progressive obstruction of venous return to the left atrium. It is often resistant to catheterization and surgical based interventions and is frequently fatal when encountered
David Nykanen, Robert Sutphin, Michael Farias, Karen Iacono, Gabriel Krivenko, Robyn Keen   +5 more
core   +1 more source

Descriptive Epidemiology From the Myhre Syndrome Foundation Registry: The Value of Self‐Reported Data

American Journal of Medical Genetics Part C: Seminars in Medical Genetics, EarlyView.
ABSTRACT Myhre syndrome is an ultrarare genetic disease characterized by short stature, distinct craniofacial features, cardiovascular and respiratory fibrosis and stenosis, neurodevelopmental delays, autism, intellectual disability, and hearing loss. The natural history of Myhre syndrome is still not fully understood due to a small patient population ...
Mary K. Young, Armelle Pindon, Maggie R. Brand, Kate Wears, Katherine H. Young, Alyssa Mendel, Michael J. Lyons   +6 more
wiley   +1 more source

Persistence Pulmonal Hypertension After Balloon Mitral Valvuiloplasty

Majalah Kardiologi Indonesia, 2013
Background.Pulmonary hypertension frequently complicates mitral stenosis. Increased pulmonary artery pressure results from raised left atrial pressure, pulmonary arteriolar vasoconstriction, and obliterative changes in the pulmonary vascular bed, and ...
doaj   +1 more source

Physiological and clinical consequences of relief of right ventricular outflow tract obstruction late after repair of congenital heart defects. [PDF]

, 2006
BACKGROUND: Right ventricular outflow tract obstruction (RVOTO) is a common problem after repair of congenital heart disease. Percutaneous pulmonary valve implantation (PPVI) can treat this condition without consequent pulmonary regurgitation or ...
Sridharan, S, Schievano, S, Coats, L, Jones, R, Mist, B, Taylor, AM, Deanfield, JE, Bonhoeffer, P, Derrick, G, Khambadkone, S, Pellerin, D   +10 more
core  

Spectrum of Congenital Anomalies in Myhre Syndrome—Insights Into Effects Brought by Altered TGF‐β Signaling via Gain‐of‐Function Variants in SMAD4

American Journal of Medical Genetics Part C: Seminars in Medical Genetics, EarlyView.
ABSTRACT Myhre syndrome is a rare genetic disorder characterized by progressive multisystem involvement. Gain‐of‐function missense heterozygous variants affecting the Ile500 residue and Arg496 residue of the SMAD4 gene are implicated in this condition.
Kawmadi Gunawardena, Alessandro De Falco, Deborah Osio, Eleanor Sherlock, Emma Kivuva, Erina Sasaki, Francis H. Sansbury, Nayana Lahiri, Patricia Foley, Sahar Mansour, Shane McKee, Tazeen Ashraf, Nicola Brunetti‐Pierri, Usha Kini   +13 more
wiley   +1 more source

Successful management of fibrosing mediastinitis with severe vascular compromise: Report of two cases and literature review

Respiratory Medicine Case Reports, 2020
Fibrosing mediastinitis is a rare disorder characterized by the invasive proliferation of fibrous tissue within the mediastinum. This fibrosis can result in compression of intrathoracic structures including the pulmonary vasculature leading to clinical ...
Franklin Argueta, David Villafuerte, Jose Castaneda-Nerio, Jay Peters, Carlos Restrepo   +4 more
doaj   +1 more source

Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension [PDF]

, 2018
Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital ...
Sirisani, Joyce Darshinee Dom, Zahari, Norazah   +1 more
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Transcatheter aortic-valve replacement for inoperable severe aortic stenosis. [PDF]

, 2012
BACKGROUND: Transcatheter aortic-valve replacement (TAVR) is the recommended therapy for patients with severe aortic stenosis who are not suitable candidates for surgery. The outcomes beyond 1 year in such patients are not known.
Makkar, Raj R, Dewey, Todd M, Pocock, Stuart, Brown, David L, Pichard, Augusto D, Bowers, Bruce, Siegel, Robert J, Smith, Craig R, Webb, John G, Tuzcu, Murat, Moses, Jeffrey W, Williams, Matthew R, Babaliaros, Vasilis C, Thourani, Vinod H, Kapadia, Samir, Svensson, Lars G, Jilaihawi, Hasan, Kodali, Susheel, Bavaria, Joseph E, MD, Fontana, Gregory P, Akin, Jodi J, Douglas, Pamela S, Bavaria, Joseph E, Herrmann, Howard C, Leon, Martin B, PARTNER Trial Investigators, Anderson, William N   +26 more
core   +1 more source

Prognostic Significance of Computed Tomography Findings in Pulmonary Vein Stenosis

, 2021
(1) Pulmonary vein stenosis (PVS) can be a severe, progressive disease with lung involvement. We aimed to characterize findings by computed tomography (CT) and identify factors associated with death; (2) Veins and lung segments were classified into five ...
Rebecca S. Beroukhim, Lynn A. Sleeper, Laureen Sena, Ryan Callahan   +3 more
core   +1 more source