Pulmonary veno-occlusive disease: illustrative cases and literature review [PDF]
Pulmonary veno-occlusive disease (PVOD), also known as “pulmonary arterial hypertension (PAH) with overt features of venous/capillary involvement”, is a rare cause of PAH characterised by substantial small pulmonary vein and capillary involvement ...
Benoit Lechartier +7 more
doaj +3 more sources
Anti-synthetase syndrome-associated pulmonary veno-occlusive disease [PDF]
Pulmonary arterial hypertension has been reported with a prevalence of 7.9% in patients with anti-synthetase syndrome; however, anti-synthetase syndrome associated with pulmonary veno-occlusive disease (PVOD) has never before been described in the ...
Dana Kay +5 more
doaj +3 more sources
Pulmonary veno-occlusive disease in Sjogren's syndrome: a case report [PDF]
Background Pulmonary arterial hypertension (PAH) associated with connective tissue disease (CTD) belongs to Group 1 pulmonary hypertension. Pulmonary veno-occlusive disease (PVOD), which is characterized by venous system aberrations, has been previously ...
Xiaofang Zeng +8 more
doaj +3 more sources
Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination [PDF]
We describe a case of an adolescent male with the rare combination of pulmonary arterial hypertension (PAH) and pulmonary arteriovenous malformations (PAVM's) without confirmed hereditary hemorrhagic telangiectasia (HHT).
Baukje M. Zaaijer +7 more
doaj +4 more sources
Outcomes and risk assessment in pulmonary veno-occlusive disease [PDF]
Introduction Pulmonary veno-occlusive disease (PVOD) is a rare and severe subtype of pulmonary arterial hypertension (PAH). Although European Society of Cardiology/European Respiratory Society (ESC/ERS) guidelines advise assessing PAH severity at ...
Athénaïs Boucly +17 more
doaj +3 more sources
Mechanisms underlying age-associated exacerbation of pulmonary veno-occlusive disease [PDF]
Pulmonary veno-occlusive disease (PVOD) is a rare but severe form of pulmonary hypertension characterized by the obstruction of pulmonary arteries and veins, causing increased pulmonary artery pressure and leading to right ventricular (RV) heart failure.
Amit Prabhakar +8 more
doaj +3 more sources
Pulmonary veno-occlusive disease: Two children with gradual disease progression
Pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis are rare forms of pulmonary vascular disease. We report two cases of affected children who had evidence of pulmonary hypertension 3–5 years before developing radiographic findings ...
Ronald W. Day +6 more
doaj +2 more sources
Gemcitabine-Induced Pulmonary Toxicity: A Case Report of Pulmonary Veno-Occlusive Disease
Introduction Gemcitabine is a chemotherapeutic agent frequently used by for the treatment of several malignancies both in the adjuvant and metastatic setting.
Célia Turco +10 more
doaj +3 more sources
Long-term sildenafil therapy for pulmonary veno-occlusive disease in association with melphalan therapy for multiple myeloma: A case report [PDF]
Pulmonary veno-occlusive disease has a significantly worse prognosis than idiopathic pulmonary arterial hypertension. According to a case series from France, the median survival time from diagnosis to death or lung transplantation was only 1 year, and in
Christian Hesse +3 more
doaj +2 more sources
Pulmonary Veno-Occlusive Disease: A Rare Cause of Pulmonary Hypertension
Pulmonary veno-occlusive disease (PVOD) is a rare entity that is usually mistaken with pulmonary arterial hypertension (PAH) but is considered class I′ of PAH. It is important to subclassify PVOD and distinguish it from PAH as treatment with vasodilators
Said Hajouli MD +2 more
doaj +2 more sources

