Results 11 to 20 of about 9,727 (224)

Long-term sildenafil therapy for pulmonary veno-occlusive disease in association with melphalan therapy for multiple myeloma: A case report [PDF]

SAGE Open Medical Case Reports
Pulmonary veno-occlusive disease has a significantly worse prognosis than idiopathic pulmonary arterial hypertension. According to a case series from France, the median survival time from diagnosis to death or lung transplantation was only 1 year, and in
Christian Hesse, Gabor Kovacs, Stefan Scheidl, Horst Olschewski   +3 more
doaj   +2 more sources

When you hear hoofbeats, think zebras – pulmonary veno‐occlusive disease: A case report [PDF]

Pulmonary Circulation, 2022
Pulmonary veno‐occlusive disease (PVOD) is a rare disease. It may be idiopathic or associated, in particular, with connective tissue disease, or it may develop after radiation exposure; in heritable forms of PVOD, the inheritance is autosomal recessive ...
Laura Scelsi, Giuseppe Lanzillo, Eloisa Arbustini, Andrea D'Armini, Alessandra Greco, Federica Meloni, Annalisa Turco, Adele Valentini, Luigi Oltrona Visconti, Stefano Ghio   +9 more
doaj   +2 more sources

Trichloroethylene increases pulmonary endothelial permeability: implication for pulmonary veno-occlusive disease [PDF]

Pulmonary Circulation, 2020
Trichloroethylene exposure is a major risk factor for pulmonary veno-occlusive disease. We demonstrated that trichloroethylene alters the endothelial barrier integrity, at least in part, through vascular endothelial (VE)-Cadherin internalisation, and ...
Julien Caliez, Marianne Riou, Grégoire Manaud, Morad K. Nakhleh, Marceau Quatredeniers, Catherine Rucker-Martin, Peter Dorfmüller, Florence Lecerf, Maria C. Vinhas, Salam Khatib, Hossam Haick, Sylvia Cohen-Kaminsky, Marc Humbert, David Montani, Frédéric Perros   +14 more
doaj   +2 more sources

Pulmonary vein occlusion and veno-occlusive disease in a bilateral lung transplant patient: A case report

Respiratory Medicine Case Reports, 2020
A pulmonary vein occlusion and biopsy proven pulmonary veno-occlusive disease (PVOD) and hemangiomatosis is found in a bilateral lung transplant patient.
Xiao Wang, Kexin Zheng, Emilian Racila, Tadashi Allen   +3 more
doaj   +2 more sources

Pulmonary veno-occlusive disease in Sjogren's syndrome: a case report [PDF]

BMC Pulmonary Medicine, 2023
Background Pulmonary arterial hypertension (PAH) associated with connective tissue disease (CTD) belongs to Group 1 pulmonary hypertension. Pulmonary veno-occlusive disease (PVOD), which is characterized by venous system aberrations, has been previously ...
Xiaofang Zeng, Qiong Liu, Anandharajan Rathinasabapathy, Lihuang Zha, Dongliang Liu, Yiyang Tang, Jing Sun, Hui Luo, Zaixin Yu   +8 more
doaj   +2 more sources

Pulmonary veno-occlusive disease: illustrative cases and literature review [PDF]

European Respiratory Review
Pulmonary veno-occlusive disease (PVOD), also known as “pulmonary arterial hypertension (PAH) with overt features of venous/capillary involvement”, is a rare cause of PAH characterised by substantial small pulmonary vein and capillary involvement ...
Benoit Lechartier, Athénaïs Boucly, Sabina Solinas, Deepa Gopalan, Peter Dorfmüller, Teodora Radonic, Olivier Sitbon, David Montani   +7 more
doaj   +2 more sources

Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination [PDF]

Respiratory Medicine Case Reports, 2021
We describe a case of an adolescent male with the rare combination of pulmonary arterial hypertension (PAH) and pulmonary arteriovenous malformations (PAVM's) without confirmed hereditary hemorrhagic telangiectasia (HHT).
Baukje M. Zaaijer, Nienke Duppen, Brigitte W.M. Willemse, Martijn V. Verhagen, Marcus T.R. Roofthooft, Wim Timens, Rolf M.F. Berger, Johannes M. Douwes   +7 more
doaj   +2 more sources

Novel AGL variants in a patient with glycogen storage disease type IIIb and pulmonary hypertension caused by pulmonary veno-occlusive disease: A case report [PDF]

Frontiers in Genetics, 2023
Glycogen storage disease type III (GSD-III) is an autosomal recessive metabolic disorder caused by mutations in the AGL gene, and may develop various types of pulmonary hypertension (PH).
Akito Shindo, Kazutaka Ueda, Shun Minatsuki, Yukiteru Nakayama, Satoshi Hatsuse, Kanna Fujita, Seitaro Nomura, Masaru Hatano, Norifumi Takeda, Hiroshi Akazawa, Issei Komuro   +10 more
doaj   +2 more sources

Outcomes and risk assessment in pulmonary veno-occlusive disease [PDF]

ERJ Open Research
Introduction Pulmonary veno-occlusive disease (PVOD) is a rare and severe subtype of pulmonary arterial hypertension (PAH). Although European Society of Cardiology/European Respiratory Society (ESC/ERS) guidelines advise assessing PAH severity at ...
Athénaïs Boucly, Sabina Solinas, Antoine Beurnier, Xavier Jaïs, Sophia Keddache, Mélanie Eyries, Andrei Seferian, Mitja Jevnikar, Anne Roche, Sophie Bulifon, Arnaud Bourdin, Ari Chaouat, Vincent Cottin, Laurent Bertoletti, Laurent Savale, Marc Humbert, Olivier Sitbon, David Montani   +17 more
doaj   +2 more sources

Reactive Pulmonary Capillary Hemangiomatosis and Pulmonary Veno-Occlusive Disease in a Patient with Repaired Scimitar Syndrome [PDF]

Case Reports in Cardiology, 2016
Pulmonary capillary hemangiomatosis (PCH) is a rare histological substrate within the spectrum of pulmonary arterial hypertension that possibly represents an unusual manifestation of pulmonary veno-occlusive disease (PVOD).
Eva Güttinger, Bart Vrugt, Rudolf Speich, Silvia Ulrich, Fabienne Schwitz, Mattia Arrigo, Lars C. Huber   +6 more
doaj   +2 more sources