Results 71 to 80 of about 4,727 (145)

United States Pulmonary Hypertension Scientific Registry (USPHSR): rationale, design, and clinical implications

Pulmonary Circulation, 2019
Diagnostic World Health Organization (WHO) Group 1 pulmonary arterial hypertension (PAH) and Diagnostic Group 1' pulmonary veno-occlusive disease (PVOD) and/or pulmonary capillary hemangiomatosis (PCH) are progressive and fatal disorders. Past registries
C. Gregory Elliott, Eric D. Austin, David Badesch, Jessica Badlam, Raymond L. Benza, Wendy K. Chung, Harrison W. Farber, Kathy Feldkircher, Adaani E. Frost, Abby D. Poms, Katie A. Lutz, Michael W. Pauciulo, Chang Yu, William C. Nichols   +13 more
doaj   +1 more source

Heritable pulmonary hypertension: from bench to bedside

European Respiratory Review, 2017
Mutations in the BMPR2 gene, and more rarely in ACVRL1, endoglin, caveolin-1, KCNK3 and TBX4 genes predispose to heritable pulmonary arterial hypertension, an autosomal dominant disease with incomplete penetrance. Bi-allelic mutations in the EIF2AK4 gene
Barbara Girerd, Jason Weatherald, David Montani, Marc Humbert   +3 more
doaj   +1 more source

Comprehensive three‐dimensional morphology of neoangiogenesis in pulmonary veno‐occlusive disease and pulmonary capillary hemangiomatosis

The Journal of Pathology: Clinical Research, 2019
Pulmonary veno‐occlusive disease (PVOD) is a rare lung disease characterized by fibrotic narrowing of pulmonary veins leading to pulmonary hypertension (PH) and finally to death by right heart failure.
Lavinia Neubert, Paul Borchert, Hoen‐Oh Shin, Friedemann Linz, Willi L Wagner, Gregor Warnecke, Florian Laenger, Axel Haverich, Helge Stark, Marius M Hoeper, Mark Kuehnel, Maximilian Ackermann, Danny Jonigk   +12 more
doaj   +1 more source

Pulmonary veno-occlusive disease [PDF]

Human Pathology, 1970
C B, Carrington, A A, Liebow
openaire   +4 more sources

Pulmonary Veno-Occlusive Disease

Advances in Pulmonary Hypertension, 2023
Salma Al Kahf, Sabina Solinas, Marc Humbert, David Montani   +3 more
openaire   +1 more source

Case report: A finding of PVOD and PAH in first degree relatives suggests shared heritable risk and overlapping features of both pulmonary vascular diseases

Respirology Case Reports
Pulmonary veno‐occlusive disease (PVOD) is a rare form of pulmonary vascular disease that is difficult to distinguish clinically from pulmonary arterial hypertension (PAH).
Roger Winters, Lindsay M. Forbes, Dunbar Ivy, Carlyne Cool, Bryan D. Park, Peter Hountras, David Badesch, Sue Gu, Edda Spiekerkoetter, Roham Zamanian, Stacey LeierGluck, Todd M. Bull   +11 more
doaj   +1 more source

Acute venodilation properties of low-dose intravenous nitroglycerine in pulmonary veno-occlusive disease: a case report. [PDF]

Eur Heart J Case Rep, 2023
Maruyama H, Sakai S, Suzuki S.
europepmc   +1 more source

A rare compound heterozygous EIF2AK4 mutation in pulmonary veno-occlusive disease. [PDF]

BMC Pulm Med, 2022
Zhang C, Du Q, Wang S, Zhang R.
europepmc   +1 more source

Pulmonary Veno-Occlusive Disease [PDF]

, 2020
openaire   +1 more source

A Challenging Case of Genetically and Histologically Diagnosed Pulmonary Veno-Occlusive Disease with Extracorporeal Life Support and Redo Lung Transplantation. [PDF]

Case Rep Cardiol, 2023
Laimoud M, Alanazi Z, Alahmadi F, Aldalaan A.   +3 more
europepmc   +1 more source