Results 61 to 70 of about 4,727 (145)
Pulmonary Circulation, Volume 16, Issue 3, July 2026.ABSTRACT Pulmonary arterial hypertension (PAH) is a rare and progressive disease characterized by remodeling of the pulmonary vasculature, which leads to increased pulmonary artery pressure and ultimately right ventricular failure. Although Japanese guidelines recommend combination therapy, real‐world data show inconsistencies in its implementation. We
Yoko Arai +4 more
wiley +1 more source
Pulmonary Veno‐Occlusive Disease: A Focused Clinicopathologic Series
Pulmonary Circulation, Volume 16, Issue 3, July 2026.ABSTRACT Pulmonary veno‐occlusive disease (PVOD) is a rare and aggressive subtype of pulmonary arterial hypertension characterized by fibroproliferative obstruction of post‐capillary pulmonary venules leading to increased pulmonary vascular resistance and progressive right ventricular failure.
Yub Raj Sedhai +12 more
wiley +1 more source
Pulmonary veno-occlusive disease misdiagnosed as idiopathic pulmonary arterial hypertension
European Respiratory Review, 2009 A 27-yr-old female with a 6-month diagnosis of idiopathic pulmonary arterial hypertension (PAH) confirmed elsewhere was referred to our centre with worsening dyspnoea.
M. Palazzini, A. Manes
doaj
Poverty and Social Deprivation in Patients With Pulmonary Arterial Hypertension—A PHAR Analysis
Pulmonary Circulation, Volume 16, Issue 3, July 2026.ABSTRACT Poverty and social deprivation have been associated with impaired clinical outcomes and survival in several chronic diseases. The association between poverty and clinical outcomes in patients with pulmonary arterial hypertension (PAH) remains unclear.
Roberto J. Bernardo +12 more
wiley +1 more source
Survival Into Adulthood With FOXF1‐Associated Pulmonary Vascular Disease After Neonatal Onset
Pulmonary Circulation, Volume 16, Issue 3, July 2026.ABSTRACT Neonates and infants with FOXF1 mutation develop alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV), which is typically considered a uniformly fatal neonatal lung disorder due to marked hypoxemic respiratory failure with severe pulmonary hypertension (PH).
Khalifah A. Aldawsari +3 more
wiley +1 more source
Rapid disease progress in a PVOD patient carrying a novel EIF2AK4 mutation: a case report
BMC Pulmonary Medicine, 2020 Background Pulmonary veno-occlusive disease (PVOD) and pulmonary arterial hypertension (PAH) share an overlapping disease phenotype. Hence it is necessary to distinguish them.
Xiaofang Zeng +5 more
doaj +1 more source
European Journal of Haematology, Volume 117, Issue 1, Page 24-41, July 2026.ABSTRACT Acute lymphoblastic leukaemia (ALL) in older adults represents a growing clinical challenge, driven by an ageing population, adverse disease biology, and reduced tolerance to intensive chemotherapy. Although pediatric‐inspired regimens have improved outcomes in younger adults with Philadelphia chromosome (Ph)‐negative ALL, survival in older ...
Antonella Bruzzese +12 more
wiley +1 more source
Pulmonary CirculationPulmonary hypertension (PH) is a severe complication observed in pediatric patients after hematopoietic cell transplantation or chemotherapy. A review of records at Hokkaido University Hospital (2014–2024) identified four cases of PH, each with different
Ayako Chida‐Nagai +5 more
doaj +1 more source
Case Reports in Cardiology, 2016 Pulmonary capillary hemangiomatosis (PCH) is a rare histological substrate within the spectrum of pulmonary arterial hypertension that possibly represents an unusual manifestation of pulmonary veno-occlusive disease (PVOD).
Eva Güttinger +6 more
doaj +1 more source