Results 21 to 30 of about 9,189,306 (207)

Systemic and Craniospinal Rosai Dorfman Disease with Intraparenchymal, Intramedullary and Leptomeningeal Disease

open access: yesInternational Journal of Hematology-Oncology and Stem Cell Research, 2021
Rosai Dorfman disease is a rare histiocytic disorder of over-production of non-Langerhans histiocytes, which typically manifests with massive lymphadenopathy and sinonasal involvement.
Yi Li   +5 more
doaj   +1 more source

Recalcitrant primary cutaneous Rosai‐Dorfman disease. Efficacy of sirolimus and intralesional methylprednisolone

open access: yesSkin Health and Disease, 2023
Sinus histiocytosis or Rosai‐Dorfman disease (RDD) is a rare disorder with severe lymphadenopathy and a limited clinical course, the aetiology of which is still controversial. The disease usually affects cervical nodes, with fever, polyclonal gammopathy,
A. Tirado-Sánchez
semanticscholar   +1 more source

Immunoglobulin G4-Associated Rosai–Dorfman Disease: Report of 3 Cases

open access: yesEuropean Journal of Rheumatology, 2023
Rosai–Dorfman disease is characterized by dilated lymph node sinuses filled with lymphocytes, plasma cells, and histiocytes. Many of these histiocytes classically exhibit emperipolesis of lymphocytes and plasma cells.
J. Gallo   +5 more
semanticscholar   +1 more source

Cytological diagnosis of Rosai–Dorfman disease: A study of twelve cases with emphasis on diagnostic challenges

open access: yesJournal of Cytology, 2020
Context: Rosai–Dorfman disease, also known as Sinus histiocytosis with massive lymphadenopathy, is a benign proliferative disorder of histiocytes. It typically affects lymph nodes; however, extranodal disease is being increasingly reported.
Rallapalli Rajyalakshmi   +5 more
doaj   +1 more source

Cutaneous Rosai-Dorfman Disease: A Treatment Challenge

open access: yesDermatologic Therapy, 2021
Rosai-Dorfman disease (RDD) is a benign histiocytosis that rarely manifests as a purely cutaneous form. Its differential diagnosis and treatment can pose a challenge to both clinicians and pathomorphologists.
Anna Gawdzik   +5 more
semanticscholar   +1 more source

Diagnosis and treatment of Rosai-Dorfman disease of the spine: a systematic literature review

open access: yesSystematic Reviews, 2021
Purpose To review and summarize the clinical features, diagnosis, treatment strategies, and prognosis of spinal Rosai-Dorfman disease (RDD). Methods RDD is also termed as sinus histiocytosis with massive lymphadenopathy.
P. Hu   +3 more
semanticscholar   +1 more source

Phenotypic intrafamilial variability including H syndrome and Rosai–Dorfman disease associated with the same c.1088G > A mutation in the SLC29A3 gene

open access: yesHuman Genomics, 2021
Background Mutations in the SLC29A3 gene, which encodes the nucleoside transporter hENT3, have been implicated in syndromic forms of histiocytosis including H syndrome, pigmented hypertrichosis with insulin-dependent diabetes, Faisalabad histiocytosis ...
H. Chouk   +8 more
semanticscholar   +1 more source

Clinicopathological features, treatment approaches, and outcomes in Rosai-Dorfman disease

open access: yesHaematologica, 2019
Rosai-Dorfman disease is a rare subtype of non-Langerhans cell histiocytosis. With the last major report published in 1990, there is a paucity of contemporary data on this disease.
G. Goyal   +13 more
semanticscholar   +1 more source

Doença de Rosai-Dorfman cutânea Cutaneous Rosai-Dorfman Disease

open access: yesAnais Brasileiros de Dermatologia, 2009
Doença de Rosai-Dorfman é uma doença benigna e autolimitada. Tem etiologia desconhecida e foi descrita pela primeira vez por Rosai e Dorfman em 1969. As manifestações clássicas incluem linfadenopatia cervical usualmente acompanhada por febre, leucocitose
Fábio Machado Landim   +5 more
doaj   +1 more source

Rosai-Dorfman Disease of Bone and Soft Tissue.

open access: yesArchives of Pathology & Laboratory Medicine, 2021
CONTEXT.— Rosai-Dorfman disease is a rare histiocytic proliferative disorder of unknown pathogenesis that may be diagnostically difficult in extranodal sites.
R. A. García, Edward F Dicarlo
semanticscholar   +1 more source

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