Results 111 to 120 of about 11,417 (249)

Extranodal Rosai-Dorfman Disease presenting as an isolated epibulbar mass

Indian Journal of Ophthalmology, 2008
Rosai-Dorfman disease is a rare idiopathic disorder characterized by painless lymphadenopathy with cervical involvement in more than 80% cases. We report a case of Rosai-Dorfman disease presenting as an isolated epibulbar mass in a healthy young ...
Maheshwari Rajat, Shekde Satish
doaj  

Rosai-Dorfman Disease: A previously unreported association with Sickle Cell Disease [PDF]

, 2007
BACKGROUND: Rosai-Dorfman Disease is an uncommon benign systemic histio-proliferative disease. This is the first time the disease, although more common in people of African descent, is described in association with Sickle cell disease. CASE PRESENTATION:
Inusa, Baba, Ramadan, Ghada, Stebbing, Claire, van der Walt, Jon   +3 more
core   +2 more sources

Rosai-Dorfman Disease of the Spine: A Case Report of a Rare Disease and Review of the Literature [PDF]

, 2022
Rabia Rabia, Alaa Al-Taie, Fatima Al-Khafaji, Ali Barah   +3 more
openalex   +1 more source

Cutaneous Rosai–Dorfman disease with MAP2K1 mutation, initially mimicking an infection with parasitized histiocytes

Journal of Cutaneous Pathology, Volume 51, Issue 12, Page 942-947, December 2024.
Abstract Rarely, Rosai–Dorfman disease (RDD) manifests exclusively in the skin, typically as nodules on the trunk and extremities. Recognition of characteristic histopathologic features enables diagnosis of RDD. A 55‐year‐old female presented with a 7‐year history of cutaneous nodules involving the trunk and extremities. A prior skin biopsy specimen at
Joseph Gillam, Ruchi Desai, Raphael J. Louie, Scott A. Turner, Grace Y. Wang, Julio A. Diaz‐Perez, Mark C. Mochel   +6 more
wiley   +1 more source

Review and a case of rare Rosai-Dorfman disease

Biotechnology & Biotechnological Equipment
Rosai-Dorfman (RDD) is a rare histiocytic syndrome with variable clinical characteristics and extranodal involvement in more than 43% of the patients. This mini-review presents an overview of the literature on Rosai-Dorfman disease.
Dragomira Nikolova, Aleksandar Yordanov, Aleksandra Maslarova, Radka Hristoskova, Vera Damyanova, Savina Hadjidekova, Atanas Radinov   +6 more
doaj   +1 more source

Idiopathic multicentric Castleman disease with marrow fibrosis and extramedullary hematopoiesis

European Journal of Haematology, Volume 113, Issue 6, Page 833-841, December 2024.
Abstract Background Idiopathic multicentric Castleman disease (iMCD) is a rare inflammatory disorder mediated by excessive proinflammatory cytokine signaling, most notably by interleukin 6 (IL‐6). IL‐6‐induced extramedullary hematopoiesis (EMH) has been reported in murine models of iMCD. Herein we present four cases of iMCD with EMH in humans.
Marley Blommers, Sorin Selegean, Richard K. Wood, Mateo Sarmiento Bustamante, Saishravan Shyamsundar, E. Ashley Wiley, Emilie Comeau, Allam A. Shawwa, Stefan Rose‐John, David C. Fajgenbaum, Luke Y. C. Chen   +10 more
wiley   +1 more source

IgG4-related disease: A systematic review of this unrecognized disease in pediatrics [PDF]

, 2016
Background: Immunoglobulin G4-related disease (IgG4-RD) is a systemic fibro-inflammatory condition with an unclear pathophysiological mechanism affecting different parts of the body.
Bramer, W.M. (Wichor), Hagen, P.M. (Martin) van, Karim, A.F. (Faiz), Laar, J.A.M. (Jan) van, Loeffen, J. (Jan), Verdijk, R.M. (Robert), Westenberg, L. (Lauren)   +6 more
core   +4 more sources

Common progenitor origin for Rosai–Dorfman disease and clear cell sarcoma

The Journal of Pathology, Volume 264, Issue 3, Page 243-249, November 2024.
Abstract Histiocytic neoplasms (HNs) in adults have been reported to be associated with a high prevalence of coexisting haematological and solid malignancies. While a proportion of coexisting HNs and haematological malignancies share identical genetic alterations, the genetic association between HNs and solid malignancies has scarcely been reported. We
Aki Sato, Nozomi Yusa, Hiroyuki Takamori, Eigo Shimizu, Kazuaki Yokoyama, Satoshi Ichikawa, Hisayuki Yokoyama, Yuki Kasahara, Kodai Enda, Fumiyoshi Fujishima, Ryo Ichinohasama, Yasunori Ota, Seiya Imoto, Yasuhito Nannya   +13 more
wiley   +1 more source

Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report Doença de Rosai-Dorfman com manifestação cutânea extensa - Relato de caso

Anais Brasileiros de Dermatologia, 2013
Rosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with ...
Paula Azevedo Borges Leal, Adrilena Lopes Adriano, Marcelle Parente Breckenfeld, Igor Santos Costa, Antônio Renê Diógenes de Sousa, Heitor de Sá Gonçalves   +5 more
doaj  

A rare presentation of Rosai-Dorfman disease as a single dural-based lumbar intradural lesion: A case report

Heliyon
Central nervous system Rosai Dorfman disease (RDD) is a rare condition and it is just reported in 5% of 600 registered RDD cases. In previously reported patients, the intradural extramedullary spinal lesion is extremely rare.
Farid Kazemi Gazik, Peyman Gookizadeh, Masoud Khadivi, Ali Zare Mehrjardi, Arad Iranmehr   +4 more
doaj   +1 more source