Sinus Histiocytosis: An Uncommon Presentation of an Uncommon Condition [PDF]
, 2015 Introduction Rosai–Dorfman Disease (RDD), also known as Sinus Histiocytosis with Massive Lymphadenopathy (SHML), is a rare, benign, proliferative disorder of macrophages and monocytes that was first described by Rosai and Dorfman in 1969.
Greco, MD, Allison, Kane, MD, Gregory
core +2 more sources
NRAS Mutations May Be Involved in the Pathogenesis of Cutaneous Rosai Dorfman Disease: A Pilot Study
Biology, 2021 Background: Purely cutaneous Rosai-Dorfman disease (RDD) is a rare histiocytic proliferative disorder limited to the skin. To date, its pathogenesis remains unclear.
Kuan-Jou Wu +5 more
semanticscholar +1 more source
Clinicopathological and Gene Mutation Analysis of 27 Cases with Extranodal Rosai–Dorfman Disease
Journal of Inflammation Research, 2022 Objective To investigate the clinicopathological features, and mutations of NRAS, KRAS, BRAF and MAP2K1 genes in extranodal Rosai–Dorfman disease (RDD).
Ming Tang, X. Gu, P.C. Wu, Xuan Yang
semanticscholar +1 more source
Rosai‐Dorfman disease in 6‐year‐old child: Presentation, diagnosis, and treatment
Clinical Case Reports, 2021 Rosai‐Dorfman disease is referred to as sinus histiocytosis massive lymphadenopathy. We are reporting a rare case of Rosai‐Dorfman disease, a case of 6‐year‐old boy with a history of multiple painless submandibular and cervical lymphadenopathy.
Kalpana Giri +3 more
doaj +1 more source
Rosai-Dorfman disease presenting as stridor and hoarseness in a young female patient
Radiology Case Reports, 2023 Rosai-Dorfman disease is a non-Langherans cell histiocytosis typically revealed by lymphadenopathy. Extranodal involvement occurs in 43% and most commonly involves the head and neck, skin, and bones. Few reports have described laryngeal lesions.
Vivianne Kokje, MD, PhD +6 more
doaj +1 more source
Potential role of 18F-FDG PET/CT in a case of progressive Rosai Dorfman disease [PDF]
Asia Oceania Journal of Nuclear Medicine and Biology, 2021 Rosai Dorfman disease is a rare form of nonlangerhans cell histiocytosis, presenting with extensive lymphadenopathies. Treatment in most cases of nodal disease, involves close observation; however, extranodal involvement requires a more definitive ...
Armaghan Fard-Esfahani +4 more
doaj +1 more source
Rosai–Dorfman Disease: Breast Involvement—Case Report and Literature Review
Medicina, 2021 Background and objectives: Rosai–Dorfman disease (RDD) is a type of histiocytosis that usually appears in young adults or children as bilateral cervical lymphadenopathy, but extranodal involvement in not uncommon.
G. Iancu +5 more
semanticscholar +1 more source
Unusual presentation of Rosai-Dorfman disease in a 14-month-old Italian child: a case report and review of the literature [PDF]
, 2016 Background: Rosai-Dorfman disease (RDD) is a rare form of histiocytosis characterized by histiocyte proliferation within lymph nodes and extranodal tissue. Here we report an unusual presentation of RDD in an Italian toddler.
Bruzzi, Patrizia +5 more
core +2 more sources
Rosai Dorfman disease- A rare entity: Case report in North Indian male
Asian Journal of Medical Sciences, 2014 Rosai Dorfman disease is a rare disease characterized by histiocytic proliferation of lymph node in young adults. We present here the case of a 67 years old Indian male presenting with lymphadenopathy and pyrexia of unknown origin for 16 months duration.
Ankur Baruah
doaj +1 more source
Otolaryngology Case Reports, 2022 Rosai-Dorfman disease is a rare non-Langerhans cell histiocytosis which classically presents with cervical lymphadenopathy. Extranodal disease in the head and neck is uncommon.
Melissa M. Liu +2 more
doaj +1 more source