Results 61 to 70 of about 2,541 (165)

Extranodal manifestation of Rosai-Dorfman disease with bilateral ocular involvement

Journal of Cytology, 2011
Rosai-Dorfman disease, that is, sinus histiocytosis with massive lymphadenopathy is a benign systemic proliferative disorder of histiocytes. The typical clinical presentation of the disease includes bilateral painless massive lymphadenopathy, fever and ...
Chayanika Kala, Asha Agarwal, Sanjay Kala   +2 more
doaj   +1 more source

Morphological, immunohistochemical and molecular analysis of follicular dendritic cell sarcomas: L1CAM as a new diagnostic marker

Histopathology, Volume 87, Issue 2, Page 258-269, August 2025.
Pathohistological analysis of FDCS revealed a morphological spectrum and led to the identification of the adhesion molecule L1CAM as a novel diagnostic immunomarker for FDCS. Sequencing identified NFKBIA as the most frequently altered gene, of note, exclusively in cases with a predominant epithelioid cytomorphology.
Selina Schelbert, Katja Maurus, Sabine Roth, German Ott, Katrin S Kurz, Carolin Mogler, Barbara Wollenberg, John Linde, Alberto Zamo, Ioannis Anagnostopoulos, Susanne Gramlich, Andreas Rosenwald, Elena Gerhard‐Hartmann   +12 more
wiley   +1 more source

Review and a case of rare Rosai-Dorfman disease

Biotechnology & Biotechnological Equipment
Rosai-Dorfman (RDD) is a rare histiocytic syndrome with variable clinical characteristics and extranodal involvement in more than 43% of the patients. This mini-review presents an overview of the literature on Rosai-Dorfman disease.
Dragomira Nikolova, Aleksandar Yordanov, Aleksandra Maslarova, Radka Hristoskova, Vera Damyanova, Savina Hadjidekova, Atanas Radinov   +6 more
doaj   +1 more source

Isolated unilateral eyelid Rosai–Dorfman disease

Oman Journal of Ophthalmology, 2018
Isolated eyelid Rosai–Dorfman disease without orbital disease or systemic involvement is very rare and needs a high degree of suspicion. In this report, we describe a 16-year-old boy who presented with isolated eyelid Rosai–Dorfman disease involving the ...
Nandini Bothra, Swathi Kaliki, Swarnalata Gowrishankar, S Anuradha   +3 more
doaj   +1 more source

Mass‐Forming Variants in Antineutrophil Cytoplasmic Antibody–Associated Vasculitis: Diagnostic Complexities in Granulomatous Disease. A Case Report

ACR Open Rheumatology, Volume 7, Issue 4, April 2025.
A middle‐aged woman presented with a granulomatous breast lesion in 2018. By 2021, antibiotic‐resistant pneumonia led to the discovery of granulomatous inflammation in the lung and thyroid. Initially misdiagnosed as Erdheim–Chester disease (ECD), she was treated with interferon without success.
Benedetta Fazzi, Elena Treppo, Simone Longhino, Maria Pillon, Luca Quartuccio   +4 more
wiley   +1 more source

Immunoglobulin G4–Related Disease of the Sternoclavicular Joint: A Case Report

Clinical Case Reports, Volume 13, Issue 4, April 2025.
ABSTRACT This case highlights the possibility that Immunoglobulin G4‐related disease (IgG4‐RD) lesions can also occur in the sternoclavicular joint. If a neoplastic lesion is found in the sternoclavicular joint, a biopsy should be attempted to diagnose IgG4‐RD as a differential.
Remi Mizuta, Shinnosuke Takemoto, Mutsumi Ozasa, Sawana Ono, Takahito Fukuda, Ryuta Tagawa, Fumiko Hayashi, Kazumasa Akagi, Hiromi Tomono, Hirokazu Taniguchi, Midori Matsuo, Hiroshi Gyotoku, Takahiro Takazono, Hiroshi Ishimoto, Noriho Sakamoto, Keitaro Matsumoto, Yasushi Obase, Tomoya Nishino, Hiroshi Mukae   +18 more
wiley   +1 more source

Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report Doença de Rosai-Dorfman com manifestação cutânea extensa - Relato de caso

Anais Brasileiros de Dermatologia, 2013
Rosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with ...
Paula Azevedo Borges Leal, Adrilena Lopes Adriano, Marcelle Parente Breckenfeld, Igor Santos Costa, Antônio Renê Diógenes de Sousa, Heitor de Sá Gonçalves   +5 more
doaj  

A rare presentation of Rosai-Dorfman disease as a single dural-based lumbar intradural lesion: A case report

Heliyon
Central nervous system Rosai Dorfman disease (RDD) is a rare condition and it is just reported in 5% of 600 registered RDD cases. In previously reported patients, the intradural extramedullary spinal lesion is extremely rare.
Farid Kazemi Gazik, Peyman Gookizadeh, Masoud Khadivi, Ali Zare Mehrjardi, Arad Iranmehr   +4 more
doaj   +1 more source

Rosai-Dorfman Disease Originating from Nasal Septal Mucosa

Case Reports in Otolaryngology, 2015
Rosai-Dorfman disease is a rarely seen disease with unknown etiology. Extranodal involvement is most commonly seen in the head and neck region. Histopathologically, it is characterized by histiocytic cell proliferation. This paper presents a case of a 15-
Abdulvahap Akyigit, Hadice Akyol, Oner Sakallioglu, Cahit Polat, Erol Keles, Ozkan Alatas   +5 more
doaj   +1 more source

A Rare Case of Primary Intraparenchymal Rosai‐Dorfman Disease

iRADIOLOGY, Volume 3, Issue 5, Page 370-371, October 2025.
Lin Chen, Rui Zhou
wiley   +1 more source