Results 41 to 50 of about 4,871,906 (165)

Giant intracranial Rosai-Dorfman disease

, 2004
Rosai-Dorfman disease is a rare, non-neoplastic disease characterized by an unusual proliferation of histiocytic cells. It rarely manifests intracranially, and only 50 cases of intracranial lesions have been reported.
BOZKURT, SÜHEYLA
core   +1 more source

Graft‐Versus‐Tumour Effect Following Allogeneic Haematopoietic Stem Cell Transplantation in a Paediatric Patient With Mogamulizumab‐Treated Primary Cutaneous Peripheral T‐Cell Lymphoma

eJHaem, Volume 7, Issue 5, October 2026.
ABSTRACT Introduction Primary cutaneous peripheral T‐cell lymphoma, not otherwise specified (pcPTCL‐NOS), is exceptionally rare in children, and evidence guiding diagnosis and treatment is limited. Case Presentation A 10‐year‐old boy with pcPTCL‐NOS refractory to chemotherapy received mogamulizumab prior to allogeneic haematopoietic stem cell ...
Maria Ebbesen Sørum, Tania Masmas, Hilde Uhlving, Lene D. Sjö, Signe Modvig, Hanne V. Marquart, Lone Skov, Lisa Hjalgrim, Marianne Ifversen, Peter Pontoppidan   +9 more
wiley   +1 more source

Rosai-Dorfman disease with diffuse gastrointestinal involvement

, 2013
Rosai-Dorfman disease, formerly known as sinus histiocytosis with massive lymphadenopathy', is a rare self-limiting histiocytic proliferative disorder typically presenting early in life with cervical lymphadenopathy and nonspecific systemic symptoms ...
Nalcaci, Meliha, Dogan, Oner, Karaca, Cetin, Cakmak, Ramazan, Isiklar, Aysun D., Kaymakoglu, Sabahattin, Yonal, Ipek, Baran, Bulent, Soyer, Ozlem M.   +8 more
core   +1 more source

Targeted proteomics reveal histiocytosis‐associated neurodegeneration signatures

HemaSphere, Volume 10, Issue 9, September 2026.
Abstract Neurodegeneration (ND) is a severe complication of Langerhans cell histiocytosis (LCH), yet its underlying biology and reliable biomarkers remain poorly defined. The aim of this study was to (1) gain insight into neuroimmunological mechanisms governing ND and (2) assess the clinical value of established and novel biomarkers for ND‐LCH.
Egle Kvedaraite, Magda Lourda, Johannes Bastiaan Munting, Matthias Papo, Martin Jädersten, Yoko Shioda, Kenichi Sakamoto, Daniel Martín Muñoz, Panagiotis Andriopoulos, Francesco Pegoraro, Evaldas Laurencikas, Ingrid Kühnle, Joakim Wille, Leonie Naeije, Helena Olkinuora, Indranil Sinha, Daniel W. Hagey, Selma Olsson‐Åkefeldt, Fleur Cohen‐Aubart, Gustaf Österlundh, Mattias Svensson, Ahmed Idbaih, Fredrik Piehl, Kaj Blennow, Henrik Zetterberg, Tatiana Greenwood von Bahr, Désirée Gavhed, Akira Morimoto, Julien Haroche, Jan‐Inge Henter   +29 more
wiley   +1 more source

Rosai-dorfman disease: A rare entity in eastern India

, 2022
Rosai-dorfman disease is a very rare disease. It is first time reported in Odisha, in IMS and SUM Hospital, Bhubaneswar. After all necessary investigations, Clinicians came to conclude that it's Rosai-dorfman disease also known as sinus histiocytosis ...
Dr. Sandeep Kumar Ratha, Sumita Sharma
core   +1 more source

Scleritis and anterior uveitis may herald the development of an epibulbar tumor in patients with extranodal Rosai-Dorfman disease: a case report

BMC Ophthalmology, 2019
Background Rosai-Dorfman disease is a rare non–Langerhans cell histiocytosis. Ocular involvement is even rarer, mostly involving the orbit and eyelids, although marginal corneal ulcers, uveitis, and epibulbar masses have also been reported, and is ...
Yu-Kuei Lee, Sheau-Chiou Chao, Chaw-Ning Lee, Jia-Horung Hung   +3 more
doaj   +1 more source

Rosai-Dorfman disease of the lung.

, 2009
Rosai-Dorfman disease is a rare disorder which seems to involve not only the lymph nodes but most other organs of the body. The case history is presented of a woman who was thought to have atypical carcinoma of the lung but in whom a diagnosis of Rosai ...
Ali, A, Mackay, D
core   +1 more source

Histiocytosis development and clinical variation through the lens of genomics

The Journal of Pathology, Volume 270, Issue 1, Page 23-39, September 2026.
Abstract Histiocytic neoplasms are rare haematologic diseases characterised by clonal expansions of cells with a monocyte, macrophage or dendritic cell phenotype. Their clinical manifestations are diverse, ranging from indolent lesions to aggressive systemic disease.
Paul G Kemps, Astrid GS van Halteren, Tom van Wezel, Pancras CW Hogendoorn   +3 more
wiley   +1 more source

Progress in diagnosis and treatment of osseous Rosai-Dorfman disease

Zhongguo aizheng zazhi, 2019
Sinus histiocytosis with massive lymphadenopathy, also known eponymously as Rosai-Dorfman disease, is a rare disease that is defined as a self-limiting proliferation of non-Langerhans histiocytes.
卫愉轩, 董　扬
doaj  

Rosai-Dorfman disease with pulmonary involvement mimicking bronchogenic carcinoma

Journal of Cardiothoracic Surgery, 2020
Background Rosai-Dorfman disease is a histiocytic lesion that affects lung rarely. Case presentation We present a 52-year-old female diagnosed with right intrabronchial mass invading the bronchial wall and the extrabronchial tissues with lymphadenopathy.
Haneen Al-Maghrabi, Ahmed Elmahrouk, Maun Feteih, Ahmed Jamjoom, Jaudah Al-Maghrabi   +4 more
doaj   +1 more source