Results 41 to 50 of about 16,762 (226)
Efficacy of stiripentol, fenfluramine, and their combination on clinical outcomes in Dravet syndrome: A preliminary report
Epilepsia Open, EarlyView.Abstract Objective
Stiripentol and fenfluramine are approved treatments for Dravet syndrome (DS), but real‐world data comparing their effectiveness and combined use remain limited. Our study aims to explore associations between treatment with stiripentol, fenfluramine, and their combination and clinical outcomes in patients with DS.Paolo Surdi, Marina Trivisano, Mattia Mercier, Nicola Pietrafusa, Angela De Dominicis, Costanza Calabrese, Simona Cappelletti, Nicola Specchio +7 morewiley +1 more sourceElectronic Devices and Digital Therapeutics in Neuromuscular Diseases: Narrative Review on Current Applications in Patients' Management and Pharmacovigilance
Health Care Science, EarlyView.Digital innovations are revolutionizing neuromuscular disease management by integrating wearable sensors, mobile applications, and telemedicine to enable continuous monitoring and personalized care. These technologies enhance diagnosis, treatment, and drug development fostering dynamic interaction between patients and clinicians paving the way toward ...Ilaria Saltarella, Concetta Altamura, Paola Laghetti, Giuseppina Settanni, Nicola Savino, Angelo Galiano, Bodvaël Fraysse, Angelo Vacca, Jean‐François Desaphy +8 morewiley +1 more sourceMechanical axis correction after total knee arthroplasty alters ankle alignment but does not affect ankle function
Knee Surgery, Sports Traumatology, Arthroscopy, EarlyView.Abstract Purpose
Total knee arthroplasty (TKA) restores knee function, but correction of coronal plane deformities may alter the biomechanics of adjacent joints. This study aimed to determine whether changes in knee alignment after TKA have clinical or radiological effects on the ankle.Alba Portes‐Chiva, Ana Soria‐Blázquez, Pedro Hinarejos, Raul Torres‐Claramunt, Simone Perelli, Juan‐Francisco Sánchez‐Soler, Alberto Ginés‐Cespedosa, Juan‐Carlos Monllau +7 morewiley +1 more sourceTiming of Deep Brain Stimulation and Cognitive Trajectories in GBA1‐Associated Parkinson's Disease
Movement Disorders, EarlyView.Abstract Background
Individuals with Parkinson's disease (PD) carrying GBA1 variants often develop advanced motor complications that prompt evaluation for deep brain stimulation (DBS). However, concerns about accelerated cognitive decline after DBS in GBA1 carriers complicate clinical decision making.Evridiki Asimakidou, Micol Avenali, Jan O. Aasly, Mitra Afshari, Roy N. Alcalay, Sharlet Anderson, Carlo Alberto Artusi, Bryan Bernard, Marco Bozzali, Susan Bressman, Giovanna Calandra‐Buonaura, Francesco Cavallieri, Roberto Cilia, Jean‐Christoph Corvol, Antoniangela Cocco, Rob M.A. de Bie, Debra Ehrlich, Roberto Eleopra, Thomas Foltynie, Alessio Di Fonzo, Giulia Giannini, Christopher Goetz, Deborah Hall, Joohi Jimenez‐Shahed, Leonardo Lopiano, Vanessa Lythe, Maria Chiara Malaguti, Francesca Mameli, Graziella Mangone, Karen Marder, M. Maral Mouradian, Augusto Rini, Luisa Sambati, Rachel Saunders‐Pullman, Vicki Lynn Shanker, Francesca Spagnolo, Marie‐Laure Welter, Roberta Zangaglia, Gian Pal, Enza Maria Valente, PARKNET Study Group, Giada Cuconato, Ilaria Palmieri, Alberto Imarisio, Pierfrancesco Mitrotti, Francesca Valentino, Claudio Pacchetti, Gabriele Imbalzano, Claudia Ledda, Silvia Gallo, Pietro Cortelli, Luca Baldelli, Ilaria Cani, Raffaella Minardi, Valerio Carelli, Franco Valzania, Edoardo Monfrini, Filippo Cogiamanian, Chiara Longo, Fabiana Colucci, Luigi M. Romito, Marco Liccari +61 morewiley +1 more sourceSoil health assessment using buried cotton underpants with the help of 1000 citizen scientists
PLANTS, PEOPLE, PLANET, EarlyView.Soil is a vital resource for life on Earth. Although many soils are degraded, societal awareness of soil‐related issues is limited. To highlight soil as a key resource and fascinating study system, we initiated a citizen science project together with 1000 participants investigating soil health across Switzerland using buried cotton underpants.S. Franz Bender, Diane Bürge, Luca Bragazza, Eva Knop, Sandie Masson, Noemi Peter, Romina Demarmels, Daniel Mueller, Ariane Imhof, Pia Viviani, Atlant Bieri, Frank Liebisch, Stefan Geisen, Yann Hautier, Panos Panagos, Pablo Garcia‐Palacios, Marta Goberna, David Johnson, Simon Jöhr, Alain Valzano‐Held, Claudia Weik, Nadine Gloor, Heidi Aguilar, Marco Agustoni, Barbara Albertoni, Regina Anderson, Alberto Andreani, Bénédicte Arguillère, Osvaldo Arrigo, Barbara Auer, Vanessa Badà, Brigitte Baenteli, Gaëlle Balleys, Dagmar Bay, Daniel Beck, Martina Becker, Alma Bender‐Freisinger, Sarah Benoit, Barbara Bernasconi, Chiara Bernasconi, Marco Bertschinger, Michael Bessard, David Bichsel, David Bichsel, Matteo Binda, Joel Bischof, Ruth Bischof, Bernadette Bisig, Andreas Bitterli, Natacha Bodenhausen, Yann Bonjour, Lucien Bovy, Tanja Boyandin, Eliane Breitenmoser, Christian Brönimann, Nathalie Brückner, Marcel Bucher, Stefan Bucher, Andreas Cadonau, Simone Cairoli, Elodie Calais, Bruno Campana, Catrina Canetta Collenberg, Davide Carrara, Cristian Cattaneo, Ester‐Camilla Cattaneo, Renzo Cattori, Silvana Cavagna, Luciano‐Grazia Cavallini, Elio Cavargna, Laura Cerri, Marlis Chanton, Camilla Chiesa, Elisabeth Clément, Morgane Clivaz‐Duc, Léonie Cocquio, Helio Correia, Cristina Corti, Stefano Corti, Fabien Dauphin, Annette Délétroz, Nicola Della Casa, Francesco Denova, Yannick Ducommun, Jacques Dugon, Monique Duplan, Lisa Ehrler, Bruno Enz, Philipp Fässler, Alain Favre, Urs Fellmann, Nadine Fischer, Serge Fischer, Johann‐Peter Flisch, Franklyn Foresti, Paola Frapolli, Simon Freiburghaus, Edie Freisinger, Peter Gamper, Agnes‐Julia Geissberger, Frères Girardin, Stephan Goppel, Fabiana Greco, Ueli Grossniklaus, Gabriela Grubenmann, Marc‐Henri Guex, Urs Hähni, Martina Haller, Gerhard Hardegger, Kyle Hartman, Anastase Hategekimana, Regula Hegglin, Matteus Heiter, Andreas Hellwig, Sandra‐John Hemsley, Chantal Herzog, Stephan Herzog, Ruedi Hess, Werner Hilber, Sarah‐Lea Hipp, Jolanda Hofmann, Mirjam Hofmann, Thomas Holdener, Mischa Hug, Erol Incesu, Sebastian Ineichen, David Iten, Regula‐Christoph Jakob, Peter Jann, Salomé‐David Jantz Bröckelmann, Markus Jocher, Simon Jöhr, Jasmin Joshi, Andreas Jud, Corinne Jud, Beatrice Jung, Daniel Jutzi, Walter Käch, Franziska‐Oli Kägi, Franziska Kaguembega‐Müller, Antonia Kaiser, Lukas Kammermann, Andreas Katz, Pirmin Kneubühler, Janique Koller, Eva Kollmann, Michèle Kraiem, Markus Künzler, Laura Kuonen, David Küttel, Romeo Ladina, Gabriella Lakatos, Anna Lazzarotto, Jean Lebedeff, Manuela Leonardi, Paola Leonardi, Simone Leoni, Eric Leuenberger, Corinne Lüthi, Sari Manaa, Simonetta Mauri, Harald Menzi, Vincenzo‐Corinne Meroni Held, Stephan Meyer, Stéphan Meylan, Matteo Minotti, Paola Molinari, Fabiola Monigatti, Vinciane Monod, Andrea Moroni‐Stampa, Jürg Moser, Res Moser, Alain Müller, Balz Müller, Laurence Müller, Nathalie Nevo, Stefan Odermatt, Lucia Oertle, Sandra Ott, Sébastien Oulevey, Ania Hans‐Peter Padrutt, Manuela Paltenghi, Nadia Paltenghi, Anna Parathazham, Nicolas Pavillard, Cesare Sonia Pedrazzini Giussani, Barbara Loris Pedroia, Alicia Perego, Paola Paolo Pieracci Cestari, Luisa Poggi, Mirko Ponti, Laurence Pot, Pierre‐Antoine Preti, Brice Prudat, Lina Rasheed, Dominique Raphael Reichenbach, Etienne Reichenbach, Beat Reidy, Ruedi Riniker, Chantal Ritter Cochand, Katharina Ritter, Julien Rondez, Fabien Roth, Adrian Rubi, Nicolas Ruch, Nicla‐Alex‐Mia‐Zoe‐Febe Rusca, Mirjam Rust, Erminia Salvi Knobloch, Alberto Sassella, Anke Schäfer, Beat Schär, Sabine Schärer, Patric Schatzmann, Belinda Schegg, Joël Scheidegger, Klaus Schläppi, Judith Schlegel, Marisa Schnüriger, Toni Schönbächler, Jürg Schönholzer, Coni Schweizer, Eugenio Scozzafava, Caroline Serafini, Tina Siegenthaler, Claudio Signer, Dustin Singer, Iris Solothurnmann, Rolf Sonderegger, Stefanie R. Spycher, Mirjam Stähli, Jean‐Pierre Stefanelli, Katja Stucki, Valentina Tanzi, Christina Thalmann, Sylvia Tiercy, Valentina Togni, Mathias Tönz, Paul Trachsel, Dino Troncatti, Pirmin‐Fredy Umbricht, Claude Valloton, Alexander van der Heijden, Liev van Moorsel, Sofia van Moorsel, Thea van Woerkom, Claude Varin, Manuela Villa‐Petraglio, Christophe Viltard, Florian Vogelsanger, Adrian von Niederhäusern, Barbara Walther, Jocelyn Widmer, Gianna Wullschleger, Thomas Würms, Thomas Wüthrich, Anita Zulliger, Renatus C. Zürcher, Thomas D. Bucheli, Marcel G. A. van der Heijden +258 morewiley +1 more sourceThe Doctrine of State Necessity
The Modern Law Review, EarlyView.This article examines the doctrine of state necessity as a distinct but relatively underexplored doctrine of constitutional law. Drawing on case law from a range of jurisdictions, it considers instances in which courts have accepted otherwise unconstitutional measures as lawful in order to preserve the operation of state institutions or protect ...Athanasios Peftinaswiley +1 more sourceArt v 1 and Amb a 4 Co‐Sensitization Identifies Italian Patients at Risk for Mugwort‐Celery‐Spice Syndrome
Allergy, EarlyView.Three molecular profiles identified among Art v 1/Amb a 4‐sensitized patients: Art v 1 monosensitization, Amb a 4 monosensitization, and dual sensitization to both allergens. Art v 1 monosensitization was predominantly associated with allergic rhinitis, reflecting a classical airborne allergy pattern.Enrico Scala, Gabriella Cusa, Valeria Villella, Damiano Abeni, Mauro Giani, Emma Cristina Guerra, Maria Locanto, Giorgia Meneguzzi, Lia Pirrotta, Donato Quaratino, Alessandra Zaffiro, Elisabetta Caprini, Maria Barrale, Ignazio Brusca, Valerio Pravettoni, Lorenzo Cecchi, Danilo Villalta, Martina Aumayr, Irene Mittermann, Christian Lupinek, Riccardo Asero +20 morewiley +1 more source