Scleroderma Renal Crisis in a Case of Mixed Connective Tissue Disease Treated Successfully with Angiotensin-Converting Enzyme Inhibitors [PDF]
Mixed connective tissue disease (MCTD) is a rheumatic disease syndrome with overlapping features of scleroderma, systemic lupus erythematosus, and polymyositis. An extremely rare but serious complication that can occur in MCTD is scleroderma renal crisis
Jomana Madieh+4 more
doaj +2 more sources
De novo normotensive scleroderma renal crisis six years after living-donor renal transplantation in a patient with overlapping systemic sclerosis/systemic lupus erythematosus syndrome: a case report [PDF]
Background Scleroderma renal crisis (SRC) is a critical kidney involvement of systemic sclerosis (SSc), often resulting in end-stage renal disease. Although the recurrence of SRC in the allograft has been reported, the development of de novo SRC after ...
Hajime Sanada+12 more
doaj +2 more sources
Eculizumab Use in Scleroderma Renal Crisis With Thrombotic Microangiopathy: A Case Report [PDF]
A Black woman in her 40s with past medical history significant for obesity treated with Roux-en-Y bypass surgery and a history of Raynaud’s phenomenon, presented with acute pulmonary edema secondary to severe malignant hypertension and critically ...
Claire Trivin-Avillach+4 more
doaj +2 more sources
Scleroderma Renal Crisis Associated With Microangiopathic Hemolytic Anemia in a Patient With Seronegative Scleroderma and Monoclonal Gammopathy [PDF]
Systemic sclerosis with negative serology, particularly that complicated by scleroderma renal crisis (SRC), is rarely encountered. We describe a patient with seronegative systemic sclerosis who developed acute kidney injury, proteinuria, and hypertensive
Mark Riley DO+8 more
doaj +2 more sources
Scleroderma renal crisis in a case of mixed connective tissue disease
Mixed connective tissue disease (MCTD) is an overlap syndrome first defined in 1972 by Sharp et al. In this original study, the portrait emerged of a connective tissue disorder sharing features of systemic lupus erythematosus, systemic sclerosis ...
Mukul Vij, Vinita Agrawal, Manoj Jain
doaj +2 more sources
Systemic sclerosis medications and risk of scleroderma renal crisis [PDF]
Background Scleroderma Renal Crisis (SRC) is associated with significant morbidity and mortality. While prednisone is strongly associated with SRC, there are no previous large cohort studies that have evaluated ace inhibitor (ACEi) calcium channel ...
S. M. Gordon+7 more
doaj +2 more sources
Scleroderma renal crisis with posterior reversible encephalopathy syndrome [PDF]
Gang Wang+4 more
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The dilemma: scleroderma renal crisis vs lupus nephritis in a patient with mixed connective tissue disorder. [PDF]
Jackson N+4 more
europepmc +2 more sources
Role of C5 inhibition in Idiopathic Inflammatory Myopathies and Scleroderma Renal Crisis-Induced Thrombotic Microangiopathies. [PDF]
Gouin A+10 more
europepmc +3 more sources
Autoantibodies from Patients with Scleroderma Renal Crisis Promote PAR-1 Receptor Activation and IL-6 Production in Endothelial Cells. [PDF]
Simon M+9 more
europepmc +3 more sources