Results 41 to 50 of about 49,572 (98)

Liver Transplantation for Alagille's Syndrome [PDF]

, 1993
Twenty-three children with Alagille's syndrome and end-stage liver disease underwent liver transplantation with cyclosporine and low-dose steroid immunosuppression. Two to 9 years (mean, 4.4 years) after surgery, 13 (57%) of the children were still alive,
Reyes, J, Starzl, TE, Tepetes, K, Todo, S, Tzakis, AG, Tzoracoleftherakis, V   +5 more
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Abnormal septal convexity into the left ventricle occurs in subclinical hypertrophic cardiomyopathy. [PDF]

, 2015
BACKGROUND: Sarcomeric gene mutations cause hypertrophic cardiomyopathy (HCM). In gene mutation carriers without left ventricular (LV) hypertrophy (G + LVH-), subclinical imaging biomarkers are recognized as predictors of overt HCM, consisting of ...
Anna S. Herrey, Arthur Nasis, B Gray, B Johansson, BJ Maron, BJ Maron, Charlotte Manisty, CM Kramer, CY Ho, CY Ho, CY Ho, CY Ho, Daniel M. Sado, DP Deva, G Captur, Gabriella Captur, GR Abecasis, HM Lever, I Christiaans, J Binder, James C. Moon, JC Moon, JM Bland, JM Bos, JM Bos, K Alfakih, K Inoue, KJ Silverman, LR Lopes, LR Lopes, Maite Tome-Esteban, Mariana Mirabel, MS Maron, MS Maron, P Charron, P Marchal, Patricia Reant, Perry M. Elliott, Petros Syrris, R Martin, RA Noureldin, RM Lang, SD Solomon, Sharon Jenkins, Silvia Castelletti, T Konno, Viviana Maestrini, William J. McKenna, WJ McKenna   +48 more
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Pattern and degree of left ventricular remodeling following a tailored surgical approach for hypertrophic obstructive cardiomyopathy. [PDF]

, 2012
Background The role of a tailored surgical approach for hypertrophic cardiomyopathy (HCM) on regional ventricular remodelling remains unknown. The aims of this study were to evaluate the pattern, extent and functional impact of regional ventricular ...
Cecchi, F, El Guindy, A, El-Hamamsy, I, Lekadir, K, Merrifield, R, Olivotto, I, Rega, L, Yacoub, MH, Yang, G   +8 more
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Non-infectious pulmonary complications of hematopoietic stem cell transplantation [PDF]

, 2014
Noninfectious pulmonary complications of hematopoietic stem cell transplant are currently more prevalent than infectious complications. Unfortunately, the pathophysiology basis is not completely understood.
Baloglu, Orkun, McArthur, Jennifer, Rowan, Courtney   +2 more
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Association between noninvasive fibrosis markers and cardio-vascular organ damage among adults with hepatic steatosis [PDF]

, 2014
Evidence suggests that advanced fibrosis, as determined by the noninvasive NAFLD fibrosis score (NFS), is a predictor of cardiovascular mortality in individuals with ultrasonography-diagnosed NAFLD. Whether the severity of histology (i.e., fibrosis stage)
Fiorentino, Tv, Perticone, F, Perticone, M, Sciacqua, A, Sesti, G, Succurro, E   +5 more
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Loss of muscleblind-like 1 results in cardiac pathology and persistence of embryonic splice isoforms. [PDF]

, 2015
Cardiac dysfunction is a prominent cause of mortality in myotonic dystrophy I (DM1), a disease where expanded CUG repeats bind and disable the muscleblind-like family of splice regulators.
Choi, Jongkyu, Comai, Lucio, Dixon, Donald M, El-Ghazali, Ayea, Fishbein, Michael C, Jordan, Maria C, Park, Sun Young, Reddy, Sita, Roos, Kenneth P   +8 more
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Cardiovascular features of possible autonomous cortisol secretion in patients with adrenal incidentalomas [PDF]

, 2018
Background: Low-grade incomplete post-dexamethasone cortisol suppression in patients with adrenal incidentalomas – recently defined as possible autonomous cortisol secretion (pACS) – has been associated with increased cardiovascular events and mortality.
Di Giorgio, Maria Rosaria, D’Aluisio, Denise, Giannetta, Elisa, Isidori, Andrea M., Lenzi, Andrea, Minnetti, Marianna, Morelli, Sergio, Pofi, Riccardo, Rizza, Laura, Sbardella, Emilia, Venneri, Mary Anna, Vestri, Annarita, Vinci, Fabio   +12 more
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99mTc-MIBI Lung Scintigraphy in the Assessment of Pulmonary Involvement in Interstitial Lung Disease and Its Comparison With Pulmonary Function Tests and High-Resolution Computed Tomography: A Preliminary Study [PDF]

, 2015
The differentiation of active inflammatory processes from an inactive form of the disease is of great value in the management of interstitial lung disease (ILD).
Assadi, M., Bahtouee, M., Eftekhari, M., Javadi, H., Nabipour, I., Raeisi, A., Saberifard, J.   +6 more
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Cardiopulmonary assessment of patients with systemic sclerosis for hematopoietic stem cell transplantation: recommendations from the European Society for Blood and Marrow Transplantation Autoimmune Diseases Working Party and collaborating partners. [PDF]

, 2017
Systemic sclerosis (SSc) is a rare disabling autoimmune disease with a similar mortality to many cancers. Two randomized controlled trials of autologous hematopoietic stem cell transplantation (AHSCT) for SSc have shown significant improvement in organ ...
A Gabrielli, A-L Hachulla, AJ Tyndall, B Sandmeier, BH Bulkley, C Denton, C Ferri, C Meune, C Meune, C Nannini, CJ Valerio, CS Desai, D C Lee, D Farge, D Farge, D G Kiely, D Launay, D Mukerjee St, DC Lee, DG Kiely, DP Tashkin, E Di Cesare, E Hachulla, E Mousseaux, F Grothues, F van den Hoogen, G Lefèvre, GE Tzelepis, GP Bezante, H Baumgartner, J A Snowden, J Avouac, J de Vries-Bouwstra, J Fransen, J Hurdman, JA Snowden, JC Plana, JD Rich, JG Coghlan, JM van Laar, JPA Ioannidis, JS Arkles, KH Yiu, L Chung, L Scussel-Lonzetti, LG Rudski, M Elhai, M Henein, M Rovira, M-C Oliveira, MC Oliveira, MH Williams, MR Fisher, N Del Papa, N Galiè, NAB Ntusi, P Clements, P de Groote, R Condliffe, R K Burt, R Saccardi, R Saccardi, RA Nishimura, RK Burt, RK Burt, RK Burt, RT Domsic, S Bae, S J Shah, S Jacobsen, S Mavrogeni, SC Mathai, SD Solomon, SJ Shah, SJ Shah, SLF Walsh, T Alexander, T Alexander, WA D’Angelo, WA Zoghbi, Y Allanore, Z Marjanovic   +81 more
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Mineralocorticoid Receptor Blockade Attenuates Chronic Overexpression of the Renin-Angiotensin- Aldosterone System Stimulation of Reduced Nicotinamide Adenine Dinucleotide Phosphate Oxidase and Cardiac Remodeling [PDF]

, 2007
doi: 10.1210/en.2006-1691The renin-angiotensin-aldosterone system contributes to cardiac remodeling, hypertrophy, and left ventricular dysfunction. Angiotensin II and aldosterone (corticosterone in rodents) together generate reactive oxygen species (ROS)
Appesh, Lama, Cooper, Shawna A., Ferrario, Carlos M., Habibi, Javad, 1947-, Hay, Meredith, Hayden, Melvin, Karuparthi, Poorna R., Link, C. Daniel, Morris, E. Matthew, Qazi, Mahnaz, Sowers, James R. (James Russell), 1942-, Stas, Sameer, Stump, Craig, Whaley-Connell, Adam T.   +13 more
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