Results 101 to 110 of about 11,396 (179)

Differentiation of Prions from L-type BSE versus Sporadic Creutzfeldt-Jakob Disease

Emerging Infectious Diseases, 2012
We compared transmission characteristics for prions from L-type bovine spongiform encephalopathy and MM2-cortical sporadic Creutzfeldt-Jakob disease in the Syrian golden hamster and an ovine prion protein–transgenic mouse line and isolated distinct prion
Simon Nicot, Anna Bencsik, Eric Morignat, Nadine Mestre-Francés, Armand Perret-Liaudet, Thierry Baron   +5 more
doaj   +1 more source

Cerebrospinal fluid biomarker supported diagnosis of Creutzfeldt-Jakob disease and rapid dementias:a longitudinal multicentre study over 10 years [PDF]

, 2012
To date, cerebrospinal fluid analysis, particularly protein 14-3-3 testing, presents an important approach in the identification of Creutzfeldt–Jakob disease cases.
Aguzzi, Adriano, Calero, Miguel, Gawinecka, Joanna, Green, Alison, Karch, Andre, Knight, Richard, Kulczycki, Jerzy, Ladogana, Anna, Laplanche, Jean-Louis, Mitrova, Eva, Peoc'h, Katell, Pocchiari, Maurizio, Saiz, Albert, Sanchez-Juan, Pascual, Sanchez-Valle, Raquel, Schelzke, Gabi, Sklaviadis, Theodor, Slivarichova, Dana, Stoeck, Katharina, van Duijn, Cornelia M., Zerr, Inga   +20 more
core   +1 more source

Neuroimaging of vacuolar tauopathy: Response to letter

Alzheimer's &Dementia, Volume 21, Issue 10, October 2025.
Ryohei Watanabe, John D. Papatriantafyllou, Kengo Maeda, Ilya M. Nasrallah, Edward B. Lee   +4 more
wiley   +1 more source

High sensitivity of an ELISA kit for detection of the gamma-isoform of 14-3-3 proteins: usefulness in laboratory diagnosis of human prion disease [PDF]

, 2011
Background The gamma-isoform of the 14-3-3 protein (14-3-3 gamma) is expressed in neurons, and could be a specific marker for neuronal damage.
Yuki Matsui, Katsuya Satoh, Toshiaki Miyazaki, Susumu Shirabe, Ryuichiro Atarashi, Kazuo Mutsukura, Akira Satoh, Yasufumi Kataoka, Noriyuki Nishida   +8 more
core   +1 more source

MRI and clinical syndrome in dura materrelated Creutzfeldt-Jakob disease [PDF]

, 2018
Objective : Iatrogenic Creutzfeldt-Jakob disease (iCJD) is mainly associated with dura mater (DM) grafts and administration of human growth hormones (hGH). Data on disease course in DM-CJD are limited.
Barsic, B., Eigenbrod, S., Gelpi, E., Heinemann, U., Kallenberg, K., Knauth, M., Krasnianski, A., Kretzschmar, H., Meissner, B., Ramljak, S., Sanchez-Juan, P., Schulz-Schaeffer, W., Zerr, I.   +12 more
core  

Sporadic cjd and retinitis punctata albescansa case report and literature review [PDF]

, 2014
Introduction Sporadic Creutzfeldt-Jakob disease (sCJD) is the most common form of CJD causing 85% of all cases. Various phenotypes of sCJD have been identified including Heidenhain variant which has early and predominant visual symptoms with most ...
Hanif Khan, Yusra, Khan, Quratulain
core   +1 more source

Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease [PDF]

, 2017
To validate the provisional findings of a number of smaller studies and explore additional determinants of characteristic diagnostic investigation results across the entire clinical spectrum of sporadic Creutzfeldt-Jakob disease (CJD), an international ...
Almonti, S., Alpérovitch, A., Brandel, J.-P, Budka, H., Collins, S. J., Cuadrado-Corrales, N., de Pedro-Cuesta, J., Gelpi, E., Glatzel, M., Heinemann, U., Hewer, E., Jansen, G. H., Klug, G. M., Kretszchmar, H. A., Mackenzie, J., Masters, C. L., Mitrova, E., Murray, K., Olsen, E., Pocchiari, M., Poleggi, A., Sanchez-Juan, P., Tolnay, M., van Duijn, C., Will, R. G., Zerr, I.   +25 more
core  

Heightened incidence of sporadic Creutzfeldt-Jakob disease is associated with a shift in clinicopathological profiles [PDF]

, 2018
: Incidences of human transmissible spongiform encephalopathies are monitored by national registries in the majority of countries in Western Europe. During the past 13 years incidences for Creutzfeldt-Jakob disease (CJD) in Switzerland fluctuated between
Aguzzi, Adriano, Amsler, Lorenz, Eckert, Tobias, Glatzel, Markus, Hess, Klaus, Stoeck, Katharina, Zimmermann, Dieter   +6 more
core  

Oxidative and Inflammatory Events in Prion Diseases: Can They Be Therapeutic Targets? [PDF]

, 2019
Prion diseases are a group of incurable infectious terminal neurodegenerative diseases caused by the aggregated misfolded PrPsc in selected mammals including humans.
Bondy, Stephen C, Prasad, Kedar N
core  

Chorea in Sporadic Creutzfeldt-Jakob Disease [PDF]

Journal of Movement Disorders, 2018
Ai Huey Tan, Tsun Haw Toh, Soon Chai Low, Si Lei Fong, Kah Kian Chong, Kee Wei Lee, Khean Jin Goh, Shen-Yang Lim   +7 more
doaj   +1 more source