Results 171 to 178 of about 1,764 (178)
Some of the next articles are maybe not open access.
Electrochemical Behavior and Determination of Succinylacetone in Amniotic Fluid
Succinylacetone (SA, 4,6 diketoheptanoic acid) is the primare diagnosis metabolite for hereditable hepatorenal tyrosinemia type I disease. In present researh, voltammetric analysis of succinylacetone was aimed. The optimum conditions for voltammetry were determined. Optimum conditions for voltammetry were determined.Karacan, Saadet Meral +2 more
openaire +1 more source
2022
Background: Nitisinone is the potent inhibitor of 4-hydroxyphenylpyruvic acid dioxygenase and is the only effective therapy of tyrosinemia type I with tyrosine restricted diet. The use of nitisinone provides a rapid decrease in succinylacetone concentrations, an increase in tyrosine, and a marked clinical improvement in most patients.
Öktem, Rıdvan Murat +5 more
openaire +1 more source
Background: Nitisinone is the potent inhibitor of 4-hydroxyphenylpyruvic acid dioxygenase and is the only effective therapy of tyrosinemia type I with tyrosine restricted diet. The use of nitisinone provides a rapid decrease in succinylacetone concentrations, an increase in tyrosine, and a marked clinical improvement in most patients.
Öktem, Rıdvan Murat +5 more
openaire +1 more source
Effect of succinylacetone administration on brain heme metabolism and behavior in mice
Biochemical Pharmacology, 1987K, Kang +2 more
openaire +2 more sources
GC‐MS identification of urinary succinylacetone in two cases of hereditary tyrosinaemia
Journal of Inherited Metabolic Disease, 1982P. Divry +4 more
openaire +1 more source
["Succinylacetone effect' after oral homogentisate loading].
L'union medicale du Canada, 1981C, Laberge +3 more
openaire +1 more source