Results 71 to 80 of about 54,606 (240)
Development of the autoinflammatory disease damage index (ADDI) [PDF]
OBJECTIVES: Autoinflammatory diseases cause systemic inflammation that can result in damage to multiple organs. A validated instrument is essential to quantify damage in individual patients and to compare disease outcomes in clinical studies.
Al-Mayouf, SM +48 more
core +6 more sources
Childhood Pseudoxanthomatousmastocytosis; Report of two cases
Cutaneous mastocytosis (CM) is a mast cell proliferative disorder that commonly affects pediatric population. It has various clinical forms such as urticaria pigmentosa, solitary mastocytoma, telangiectasia macularis eruptiva perstans, diffuse CM, and ...
Bhabani S. T. P. Singh +3 more
doaj +1 more source
Summary Systemic mastocytosis (SM) is a rare haematological neoplasm associated with the gain of function mutation KIT D816V in 90% of adult patients. Classically, cytogenetic aberrations are not common except in cases of SM associated with another haematological neoplasm.
Signy Chow +5 more
wiley +1 more source
A mastocitose é caracterizada pelo acúmulo patológico e ativação de mastócitos nos tecidos e órgãos. Embora a classificação da mastocitose e seus critérios diagnósticos sejam bem aceitos, há necessidade de estabelecer parâmetros para aplicação de testes ...
Luciana Cirillo Maluf +2 more
doaj +1 more source
Erhöhte basale Serumtryptasekonzentration oder Mastozytose als Risikofaktor der Hymenopterengiftallergie Leitlinie der Deutschen Gesellschaft für Allergologie und Klinische Immunologie (DGAKI) (AWMF-Leitlinie 061/018) [PDF]
Hymenopterengift-allergische Patienten mit Mastzellerkrankung, das heißt Mastozytose und/oder erhöhtem basalen Serumtryptasespiegel, haben ein hohes Risiko schwerer, lebensbedrohender Stichreaktionen.
Jarisch, Reinhart +3 more
core
Research hotspots in urticaria: A bibliometric study of the top 100 most cited articles
Abstract Background and Purpose Urticaria is a prevalent recurrent skin allergic condition. Severe itching significantly impacts patients' quality of life. This paper aims to investigate the development status of urticaria through bibliometric analysis to predict future research hotspots and trends.
Tingting Fu +7 more
wiley +1 more source
Scabies mimicking mastocytosis in two infants
Scabies is a common parasitic human infection in infants and children. However, diagnostic pitfalls are frequent in infants, in whom the clinical presentation is usually atypical and different from that in adults.
Emine Cölgeçen-Özel +3 more
doaj
Abstract YPEL2 is a member of the evolutionarily conserved YPEL family involved in cellular proliferation, mobility, differentiation, senescence, and death. However, the mechanism by which YPEL2, or YPEL proteins, mediates its effects is largely unknown.
Gizem Turan +7 more
wiley +1 more source
Cutaneous mastocytosis: Two pediatric cases treated with topical pimecrolimus. [PDF]
Cutaneous mastocytosis is characterized by increased numbers of skin mast cells that release mediators causing pruritus, urticaria, and flushing. Most pediatric mastocytosis patients exhibit the pattern of urticaria pigmentosa, which typically appears ...
Azevedo, R +4 more
core +1 more source
The Report of a Very Rare Case of Peseudoxanthomatous Mastocytosis
Diffuse cutaneous mastocytosis is very rare variety mast-cell disorder which is called peseudoxanthomatous mastocytosis. Our case was a man who was eighteen years old.
Mahmoud Farshchain +2 more
doaj

