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Клинический разбор в общей медицине, 2020 Mastocytosis is a heterogeneous group of neoplasms characterized by increased mast cells proliferation and accumulation in various organs and tissues. The paper introduces the newest mastocytosis classification and diagnosis principles.
Olga B. Tamrazova, Evgeniya A. Glukhova
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PEDIATRIC MASTOCYTOSIS: AN UPDATE
Mediterranean Journal of Hematology and Infectious Diseases, 2021 Mastocytosis is a rare clonal disorder, characterized by excessive proliferation and accumulation of mast cells (MC) in various organs and tissues. Cutaneous mastocytosis (CM), the most common form in children, is defined when MC infiltration is limited ...
Fiorina Giona
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Review papers The role of KIT gene mutations in pathogenesis of pediatric mastocytosis
Przegląd Dermatologiczny, 2015 Mastocytosis is characterized by excessive proliferation and accumulation of mast cells in skin and/or other organs. Two forms of the disease, cutaneous and systemic mastocytosis, differ significantly in symptomatology and clinical course.
Joanna Dawicka +5 more
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Systemic Lymphadenopathic Mastocytosis with Eosinophilia
Diagnostics, 2022 Systemic mastocytosis is a neoplastic proliferation of mast cells that most frequently involves cutaneous sites. Mastocytosis involves various extracutaneous sites, but the lymph node is rare.
Soyoung Im +3 more
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Drug hypersensitivity reactions and allergy in patients with mastocytosis [PDF]
Przegląd Dermatologiczny, 2017 Mastocytosis is a rare myeloproliferative disease caused by excessive proliferation and accumulation of mast cells in the skin and internal organs. The most common variant of mastocytosis in children is cutaneous mastocytosis.
Justyna H. Czarny +7 more
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Diffuse cutaneous mastocytosis in an infant
Indian Journal of Paediatric Dermatology, 2016 Mastocytosis is a group of a disorder characterized by infiltration of mast cell in various organs, e.g. skin, bone marrow, liver, spleen, gastrointestinal tract, lymph node, etc., The term bullous mastocytosis is generally used to describe the varieties
Sitangshu Chatterjee +2 more
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Cutaneous mastocytosis: Clinical Case
Педиатрическая фармакологияSkin syndrome is common in the practice of allergologist-immunologist, and it requires differential diagnosis. One of the rare skin diseases among children is mastocytosis caused by excessive accumulation of mast cells in various organs.
Aset Kh. Ibisheva +5 more
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Hematology/Oncology Clinics of North America, 2010 An unusual disease, mastocytosis challenges the pathologist with a variety of morphologic appearances and heterogeneous clinical presentations ranging from skin manifestations (pruritus, urticaria, dermatographism) to systemic signs and symptoms indicative of mast cell mediator release, including flushing, hypotension, headache, and anaphylaxis among ...
Tracy I, George, Hans-Peter, Horny
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Journal of Investigative Dermatology, 1991 The onset of mastocytosis occurs between birth and 2 years of age in approximately 55% of all cases; an additional 10% develop the disease before the age of 15 years. Mastocytosis in these age groups differs in many respects from mastocytosis that has its onset in adulthood. The typical presentation of pediatric-onset mastocytosis consists of cutaneous
Kettelhut, Brett V., Metcalfe, Dean D.
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French guidelines for the management of nonadvanced mastocytosis in adults [PDF]
Orphanet Journal of Rare DiseasesMastocytosis is a rare disease caused by abnormal mast cell accumulation/proliferation in various organs/tissues. Its clinical features exhibit significant variability irrespective of its clinical presentation, classification, global survival or impact ...
Cristina Bulai Livideanu +5 more
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