Results 11 to 20 of about 66,673 (183)
Childhood Pseudoxanthomatousmastocytosis; Report of two cases
Indian Journal of Dermatopathology and Diagnostic Dermatology, 2018 Cutaneous mastocytosis (CM) is a mast cell proliferative disorder that commonly affects pediatric population. It has various clinical forms such as urticaria pigmentosa, solitary mastocytoma, telangiectasia macularis eruptiva perstans, diffuse CM, and ...
Bhabani S. T. P. Singh +3 more
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Dermatologic Clinics, 2001 Mastocytosis represents a heterogeneous group of clinical disorders resulting from the infiltration of mast cells in the skin and other organs. Although mastocytosis was first described over 130 years ago, the pathophysiologic mechanisms responsible for this disease have been identified only recently.
M D, Tharp, B J, Longley
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Immunology and Allergy Clinics of North America, 2014 Mastocytosis is a disorder of abnormal mast cell proliferation, with clinical features that include flushing, pruritus, abdominal pain, diarrhea, hypotension, syncope, and musculoskeletal pain. These features are the result of mast cell mediator release and infiltration into target organs.
Melody C, Carter +2 more
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American Journal of Clinical Pathology, 2020 Abstract Objectives The 2019 Workshop of the Society for Hematopathology/European Association for Haematopathology received and reviewed cases covering the spectrum of mastocytosis and related diseases, including morphologic mimics, focusing on recent updates and relevant findings for pathologists.
Alexandar, Tzankov +11 more
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Advanced systemic mastocytosis: from molecular and genetic progress to clinical practice
Haematologica, 2016 Systemic mastocytosis is a heterogeneous disease characterized by the accumulation of neoplastic mast cells in the bone marrow and other organ organs/tissues.
Celalettin Ustun +15 more
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Клинический разбор в общей медицине, 2020 Mastocytosis is a heterogeneous group of neoplasms characterized by increased mast cells proliferation and accumulation in various organs and tissues. The paper introduces the newest mastocytosis classification and diagnosis principles.
Olga B. Tamrazova, Evgeniya A. Glukhova
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Review papers The role of KIT gene mutations in pathogenesis of pediatric mastocytosis
Przegląd Dermatologiczny, 2015 Mastocytosis is characterized by excessive proliferation and accumulation of mast cells in skin and/or other organs. Two forms of the disease, cutaneous and systemic mastocytosis, differ significantly in symptomatology and clinical course.
Joanna Dawicka +5 more
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Phenotypic and genotypic characteristics of mastocytosis according to the age of onset. [PDF]
PLoS ONE, 2008 Adult's mastocytosis is usually associated with persistent systemic involvement and c-kit 816 mutation, while pediatrics disease is mostly limited to the skin and often resolves spontaneously.
Fanny Lanternier +26 more
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Diffuse cutaneous mastocytosis in an infant
Indian Journal of Paediatric Dermatology, 2016 Mastocytosis is a group of a disorder characterized by infiltration of mast cell in various organs, e.g. skin, bone marrow, liver, spleen, gastrointestinal tract, lymph node, etc., The term bullous mastocytosis is generally used to describe the varieties
Sitangshu Chatterjee +2 more
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Mastocytosis: Fertility and Pregnancy Management in a Rare Disease
Frontiers in Oncology, 2022 Mastocytosis encompasses a subset of rare diseases, characterized by the presence and accumulation of abnormal neoplastic MC in various organ systems, including skin, bone marrow, spleen and gastrointestinal tract.
Jacqueline Ferrari +5 more
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