Validity and Reliability of Clinical and Patient‐Reported Outcomes in Multisystem Proteinopathy 1
ABSTRACT Objective Valosin‐containing protein (VCP)‐associated multisystem proteinopathy 1 (MSP1) is caused by variants in the VCP gene. MSP1 results in various phenotypes including progressive myopathy, Paget's disease of bone, frontotemporal dementia, amyotrophic lateral sclerosis, and parkinsonism, among others.
Lindsay N. Alfano+15 more
wiley +1 more source
A damaged-informed lung model for ventilator waveforms [PDF]
The acute respiratory distress syndrome (ARDS) is characterized by the acute development of diffuse alveolar damage (DAD) resulting in increased vascular permeability and decreased alveolar gas exchange. Mechanical ventilation is a potentially lifesaving intervention to improve oxygen exchange but has the potential to cause ventilator-induced lung ...
arxiv
Heat demand uncertainty evaluation of typical multiâ€flat panel building
Heat consumption of similar buildings under the same climatic conditions normally shows different values. This phenomenon has not been adequately explored yet.
Egle Jaraminiene, Egidijus Juodis
doaj +1 more source
Evaluation of parametrics for the development of vertical solar chimney ventilation in hot and humid climate [PDF]
In terms of housing passive cooling design, tropical climatic regions present the most difficult problem to solve. A good dwelling design can keep the indoor environment favorable and comfortable during most of the year without the use of any mechanical ...
Ahmad, Mohd. Hamdan+2 more
core
Increasing compliance with low tidal volume ventilation in the ICU with two nudge-based interventions: evaluation through intervention time-series analyses [PDF]
Objectives: Low tidal volume (TVe) ventilation improves outcomes for ventilated patients, and the majority of clinicians state they implement it. Unfortunately, most patients never receive low TVes.
Bourdeaux, C. P.+6 more
core +3 more sources
CONTEXT The outcome of patients receiving mechanical ventilation for particular indications has been studied, but the outcome in a large number of unselected, heterogeneous patients has not been reported. OBJECTIVE To determine the survival of patients
A. Esteban+11 more
semanticscholar +1 more source
ABSTRACT Objective To provide a comprehensive clinical and genetic characterization of individuals with arthrogryposis multiplex congenita (AMC), focusing on the distribution of genetic etiologies across the neuromuscular spectrum and comparing myogenic and neurogenic subtypes. Methods A total of 105 individuals with AMC were clinically and genetically
Florencia Pérez‐Vidarte+13 more
wiley +1 more source
Spatial features of CO2 for occupancy detection in a naturally ventilated school building [PDF]
Accurate occupancy information helps to improve building energy efficiency and occupant comfort. Occupancy detection methods based on CO2 sensors have received attention due to their low cost and low intrusiveness. In naturally ventilated buildings, the accuracy of CO2-based occupancy detection is generally low in related studies due to the complex ...
arxiv +1 more source
During construction in the Far North, due to the preservation of permafrost soils, the buildings are arranged on piles and foundations on the bedding soil.
Ivanov Victor, Ivanova Anastasiya
doaj +1 more source
Simultaneous observations of haemolymph flow and ventilation in marine spider crabs at different temperatures: a flow weighted MRI study [PDF]
In vivo magnetic resonance imaging (MRI) and angiography were applied to the marine spider crab Maja squinado for a study of temperature effects and thermal tolerance.
Bock, Christian+3 more
core +1 more source