SPLENIC HOMOTRANSPLANTATION. [PDF]
During the past 12 months, five clinical whole-organ splenic homotransplantations have been carried out with the objective of providing active immunologic tissue for the recipient patients.
FUDENBERG, H+5 more
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Bone marrow cells in X-linked agammaglobulinemia express pre-B-specific genes (lambda-like and V pre-B) and present immunoglobulin V-D-J gene usage strongly biased to a fetal-like repertoire. [PDF]
Michèle Milili+5 more
openalex +1 more source
Characterization of a CD38-like 78-kilodalton soluble protein released from B cell lines derived from patients with X-linked agammaglobulinemia. [PDF]
Roberto Mallone+6 more
openalex +1 more source
Mutations in the Human λ5/14.1 Gene Result in B Cell Deficiency and Agammaglobulinemia [PDF]
Yoshiyuki Minegishi+5 more
openalex +1 more source
BTKbase, mutation database for X-linked agammaglobulinemia (XLA) [PDF]
Mauno Vihinen+13 more
openalex +1 more source
New insights in the use of immunoglobulins for the management of immune deficiency (PID) patients [PDF]
Immunoglobulin replacement therapy (IRT) is standard treatment for patients with primary immunodeficiency (PID). Because most of the patients with PID will require long life-time immunoglobulin replacement therapy, the quality of the prescribed ...
Alfa Cissé, Ousmane+6 more
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GRANULOPOIESIS IN X-LINKED AGAMMAGLOBULINEMIA PATIENTS: THE EFFECTS OF IN VITRO AND IN VIVO IMMUNOGLOBULINES 60 [PDF]
Serge Gradstein+3 more
openalex +1 more source
Mutations in topoisomerase IIβ result in a B cell immunodeficiency. [PDF]
B cell development is a highly regulated process involving multiple differentiation steps, yet many details regarding this pathway remain unknown. Sequencing of patients with B cell-restricted immunodeficiency reveals autosomal dominant mutations in ...
Austin, Caroline A+22 more
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Stability and peptide binding specificity of Btk SH2 domain: Molecular basis for X‐linked agammaglobulinemia [PDF]
Shiou‐Ru Tzeng+10 more
openalex +1 more source
Involvement of Bruton's tyrosine kinase in FcepsilonRI-dependent mast cell degranulation and cytokine production. [PDF]
We investigated the role of Bruton's tyrosine kinase (Btk) in FcepsilonRI-dependent activation of mouse mast cells, using xid and btk null mutant mice.
Alt, FW+16 more
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