Results 31 to 40 of about 7,162 (211)
Thrombosis Update, 2020 Atypical hemolytic uremic syndrome (aHUS) is a thrombotic microangiopathy (TMA) characterized by dysregulation of the alternative pathway of complement. Heterozygous variants in complement and complement regulatory proteins may increase risk for aHUS and,
Meera Sridharan +4 more
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Rapid Resolution of Atypical Hemolytic Uremic Syndrome by Eculizumab Treatment [PDF]
Childhood Kidney Diseases, 2020 Atypical hemolytic uremic syndrome (aHUS) is an extremely rare and life-threatening disorder. Typical HUS is often caused by Shiga toxin-positive Escherichia coli, while aHUS is caused by dysregulation of the alternative pathway of the complement system ...
Min Seung Kim +5 more
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Autoimmunity, 2018 Complement convertases are enzymatic complexes, which play a critical role in propagation and amplification of the complement cascade. Under physiological conditions, convertases decay shortly after being formed in either spontaneous or inhibitor-driven ...
Aleksandra Urban +6 more
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Case Report: Lipoprotein Glomerulopathy Complicated by Atypical Hemolytic Uremic Syndrome
Frontiers in Medicine, 2021 Lipoprotein glomerulopathy (LPG) is a rare inherited disease caused by mutations in the APOE gene, encoding apolipoprotein E (apoE). Atypical hemolytic uremic syndrome (aHUS) is a thrombotic microangiopathy (TMA) characterized by overactivation of the ...
Lara Kollbrunner +7 more
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Demographic data of Brazilian aHUS cohort patients in renal transplantation.
, 2021 Demographic data of Brazilian aHUS cohort patients in renal transplantation.
Hong Si Nga (4592092) +9 more
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Clinical and genetic characteristics of patients diagnosed with atypical hemolytic uremic syndrome (aHUS): epidemiological data from the Belgian cohort of the Global aHUS Registry [PDF]
Journal of NephrologyImad Al-Dakkak +2 more
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Epidemiology of Atypical Hemolytic Uremic Syndrome: A Systematic Literature Review
Clinical Epidemiology, 2020 Kevin Yan,1,2 Kamal Desai,1 Lakshmi Gullapalli,1 Eric Druyts,1 Chakrapani Balijepalli1 1Pharmalytics Group, Vancouver, British Columbia, Canada; 2Faculty of Medicine, University of British Columbia, Vancouver, British Columbia, CanadaCorrespondence ...
Yan K +4 more
doaj
The Ahu (Capreolus pygargus) [PDF]
Annals and Magazine of Natural History, 1872 n ...
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COMPLEMENTing the diagnosis of aHUS
Blood, 2014 In this issue of Blood , Noris et al describe a functional complement assay that can be used to diagnose atypical hemolytic-uremic syndrome (aHUS).[1][1] This assay might also be useful in identifying aHUS patients in remission and in detecting asymptomatic carriers of complement gene mutations.
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Paediatric renal transplantation: Paediatric surgeons' perspective
Surgical Practice, EarlyView.Abstract Renal transplantation is the most effective treatment for paediatric end‐stage renal disease (ESRD), offering advantages in survival, growth and neurocognitive development that surpass other renal replacement therapies (RRT). The paediatric setting, however, introduces distinct complexities that distinguish it from adult practice.
Adrian Chi‐heng Fung +3 more
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