Results 261 to 270 of about 79,953 (279)
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Sudden Death by AL Amyloidosis
American Journal of Forensic Medicine & Pathology, 2023Abstract We report the case of a young female that died due to systemic amyloidosis.
Christian, Perez, Kristy, Waite
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Macroglossia – not always AL amyloidosis
Amyloid, 2010Abstract Abstract 5007 Introduction: Amyloidosis is characterized by extracellular deposition of abnormal insoluble fibrillar proteins. The two most frequent systemic amyloidoses are the light-chain (AL amyloidosis) and familial transthyretin (ATTR) forms.
Andrew J, Cowan +6 more
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Primary amyloidosis (AL) in families
American Journal of Hematology, 1986AbstractWe report the occurrence of immunoglobulin‐related amyloidosis (AL) in three separate families, each family having two members affected. None of the six patients had evidence to suggest the presence of familial amyloidosis (AF). Previously, immunoglobulin‐related amyloidosis (AL) was considered to be a sporadic disease process.
M A, Gertz, J P, Garton, R A, Kyle
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Revue medicale de Bruxelles, 2001
AL amyloidosis is a systemic disease caused by the deposition of fibrillar proteins in organs and tissues. These deposits are responsible for organic dysfunctions and may be rapidly lethal. Current therapy is unsatisfactory. We describe three clinical cases of multisystemic AL amyloidosis but with different initial presentation: nephrotic syndrome ...
A R, Hedeshi +6 more
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AL amyloidosis is a systemic disease caused by the deposition of fibrillar proteins in organs and tissues. These deposits are responsible for organic dysfunctions and may be rapidly lethal. Current therapy is unsatisfactory. We describe three clinical cases of multisystemic AL amyloidosis but with different initial presentation: nephrotic syndrome ...
A R, Hedeshi +6 more
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Monoclonal IgM-related AL amyloidosis
Best Practice & Research Clinical Haematology, 2016Monoclonal immunoglobulin M (IgM)-related light chain (AL) amyloidosis, which accounts for 5%-7% of all AL amyloidosis cases, is a distinct clinical entity that poses specific challenges to clinicians. Several studies reported that although there is a substantial overlap, the pattern of organ involvement is peculiar, with higher frequencies of lung ...
Milani P., Merlini G.
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Archives of Internal Medicine, 1984
[ill]myloidosis is considered by many to be a rare disease. In a retrospective review by Alexanian al in this issue,130 cases of amyloidosis were [ill]gnosed during a 15-year span. Because symptoms [ill]re present for 20 months before diagnosis, the [ill]hors point out the need for better identification [ill]d earlier diagnosis.
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[ill]myloidosis is considered by many to be a rare disease. In a retrospective review by Alexanian al in this issue,130 cases of amyloidosis were [ill]gnosed during a 15-year span. Because symptoms [ill]re present for 20 months before diagnosis, the [ill]hors point out the need for better identification [ill]d earlier diagnosis.
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Immunomodulatory drugs in AL amyloidosis
Critical Reviews in Oncology/Hematology, 2016Immunoglobulin light chain amyloidosis (AL amyloidosis) is indeed a rare plasma cell disorder, yet the most common of the systemic amyloidoses. The choice of adequate treatment modality is complicated and depends dominantly on the risk stratification of these fragile patients.
T, Jelinek, Z, Kufova, R, Hajek
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Nihon rinsho. Japanese journal of clinical medicine, 1995
AL amyloidosis is one type of systemic amyloidosis. AL represents Amyloid of Light chains (of Ig's) type. Diagnosis of amyloid must be carried out by patho-histological Congo-red stains of the biopsied materials under suspicion of amyloid deposits from patients with various clinical manifestations, including macroglossia, cardiac abnormalities, ECG ...
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AL amyloidosis is one type of systemic amyloidosis. AL represents Amyloid of Light chains (of Ig's) type. Diagnosis of amyloid must be carried out by patho-histological Congo-red stains of the biopsied materials under suspicion of amyloid deposits from patients with various clinical manifestations, including macroglossia, cardiac abnormalities, ECG ...
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The Journal of the Association of Physicians of India, 2013
Susanta Kr, Das +5 more
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Susanta Kr, Das +5 more
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