Results 31 to 40 of about 10,911,887 (292)

Supportive Care in AL Amyloidosis [PDF]

Acta Haematologica, 2020
Immunoglobulin light-chain (AL) amyloidosis is a systemic disease characterized by the production and deposition of light chain-derived amyloid fibrils in different organs. Prompt treatment directed to the underlying plasma cell clone is crucial in order to achieve a rapid, deep and durable hematologic response.
M Teresa, Cibeira, José T, Ortiz-Pérez, Luis F, Quintana, Carlos, Fernádez de Larrea, Natalia, Tovar, Joan, Bladé   +5 more
openaire   +2 more sources

A case report of pulmonary amyloidosis recognized by detection of AA amyloid exclusively in alveolar macrophages [PDF]

, 2020
Amyloidosis is a rare condition in which tissue deposits of inert fibrillar protein result in organ damage and dysfunction. There are several types of amyloid fibrils.
Bychkov, Andrey, Tanaka, Kei, Mukae, Hiroshi, Fukuoka, Junya, Ando, Kouji, Zaizen, Yoshiaki, Ishimoto, Hiroshi, Tabata, Kazuhiro, Miyazaki, Yasushi, Laohawetwanit, Thiyaphat   +9 more
core   +1 more source

Prognosis and Staging of AL Amyloidosis [PDF]

Acta Haematologica, 2020
The treatment options for systemic light chain amyloidosis (AL) are currently widening in an unprecedented way, brought about by an expanding arsenal of anti-myeloma therapy as well as by novel approaches to target toxic light chains and, most recently, deposited amyloid directly.
Tobias, Dittrich, Christoph, Kimmich, Ute, Hegenbart, Stefan O, Schönland   +3 more
openaire   +2 more sources

Marked shrinkage of amyloid lymphadenopathy after an intensive chemotherapy in a patient with IgM-associated AL amyloidosis [PDF]

, 2009
This is an electronic version of an article published in Amyloid 2009, Vol. 16, No. 3 : Pages 183-185. Amyloid is available online at: http://informahealthcare.com/doi/pdf/10.1080/13506120903151825A male patient with primary AL amyloidosis who had been ...
Tazawa, Ko-Ichi, Ikeda, Shu-ichi, Matsuda, Masayuki, Shimojima, Yasuhiro, Katoh, Nagaaki   +4 more
core   +1 more source

Incidence and clinical outcome of renal amyloidosis: A retrospective study

Saudi Journal of Kidney Diseases and Transplantation, 2013
The kidneys are affected in almost all patients with amyloid A in secondary amyloidosis (AA) amyloidosis but less frequently in immunoglobulin light chains in primary systemic amyloidosis (AL) amyloidosis.
Emad Abdallah, Emam Waked
doaj   +1 more source

Daratumumab plus CyBorD for patients with newly diagnosed light chain (AL) amyloidosis

Therapeutic Advances in Hematology, 2021
Primary systemic immunoglobulin light chain (AL) amyloidosis is caused by a plasma cell clone of, usually low, malignant potential that expresses CD38 molecules on their surface.
Foteini Theodorakakou, Meletios A. Dimopoulos, Efstathios Kastritis   +2 more
doaj   +1 more source

Cardiac Amyloidosis and Endomyocardial Biopsy: Correlation of Extent and pattern of Deposition with Amyloid Immunophenotype by immunogold in a single institution [PDF]

, 2023
openBackground: Amyloidosis is an infiltrative systemic disease characterized by the extracellular deposition of fibrillar proteins in different organs leading to tissue damage and dysfunction. Cardiac involvement by amyloidosis is common.
DI MIRA, COSIMO JUNIOR
core  

A bibliometric analysis of light chain amyloidosis from 2005 to 2024: research trends and hot spots

Frontiers in Medicine
BackgroundLight chain (AL) amyloidosis stands as the most prevalent subtype of systemic amyloidosis, encompassing a group of rare diseases. Here, we evaluated the scientific landscape of AL amyloidosis to investigate research trends and identify hotspots
Xiangdong Liu, Xiangdong Liu, Junyan Wang, Junyan Wang, Yingmin Li, Yingmin Li, Yingmin Li, Weibo Shi, Weibo Shi, Weibo Shi, Xiaojing Zhang, Xiaojing Zhang, Xiaojing Zhang, Shujin Li, Shujin Li, Shujin Li, Bin Cong, Bin Cong, Bin Cong, Bin Cong   +19 more
doaj   +1 more source

Amyloid light-chain amyloidosis presented as focal segmental glomerulosclerosis in a kidney transplant recipient

Korean Journal of Transplantation, 2020
Amyloid light-chain (AL) amyloidosis after kidney transplantation is a rare disease in the world, and only one case of systemic AL amyloidosis after kidney transplantation is reported in Korea.
Sung Hyun Park, So Hyun Kwon, Hwa Young Lee, Sua Lee, Eun Jeong Ko, Tae Hyun Ban, Byung Ha Chung, Yeong Jin Choi, Chul Woo Yang   +8 more
doaj   +1 more source

Joint position statement of the diagnosis and management of light chain amyloidosis and light chain cardiac amyloidosis by the Taiwan Society of Cardiology (TSOC) and the Hematology Society of Taiwan (HST)

Journal of the Formosan Medical Association
Light chain (AL) amyloidosis, defined by the organ deposition of misfolded and aggregated amyloid light chain, is the most common subtype of systematic amyloidosis with an incidence rate of around 1 case per 100,000 person-years in Taiwan.
Yen-Wen Wu, Chao-Hung Wei, Yen-Hung Lin, Shang-Yi Huang, Yen-Wen Liu, Tran-Der Tan, Wen-Chung Yu, Chia-Jen Liu, Chung-Lieh Hung, Po-Shen Ko, Ning-I Yang, Shih-Feng Cho, Chun-Yao Huang, Chun-Kai Liao, Chieh-Lin Jerry Teng, Tsai-Yun Chen, Wen-Jone Chen, Bor-Sheng Ko   +17 more
doaj   +1 more source