Marked shrinkage of amyloid lymphadenopathy after an intensive chemotherapy in a patient with IgM-associated AL amyloidosis [PDF]
This is an electronic version of an article published in Amyloid 2009, Vol. 16, No. 3 : Pages 183-185. Amyloid is available online at: http://informahealthcare.com/doi/pdf/10.1080/13506120903151825A male patient with primary AL amyloidosis who had been ...
Tazawa, Ko-Ichi +4 more
core +1 more source
Cardiac Amyloidosis and Endomyocardial Biopsy: Correlation of Extent and pattern of Deposition with Amyloid Immunophenotype by immunogold in a single institution [PDF]
openBackground: Amyloidosis is an infiltrative systemic disease characterized by the extracellular deposition of fibrillar proteins in different organs leading to tissue damage and dysfunction. Cardiac involvement by amyloidosis is common.
DI MIRA, COSIMO JUNIOR
core
Incidence and clinical outcome of renal amyloidosis: A retrospective study
The kidneys are affected in almost all patients with amyloid A in secondary amyloidosis (AA) amyloidosis but less frequently in immunoglobulin light chains in primary systemic amyloidosis (AL) amyloidosis.
Emad Abdallah, Emam Waked
doaj +1 more source
Retinitis pigmentosa associated with systemic light chain amyloidosis (AL amyloidosis)
Retinitis pigmentosa (RP) or hereditary retinal dystrophy is a rare disease that can be isolated (non-syndromic RP) or associated with other systemic signs (syndromic RP).
Salem Bouomrani +2 more
core +1 more source
Amyloid light-chain (AL) amyloidosis after kidney transplantation is a rare disease in the world, and only one case of systemic AL amyloidosis after kidney transplantation is reported in Korea.
Sung Hyun Park +8 more
doaj +1 more source
Daratumumab plus CyBorD for patients with newly diagnosed light chain (AL) amyloidosis
Primary systemic immunoglobulin light chain (AL) amyloidosis is caused by a plasma cell clone of, usually low, malignant potential that expresses CD38 molecules on their surface.
Foteini Theodorakakou +2 more
doaj +1 more source
Hemostasis disorders in patients with systemic AL-amyloidosis
Aim. To analyze the frequency and nature of hemorrhagic and thrombotic complications in patients with systemic AL-amyloidosis and compare with laboratory changes in the hemostasis system. Materials and methods.
Irina G. Rekhtina +4 more
doaj +1 more source
Abstract Hepatocellular adenomas (HCAs) are benign liver tumors associated with bleeding or malignant transformation. Data on the indication for surgery are scarce. We analyzed indications and outcome of patients operated for HCAs < 50 mm compared to HCAs ≥ 50 mm. Changes in final postoperative diagnosis were assessed.
Martijn P. D. Haring +70 more
wiley +1 more source
Duodenal biopsy: an unexpected confirmatory test for a patient with al-amyloidosis
SSystemic AL- amyloidosis is a disorder of protein folding in which there is extra-cellular accumulation as β pleated fibrillar deposits of monoclonal immunoglobulin light chain fragments. AL- amyloidosis is a rare clinical entity.
S. Pirasath +4 more
doaj +1 more source
A bibliometric analysis of light chain amyloidosis from 2005 to 2024: research trends and hot spots
BackgroundLight chain (AL) amyloidosis stands as the most prevalent subtype of systemic amyloidosis, encompassing a group of rare diseases. Here, we evaluated the scientific landscape of AL amyloidosis to investigate research trends and identify hotspots
Xiangdong Liu +19 more
doaj +1 more source

