Expert recommendation from the Swiss Amyloidosis Network (SAN) for systemic AL-amyloidosis [PDF]
Swiss Medical Weekly, 2020 Systemic amyloidosis is a heterogeneous group of diseases associated with protein misfolding into insoluble beta-sheet rich structures that deposit extracellularly in different organs, eventually compromising their function.
Rahel Schwotzer +42 more
doaj +5 more sources
Amyloidosis – short review [PDF]
Journal of Medical Science, 2016 Amyloidosis is a heterogeneous group of disorders associated with pathological deposition of amyloid. We can recognize two major categories of amyloidosis: primary (AL) and secondary (AA) type.
Agnieszka Danuta Gaczkowska +2 more
doaj +2 more sources
Chronic Viral Infections and Al Amyloidosis: An Uncommon Association
Clinical Case ReportsAL‐amyloidosis is caused by deposition of pathological insoluble proteins in organs and tissues. HIV infection is a multi‐system disorder causing chronic inflammation.
Alberto Palladini +7 more
doaj +2 more sources
Localized Gastrointestinal Light Chain (AL) Amyloidosis Under Surveillance for Five Years: A Case Report. [PDF]
DEN OpenABSTRACT Amyloidosis, characterized by the deposition of abnormal protein fibrils in organs, is classified as systemic or localized. Amyloid light chain (AL)‐type localized amyloidosis is uncommon, particularly when confined to the gastrointestinal tract.
Kojimahara S +7 more
europepmc +2 more sources
Aggressive Hepatic AL Amyloidosis Encountering Therapeutic Frailty: Rapid Organ Reversal With Tailored Daratumumab-Based Therapy and Low-Dose Corticosteroids in a Patient With Steroid-Induced Psychosis. [PDF]
Clin Case RepABSTRACT Hepatic AL amyloidosis can cause severe cholestasis independent of marrow tumor burden. In patients with absolute contraindications to high‐dose steroids—such as steroid‐induced psychosis—tailored daratumumab regimens with low‐dose corticosteroids can drive rapid, life‐saving organ reversal.
Ceccarelli R +8 more
europepmc +2 more sources
Retinitis pigmentosa associated with systemic light chain amyloidosis (AL amyloidosis) [PDF]
, 2021 Retinitis pigmentosa (RP) or hereditary retinal dystrophy is a rare disease that can be isolated (non-syndromic RP) or associated with other systemic signs (syndromic RP).
Bouomrani,Salem +2 more
core +3 more sources
Dysregulation of miRNAs In AL Amyloidosis [PDF]
Blood, 2010 Abstract Abstract 4648 Bone marrow plasma cells (BMPC) were purified from aspirates obtained from patients with AL amyloidosis using anti-CD138 immunomagnetic beads, and from controls. Expression levels of micro RNAs (miRNAs) were compared by microarray.
Liangping, Weng +5 more
openaire +2 more sources
Systemic Immunoglobulin Light Chain Amyloidosis Presenting as Painful Penile Ulcers
Annals of Internal Medicine: Clinical Cases, 2022 Immunoglobulin light chain (AL) amyloidosis is a systemic form of amyloidosis that commonly affects the heart, kidney, liver, and nervous system. Penile involvement in AL amyloidosis is rare and thus often not considered in the differential diagnosis for
Crystal Lihong Yan +3 more
doaj +1 more source
Senile Systemic Amyloidosis: Clinical Features at Presentation and Outcome [PDF]
, 2013 Background Cardiac amyloidosis is a fatal disease whose prognosis and treatment rely on identification of the amyloid type. In our aging population transthyretin amyloidosis (ATTRwt) is common and must be differentiated from other amyloid types.
Banypersad, SM +15 more
core +1 more source
Be SMART About AL Amyloidosis [PDF]
Mayo Clinic Proceedings, 2021 n ...
Palladini, Giovanni, Merlini, Giampaolo
openaire +4 more sources