Procedural outcomes in patients undergoing non-cardiac surgery with cardiac variant amyloidosis
Background Amyloidosis is a complex disease with a multitude of sequalae, particularly with the variants that cause cardiac amyloidosis. There is minimal literature on the types of procedures these patients undergo and the associated postprocedural ...
Michael A. Smith +5 more
doaj +1 more source
Precision medicine with pioneering RNAi therapeutics in ATTR amyloidosis: from bench to bedside
Transthyretin (ATTR) amyloidosis is a multisystem disease caused by misfolding and aggregation of the plasma protein transthyretin (TTR) into insoluble amyloid fibrils in various organs. In clinical practice, ATTRwt amyloidosis manifests as a predominant
Malinverni, Silvia +3 more
core +1 more source
Defining Heart Failure Endpoint in ATTR Amyloidosis Clinical Trials: Time for an Update? [PDF]
Gjermeni D +3 more
europepmc +1 more source
Wearables for Telemonitoring in ATTR-Amyloidosis: Current Perspectives. [PDF]
Kind A +10 more
europepmc +1 more source
Specific therapeutic options for transthyretin amyloidosis
The epidemiology of systemic amyloidosis has recently undergone a spectacular transformation. While light-chain amyloidosis remains a rare disease with a stable incidence, chronic inflammatory disease associated amyloidosis (AA) is diagnosed less ...
Zoltán Pozsonyi
core +1 more source
Vutrisiran-Mediated Knockdown of Transthyretin in Patients with ATTR Amyloidosis. [PDF]
Fontana M +11 more
europepmc +1 more source
Common transthyretin-derived amyloid fibril structures in patients with hereditary ATTR amyloidosis. [PDF]
Steinebrei M +8 more
europepmc +1 more source
Utilization and Prognosis of Cardiac Device Implantation in AL Versus ATTR Amyloidosis. [PDF]
Hussain B +7 more
europepmc +1 more source
ATTR Amyloidosis Concomitant with Parkinsonism and Cardiac Sympathetic Neuropathy. [PDF]
Haga F +7 more
europepmc +1 more source

