Results 141 to 150 of about 24,341 (292)

An adult case of atypical hemolytic uremic syndrome presented with posterior reversible encephalopathy syndrome: Successful response to late-onset eculizumab treatment

Hematology Reports, 2018
Atypical hemolytic uremic syndrome is a rare and progressive disease caused by uncontrolled alternative complement activation. Dysregulatıon of the complement activation results in thrombotic microangiopathy and multiorgan damage.
Serife Solmaz Medeni, Sinem Namdaroglu, Tugba Cetintepe, Can Ozlu, Funda Tasli, Zehra Hilal Adibelli, Oktay Bilgir, Erhan Tatar   +7 more
doaj   +1 more source

Identification and management of atypical Hemolytic Uremic Syndrome immediately post heart transplantation [PDF]

, 2015
Atypical hemolytic uremic syndrome (aHUS) is a serious hematologic disorder with high mortality if left untreated. A comprehensive literature review revealed only two cases of aHUS post–heart transplantation.
Hadi, M. Azam, Hashmi, Zubair A., Vardas, Panos N.   +2 more
core   +1 more source

Structural and Functional Characterization of Factor H Mutations Associated with Atypical Hemolytic Uremic Syndrome [PDF]

, 2002
Pilar Sánchez‐Corral, David Pérez-Caballero, Olatz Huarte, Ari M. Simckes, Elena Goicoechea de Jorge, Margarita López‐Trascasa, Santiago Rodrı́guez de Córdoba   +6 more
openalex   +1 more source

X-linked C1GALT1C1 mutation causes atypical hemolytic uremic syndrome

European Journal of Human Genetics, 2023
N. Hadar, R. Schreiber, M. Eskin-Schwartz, Eyal Kristal, G. Shubinsky, G. Ling, Idan Cohen, Michael Geylis, A. Nahum, Y. Yogev, O. Birk   +10 more
semanticscholar   +1 more source

Hemolytic Uremic Syndrome Caused by Enteroviral Infection [PDF]

, 2013
A 4-year-old boy presented with enteroviral infection complicated with atypical hemolytic uremic syndrome (aHUS). Enterovirus RNA was detected by reverse transcription polymerase chain reaction (RT-PCR) of both blood and kidney biopsy specimens. A survey
Huang, Fu-Yuan, Lee, Ming-Dar, Lin, Chun-Chen, Liu, Hsi-Che, Tsai, Jeng-Daw, Tzen, Chin-Yuan   +5 more
core   +2 more sources

Síndrome Hemolítico Urémico Atípico en Cuidados Intensivos: Caso Clínico de un Adulto [PDF]

, 2016
info:eu-repo/semantics ...
Agudo, I, Azevedo, L, Bento, L, Cavaco, R, Germano, N, Souto-Moura, T   +5 more
core   +1 more source

Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults.

American Society of Nephrology. Clinical Journal, 2013
BACKGROUND AND OBJECTIVES Atypical hemolytic uremic syndrome (aHUS) is a rare complement-mediated kidney disease that was first recognized in children but also affects adults.
V. Frémeaux-Bacchi, F. Fakhouri, A. Garnier, F. Bienaimé, M. Dragon-Durey, S. Ngo, B. Moulin, A. Servais, F. Provôt, L. Rostaing, S. Burtey, P. Niaudet, G. Deschênes, Y. Lebranchu, J. Zuber, C. Loirat   +15 more
semanticscholar   +1 more source

Atypical hemolytic-uremic syndrome, manifesting without thrombocytopenia (clinical case)

Известия высших учебных заведений. Поволжский регион: Медицинские науки
Background. Atypical hemolytic uremic syndrome is an ultra-rare (orphan) disease from the group of thrombotic microangiopathies of progressive course, which is caused by uncontrolled activation of the alternative complement pathway of hereditary or ...
A.A. Dyachkova, A.N. Anokhin, M.A. Shlykova, I.S. Kiseleva   +3 more
doaj   +1 more source

Thrombomodulin enhances complement regulation through strong affinity interactions with factor H and C3b-Factor H complex [PDF]

, 2016
Introduction Coagulation and complement systems are simultaneously activated at sites of tissue injury, leading to thrombin generation and opsonisation with C3b.
Baerga-Ortiz, Bajzar, Boehme, Bossi, Campbell, Conway, de Córdoba S, Delvaeye, Dragon-Durey, Esmon, Esmon, Esmon, Esparza-Gordillo, Faust, Fuentes-Prior, Gordon, Hakobyan, Hamad, Harris, Heurich, Hindmarsh, Honda, Huntington, Ikeda, Ito, Jokiranta, Kavanagh, Li, Light, Maga, Markiewski, Martinez-Barricarte, Mayer, Meri, Mizuno, Moll, Morgan, Mouksassi, Noris, Owen, Pangburn, Sadler, Sadler, Saito, Salem, Sawada, Schramm, Shental-Bechor, Suzuki, Tateishi, Tortajada, Udagawa, Vincent, Walport, Walport, Wu, Yada, Yamamoto, Zushi   +58 more
core   +1 more source

Predisposition to atypical hemolytic uremic syndrome involves the concurrence of different susceptibility alleles in the regulators of complement activation gene cluster in 1q32 [PDF]

, 2005
Jorge Esparza-Gordillo, Elena Goicoechea de Jorge, Alfonso Buil, Luis Carreras Berges, Margarita López‐Trascasa, Pilar Sánchez‐Corral, Santiago Rodrı́guez de Córdoba   +6 more
openalex   +1 more source