Results 271 to 280 of about 22,851 (287)

The treatment of phenylalanine hydroxylase (PAH)-deficient BH4-responsive patints with tetrahydrobiopterin (BH4): tolerance to Phe and response to BH4.

2005
LEUZZI, Vincenzo, CARDUCCI, Claudia, DE LEO S, MONTIERI P, CARDUCCI, Carla, ANTONOZZI I.   +5 more
openaire   +2 more sources

Improved metabolic control in tetrahydrobiopterin (BH4), responsive phenylketonuria with sapropterin administered in two divided doses vs. a single daily dose

Journal of Pediatric Endocrinology and Metabolism, 2017
Deniz Kor, Halise Neslihan Önenli, Berna Seker Yilmaz   +2 more
exaly  

BH4 antagonists and methods related thereto

2015
DENG XINGMING, ZHOU JIA, DING CHUNYONG
openaire   +4 more sources

Targeting Bcl-2 based on the interaction of its BH4 domain with the inositol 1,4,5-trisphosphate receptor

Biochimica Et Biophysica Acta - Molecular Cell Research, 2009
Paul M Barr, Clark W Distelhorst, Vivien C Yee   +2 more
exaly  

Study on the dehydrogenation properties and reversibility of Mg(BH4)2AlH3 composite under moderate conditions

, 2017
Jiaguang Zheng, Xue-Zhang Xiao, Liuting Zhang, Yan He, Shouquan Li, Hong-Wei Ge, Lixin Chen   +6 more
semanticscholar   +1 more source

Facile synthesis of bowl-like 3D Mg(BH4)2–NaBH4–fluorographene composite with unexpected superior dehydrogenation performances

, 2017
Jiaguang Zheng, Xue-Zhang Xiao, Liuting Zhang, Shouquan Li, Hong-Wei Ge, Lixin Chen   +5 more
semanticscholar   +1 more source

BH4-responsive Mild PKU

2009
Alexander K. C. Leung, Marcus Schmitt, Christie P. Thomas, Cord Sunderkötter, Meinhard Schiller, Thomas Schwarz, Mark Berneburg, Alfried Kohlschütter, Lorenzo Cerroni, Haner Direskeneli, Kenneth Calamia, Gloria L. David, Darryl C. Zeldin, Bärbel Schütte, Lee A. Denson, Andreas Erhardt, Ralf Kubitz, Dieter Häussinger, Wendy M. Sealey, Donald M. Mock, Barry Wolf, Johannes Schumacher, Peter Propping, Dieter Metze, Alexander K. C. Leung, Andrew L. Wong, Mark Berneburg, Thomas Schwarz, Markus Hengstschläger, Whitney A. High, Kenneth R. Shroyer, M. Elizabeth McCready, Dennis E. Bulman, Ali R. Afzal, David B. Everman, Claude Stoll, Sukran Darcan, Yu Ru Kou, You Shuei Lin, Yoichi Suzuki, Keiya Tada, Alexander K. C. Leung, Susan Kupka, Wolfgang Dietmaier, Arndt Hartmann, Raoul C. M. Hennekam, John A. Belperio, Michael P. Keane, M. Iain Smith, Robert M. Strieter, Nestor A. Molfino, Francesca Sciandra, Tom Rossenbacker, Silvia G. Priori, Marco Senzolo, Christos Triantos, Dimitrios Samonakis, Evangelos Cholongitas, Andrew K. Burroughs, Marco Mura, Markus Braun-Falco, Silke Hofmann, Leena Bruckner-Tuderman   +62 more
openaire   +1 more source

Carbon metabolism characteristics of quorum quenching bacteria sp. BH4 determine the bioaugmentation efficiency under different carbon source conditions

Water Research
Xiujie Wang, Dongbo Liang, Dongyue Li
exaly  

Destabilisation of Ca(BH4)2 and Mg(BH4)2via confinement in nanoporous Cu2S hollow spheres

, 2017
Qi-Wen Lai, Kondo-François Aguey-Zinsou
semanticscholar   +1 more source

Tetrahydrobiopterin (BH4) responsiveness and long-term treatment with BH4 in hyperphenyalaninemia

2008
Scala I, Ungaro C, Paladino S, Nastasi A, Zuppaldi A, Sibilio M, Figliuolo C, Scarpato E, Capaldo B, Cardillo G, Daniele A, DELLA CASA, ROBERTO, PARENTI, GIANCARLO, ANDRIA, GENEROSO   +13 more
openaire   +1 more source