Results 11 to 20 of about 226,924 (326)

Association of Gut Microbiota and Metabolites With Disease Progression in Children With Biliary Atresia

Frontiers in Immunology, 2021
Background and AimsBiliary atresia is the most common cause of liver disease and liver transplantation in children. The accumulation of bile acids in hepatocytes and the stimulation of the intestinal microbiome can aggravate the disease progression. This
Wei Song, Wei Song, Li-Ying Sun, Li-Ying Sun, Li-Ying Sun, Zhi-Jun Zhu, Zhi-Jun Zhu, Lin Wei, Lin Wei, Wei Qu, Wei Qu, Zhi-Gui Zeng, Zhi-Gui Zeng, Ying Liu, Ying Liu, Hai-Ming Zhang, Hai-Ming Zhang, Wei Guo   +17 more
doaj   +2 more sources

Japanese biliary atresia registry [PDF]

World Journal of Pediatric Surgery
The Japanese Biliary Atresia Registry (JBAR) was launched in 1989 by the Japanese Biliary Atresia Society (JBAS) to investigate the epidemiology and etiology of biliary atresia and to improve surgical outcomes.
Masaki Nio, Ryuji Okubo, Hideyuki Sasaki, Motoshi Wada   +3 more
doaj   +2 more sources

Development and validation of bile acid profile-based scoring system for identification of biliary atresia: a prospective study

BMC Pediatrics, 2020
Background Early distinguishing biliary atresia from other causes of infantile cholestasis remains a major challenge. We aimed to develop and validate a scoring system based on bile acid for identification of biliary atresia.
Dongying Zhao, Kejun Zhou, Yan Chen, Wei Xie, Yongjun Zhang   +4 more
doaj   +2 more sources

Organoids in biliary atresia. [PDF]

World J Pediatr Surg
Organoids are three-dimensional and self-organizing cell cultures of various lineages that resemble structures and functions of an organ in many ways, and they are versatile tools in disease modeling and patho-mechanistic study of human diseases affecting their tissues of origin.
Lui VCH.
europepmc   +4 more sources

Biliary atresia

Medisur, 2005
Biliary atresia is an obstructive and progressive process of unknown etiology that affects intra and/or extrahepatics biliary tracts and cause neonatal jaundice by serious obstruction of the biliary flow.
Miurkis Endis Miranda, Ramón Villamil Martínez, Pastor Thomas Olivares   +2 more
doaj   +5 more sources

Physical development and cognitive performance in a monozygotic twins for biliary atresia: Report of a case and literature reviewing

Journal of Pediatric Surgery Case Reports, 2016
A case of monozygotic twins, one of whom suffered from biliary atresia and the other one was apparently healthy, is described herein. Children with biliary atresia appear to be vulnerable to developmental lags in the physical and cognitive performance ...
Yang Chen, Jianghua Zhan
doaj   +2 more sources

Process Model for Transitioning Care Responsibility to Adolescents and Young Adults with Biliary Atresia: A Secondary and Integrative Analysis. [PDF]

Nurs Rep
Hiratsuka K, Nakamura N.
europepmc   +3 more sources

Biliary Atresia [PDF]

Journal of Indian Association of Pediatric Surgeons, 2008
Biliary atresia (BA) is a cholangiodestructive disease affecting biliary tract, which ultimately leads to cirrhosis, liver failure and death if not treated. The incidence is higher in Asian countries than in Europe. Up to 10% of cases have other congenital anomalies, such as polysplenia, asplenia, situs inversus, absence of inferior vena cava and pre ...
Sinha, C.K., Davenport, Mark
openaire   +5 more sources

Outcomes of 38 patients with PFIC3: Impact of genotype and of response to ursodeoxycholic acid therapy

JHEP Reports, 2023
Background & Aims: Progressive familial intrahepatic cholestasis type 3 (PFIC3) is a rare liver disease caused by biallelic variations in ABCB4. Data reporting on the impact of genotype and of response to ursodeoxycholic acid (UDCA) therapy on long ...
Emmanuel Gonzales, Antoine Gardin, Marion Almes, Amaria Darmellah-Remil, Hanh Seguin, Charlotte Mussini, Stéphanie Franchi-Abella, Mathieu Duché, Oanez Ackermann, Alice Thébaut, Dalila Habes, Bogdan Hermeziu, Martine Lapalus, Thomas Falguières, Jean-Philippe Combal, Bernard Benichou, Sonia Valero, Anne Davit-Spraul, Emmanuel Jacquemin   +18 more
doaj   +1 more source

Serum FGF19 predicts outcomes of Kasai portoenterostomy in biliary atresia

Hepatology, 2023
Background and Aims: Outcomes after Kasai portoenterostomy (KPE) for biliary atresia remain highly variable for unclear reasons. As reliable early biomarkers predicting KPE outcomes are lacking, we studied the prognostic value of FGF19.
I. Nyholm, M. Hukkinen, M. Pihlajoki, J. Davidson, A. Tyraskis, J. Lohi, P. Heikkilä, Satu Hänninen, Noora Andersson, K. Eloranta, O. Carpén, M. Heikinheimo, M. Davenport, M. Pakarinen   +13 more
semanticscholar   +1 more source