Results 21 to 30 of about 226,924 (326)
Pediatrics In Review, 2006 Biliary atresia (BA) is a rare disease characterised by a biliary obstruction of unknown origin that presents in the neonatal period. It is the most frequent surgical cause of cholestatic jaundice in this age group. BA occurs in approximately 1/18,000 live births in Western Europe.
Garret S, Zallen +4 more
openaire +7 more sources
Biliary Atresia in 2021: Epidemiology, Screening and Public Policy
Journal of Clinical Medicine, 2022 Biliary atresia (BA) is a rare newborn liver disease with significant morbidity and mortality, especially if not recognized and treated early in life.
R. Schreiber +3 more
semanticscholar +1 more source
Clinical Case Reports, 2023 Key Clinical Message A newborn with a rare form of biliary atresia had posterior fossa bleed and subarachnoid hemorrhage despite vitamin K prophylaxis, indicating biliary atresia is a causality rather than chance.
Susmin Karki +5 more
doaj +1 more source
Newborn Screening for Biliary Atresia: a Review of Current Methods
Current Gastroenterology Reports, 2021 Tebyan Rabbani +4 more
openalex +3 more sources
Risk of variceal hemorrhage and pretransplant mortality in children with biliary atresia
Hepatology, 2022 The natural history of gastroesophageal variceal hemorrhage (VH) in biliary atresia (BA) is not well characterized. We analyzed risk factors, incidence, and outcomes of VH in a longitudinal multicenter study.
Lee M. Bass +18 more
semanticscholar +1 more source
Hepatology, EarlyView., 2022 Natural history of liver disease in a large international cohort of children with Alagille syndrome: Results from the GALA study. Abstract Background and Aims Alagille syndrome (ALGS) is a multisystem disorder, characterized by cholestasis. Existing outcome data are largely derived from tertiary centers, and real‐world data are lacking.
Shannon M. Vandriel +93 more
wiley +1 more source
Interleukin‐18 signaling promotes activation of hepatic stellate cells in mouse liver fibrosis
Hepatology, EarlyView., 2022 Interleukin‐18 signaling promotes activation of hepatic stellate cells in mouse liver fibrosis. Abstract Background and Aims Nucleotide‐binding oligomerization domain‐like receptor‐family pyrin domain‐containing 3 (NLRP3) inflammasome activation has been shown to result in liver fibrosis.
Jana Knorr +19 more
wiley +1 more source
Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy
Hepatology, EarlyView., 2022 Serum bile acid levels predict outcomes in patients with biliary atresia who achieve normalized bilirubin levels after Kasai portoenterostomy. Abstract Background and Aims In biliary atresia, serum bilirubin is commonly used to predict outcomes after Kasai portoenterostomy (KP).
Sanjiv Harpavat +22 more
wiley +1 more source
Pathogenesis of biliary atresia: defining biology to understand clinical phenotypes
Nature Reviews Gastroenterology and Hepatology, 2015 Akihiro Asai +2 more
exaly +2 more sources
Alagille Syndrome Mimicking Biliary Atresia in Early Infancy. [PDF]
PLoS ONE, 2015 Alagille syndrome may mimic biliary atresia in early infancy. Since mutations in JAG1 typical for Alagille syndrome type 1 have also been found in biliary atresia, we aimed to identify JAG1 mutations in newborns with proven biliary atresia (n = 72). Five
Tomáš Dědič +5 more
doaj +1 more source