Results 41 to 50 of about 98,834 (305)

HAE international home therapy consensus document [PDF]

, 2010
Hereditary angioedema (C1 inhibitor deficiency, HAE) is associated with intermittent swellings which are disabling and may be fatal. Effective treatments are available and these are most useful when given early in the course of the swelling.
Bowen, Tom, Craig, Timothy, Boysen, Henrik, E. Aygören Pürsün, Janet Long, Zuraw Bruce, Avner Reshef, Longhurst, Hilary J., Cicardi Marco, Bygum, Anette, Hilary J Longhurst, Bruce Zuraw, Anette Bygum, Martinez-Saguer, Inmaculada, Bork Konrad, Inmaculada Martinez-Saguer, Sofia Grigoriadou, Caballero, Teresa, Claire Bethune, I. Martinez Saguer, Reshef Avner, Martinez Saguer, Inmaculada, M. Raguet, H. J. Longhurst, J. Bjorkander, Laurence Bouillet, Levi Marcel M, Raguet Michel, Timothy Craig, Bethune Claire, T. Bowen, Michel Raguet, L. Bouillet, Marco Cicardi, Gompels Mark, Bork, Konrad, C. Bethune, Dempster, John, Huffer Ursula, Marcel M Levi, Longhurst, Hilary, Aygören-Pürsün Emel, M. Cicardi, Farkas Henriette, Henriette Farkas, Raguet, Michel, Bygum Anette, Bjorkander Janne, Levi, Marcel M, Longhurst Hilary J, Martinez-Saguer Inmaculada, Teresa Caballero, Ursula Huffer, Bouillet, Laurence, H. Farkas, Boysen Henrik, Huffer, Ursula, M. M. Levi, M. Gompels, Gompels, Mark, S. Grigoriadou, Kreuz, Wolfhart, Janne Bjorkander, A. Bygum, Craig Timothy, Longhurst, Hilary J, Farkas, Henriette, Bygum, Anette; id_orcid, Bowen Tom, Gooi Jimmy, Bouillet Laurence, Boysen, Henrik B., A. Reshef, J. Gooi, J. Dempster, Konrad Bork, Henrik Boysen, Gooi, Jimmy, Jimmy Gooi, Cicardi, Marco, T. Craig, B. Zuraw, Caballero Teresa, Bethune, Claire, U. Huffer, Levi, Marcel M., Dempster John, John Dempster, Grigoriadou Sofia, Reshef, Avner, Long Janet, H. Boysen, Grigoriadou, Sofia, Bjorkander, Janne, T. Caballero, Tom Bowen, Zuraw, Bruce, J. Long, W. Kreuz, Mark Gompels, Emel Aygören-Pürsün, Aygören-Pürsün, Emel, K. Bork, Kreuz Wolfhart, Long, Janet, Wolfhart Kreuz   +105 more
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2010 international consensus algorithm for the diagnosis, therapy and management of hereditary angioedema [PDF]

, 2010
Background We published the Canadian 2003 International Consensus Algorithm for the Diagnosis, Therapy, and Management of Hereditary Angioedema (HAE; C1 inhibitor [C1-INH] deficiency) and updated this as Hereditary angioedema: a current state-of-the-art ...
S. Waserman, Harmat, George, E. Leith, Bernstein Jonathan, Bowen, Tom, Leith, Eric, Doris Neurath, Craig, Timothy, Paul K Keith, Eric Leith, A. Hamed, D. Moldovan, Zuraw Bruce, Betschel Stephen, Avner Reshef, Dean, John, Cicardi Marco, Moldovan, Dumitru, Lilian Varga, Hilary J Longhurst, Rowe Anne, Nordenfelt Patrik, Barbara Mako, Harmat George, B. Ritchie, Martinez-Saguer, Inmaculada, Fust George, Della Cogar, Inmaculada Martinez-Saguer, George Fust, Devaraj, Ramachand, Mike Frank, Richard Warrington, J. Bernstein, Rowan, Dereth, Nielsen Erik W, Li, Henry, Tsai Ellie, D. Cogar, Timothy Craig, Zhi Xiang, Poon Man-Chiu, J. Brosz, E. Tsai, Marco Cicardi, R. Schellenberg, R. Warrington, Sur, Smeeksha, B. Mako, I. Nagy, Bork, Konrad, Frank Mike, George Harmat, Frank, Mike, Karen Binkley, H. Lyons, Schellenberg, Robert, Longhurst, Hilary, Erik W Nielsen, L. Varga, Farkas Henriette, Henriette Farkas, Mako, Barbara, Devaraj Ramachand, Longhurst Hilary J, G. E. Rivard, Rusicke, Eva, Hamed, Azza, Kreuz, Wolfhart, Eva Rusicke, Poon, Man-Chiu, Späth, Peter, Binkley Karen, Anne Rowe, Craig Timothy, Istvan Nagy, Neurath, Doris, Xiang, Zhi Yu, Bowen Tom, E. W. Nielsen, Lacuesta, Gina, Sean Mace, Bouillet Laurence, Nagy Istvan, Lacuesta Gina, Brosz Kristylea, Nielsen, Erik W, John Brosz, D. Rowan, D. Neurath, Peter Späth, A. Kanani, Nagy, Istvan, Ameratunga Rohan, Bruce Ritchie, Aygoeren-Pürsün Emel, Li Henry, A. Rowe, G. Lacuesta, Keith Paul K, B. Zuraw, T. Craig, Ritchie, Bruce, Caballero Teresa, Cogar Della, S. Mace, M. Frank, Dumitru Moldovan, S. Betsche, Mace Sean, M. Poon, Zhi Yu Xiang, Lyons, Harriet, Waserman Susan, J. Dean, T. Caballero, Xiang Zhi, Tom Bowen, Rohan Ameratunga, Gina Lacuesta, M. Levi, Smith-Foltz Sarah, S. Sur, Brosz, John, Björkander, Janne, Aygören-Pürsün, Emel, Warrington Richard, Aygoeren-Pürsün, Emel, Susan Waserman, Binkley, Karen, Waserman, Susan, Ritchie Bruce, Donald Stark, Keith, Paul K, Xiang, Zhi Y, Bygum, Anette, Bruce Zuraw, Anette Bygum, H. Li, R. Ameratunga, Bork Konrad, Robert Schellenberg, Rivard Georges-Etienne, Sarah Smith-Foltz, Caballero, Teresa, I. Martinez Saguer, Reshef Avner, Martinez Saguer, Inmaculada, H. J. Longhurst, Varga Lilian, J. Björkander, Laurence Bouillet, Palinder Kamra, Leith Eric, Betschel, Stephen, Bernstein, Jonathan, Ellie Tsai, T. Bowen, K. Brosz, Ramachand Devaraj, J. Hebert, Rowe, Anne, L. Bouillet, Kristylea Brosz, Dereth Rowan, Marcel Levi, Neurath Doris, P. Späth, Kanani, Amin, G. Harmat, M. Cicardi, Kanani Amin, Bygum Anette, Stephen Betschel, Sur Smeeksha, Martinez-Saguer Inmaculada, G. Fust, Nordenfelt, Patrik, Teresa Caballero, Bouillet, Laurence, Fust, George, H. Farkas, Jonathan Bernstein, Levi, Marcel, Jacques Hebert, Keith, Paul K., Stark, Donald, P. Nordenfelt, Hebert, Jacques, Xiang, Zhi, Warrington, Richard, D. Stark, Harriet Lyons, A. Bygum, Longhurst, Hilary J, Stark Donald, Henry Li, Rowan Dereth, Farkas, Henriette, Lyons Harriet, Bygum, Anette; id_orcid, Levi Marcel, Kamra, Palinder, Dean John, Ameratunga, Rohan, E. Aygoeren Pürsün, A. Reshef, Brosz, Kristylea, Janne Björkander, R. Devaraj, Konrad Bork, P. K. Keith, Björkander Janne, Kamra Palinder, Bernstein, Jonathan A., Späth Peter, Azza Hamed, Schellenberg Robert, P. Kamra, Cicardi, Marco, Amin Kanani, Mace, Sean, Smeeksha Sur, Levi, Marcel M., Y. X. Zhi, Varga, Lilian, Reshef, Avner, S. Smith Foltz, Georges-Etienne Rivard, Rusicke Eva, Rivard, Georges-Etienne, Smith-Foltz, Sarah, K. Binkley, Yu Xiang, Zhi, Emel Aygoeren-Pürsün, Cogar, Della, Hebert Jacques, Patrik Nordenfelt, E. Rusicke, Brosz John, John Dean, Mako Barbara, Zuraw, Bruce, Moldovan Dumitru, W. Kreuz, K. Bork, Tsai, Ellie, Kreuz Wolfhart, Man-Chiu Poon, Wolfhart Kreuz, Nielsen, Erik W., Hamed Azza   +251 more
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Nine year follow-up of a rare case of angioedema due to acquired C1-inhibitor deficiency with late onset and good response to attenuated androgen

Allergy, Asthma & Clinical Immunology, 2018
Background Angioedema due to acquired deficiency of C1-inhibitor (C1-INH-AAE) is a rare disease sharing some clinical and laboratory similarities with hereditary angioedema, but with late onset and no positive family history. The underlining cause may be
Polliana Mihaela Leru, Vlad Florin Anton, Horia Bumbea   +2 more
doaj   +1 more source

Abstracts of 11th C1-inhibitor Deficiency & Angioedema Workshop [PDF]

Allergy, Asthma & Clinical Immunology, 2019
doaj   +2 more sources

Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature

Case Reports in Otolaryngology, 2012
Angioedema related to a deficiency in the C1-inhibitor protein is characterized by its lack of response to therapies including antihistamine, steroids, and epinephrine. In the case of laryngeal edema, mortality rate is approximately 30 percent. The first
Bassel Hallak, Propser Konu, Florian Lang, Christian Simon, Philippe Monnier   +4 more
doaj   +1 more source

Hereditary angioedema C1-esterase inhibitor replacement therapy and coexisting autoimmune disorders: findings from a claims database

Allergy, Asthma & Clinical Immunology, 2020
In this letter to the editor, we present results of claims data analysis. This claims data analysis supports a hypothesis that in patients with hereditary angioedema due to C1-esterase inhibitor (C1-INH) deficiency, the occurrence and/or symptomatology ...
Henriette Farkas, Donald Levy, Dylan Supina, Melvin Berger, Subhransu Prusty, Moshe Fridman   +5 more
doaj   +1 more source

HAE-AS, a specific disease activity scale for hereditary angioedema with C1-inhibitor deficiency.

Journal of investigational allergology & clinical immunology, 2020
BACKGROUND AND OBJECTIVE Hereditary angioedema due to C1-inhibitor deficiency (C1-INH-HAE) shows variability in disease activity among patients and within individual patients.
M. JoãoForjaz, A. Ayala, M. Caminoa, N. Prior, E. Pérez-Fernández, T. Caballero   +5 more
semanticscholar   +1 more source

Pediatric hereditary angioedema: an update [version 1; referees: 2 approved]

F1000Research, 2017
Hereditary angioedema (HAE) with C1-inhibitor (C1-Inh) deficiency (C1-Inh-HAE) is a rare, life-threatening, and disabling genetic disorder characterized by self-limited tissue swelling caused by deficiency or dysfunction of C1-Inh. Our aim in this update
Geetika Sabharwal, Timothy Craig
doaj   +1 more source

A novel deep intronic SERPING1 variant as a cause of hereditary angioedema due to C1-inhibitor deficiency.

Allergology International, 2020
BACKGROUND In about 5% of patients with hereditary angioedema due to C1-inhibitor deficiency (C1-INH-HAE) no mutation in the SERPING1 gene is detected.
Sofia Vatsiou, M. Zamanakou, Gedeon Loules, F. Psarros, Faidra Parsopoulou, D. Csuka, A. Valerieva, M. Staevska, G. Porębski, K. Obtulowicz, M. Magerl, M. Maurer, M. Speletas, H. Farkas, A. Germenis   +14 more
semanticscholar   +1 more source

The hereditary angioedema burden of illness study in Europe (HAE-BOIS-Europe) : background and methodology [PDF]

, 2012
Background: Hereditary angioedema (HAE) is a rare but serious disease marked by swelling attacks in the extremities, face, trunk, airway, or abdominal areas that can be spontaneous or the result of trauma and other triggers.
Beusterien, Kathleen, Caballero, Teresa, Boysen, Henrik, Boysen, Henrik B., Musingarimi, Patience, Emel Aygören-Pürsün, Kathleen Beusterien, Gholizadeh, Shadi, Bygum, Anette, Wait, Suzanne, Patience Musingarimi, Aygören-Pürsün, Emel, Teresa Caballero, Suzanne Wait, Henrik Boysen, Anette Bygum, Shadi Gholizadeh, Bygum, Anette; id_orcid   +17 more
core   +1 more source