Results 81 to 90 of about 98,834 (305)
Pathogenetic and Clinical Aspects of C1 Inhibitor Deficiency
Immunobiology, 1998 People deficient in C1-INH present recurrent angioedema localized to subcutaneous or mucous tissues. The defect can be caused by impaired synthesis, due to a genetic defect (hereditary angioedema), or by increased catabolism (acquired angioedema). In our experience the majority of patients with acquired angioedema (16 of 18) have autoantibodies to C1 ...
M. Cicardi +6 more
openaire +2 more sources
C1-inhibitor deficiency and angioedema : molecular mechanisms and clinical progress
, 2009 C1 inhibitor (C1-INH, also known as SERPING1) can be deficient in plasma as a result of genetic or acquired conditions, and this causes an episodic, local increase in vascular permeability in the subcutaneous and submucosal layers, identified as ...
A. Zanichelli +9 more
core +1 more source
Evaluating the involvement of autolysosomes in the nuclear translocation of fluorescent proteins
FEBS Open Bio, EarlyView.Endogenously expressed fluorescent proteins can be degraded by autophagy and transported to cell nuclei via the nuclear pore complex. But in some cell lines, for example, HeLa cells which are positive for immunoreactivity of a receptor ligand, such as UCN I, in cell nuclei, fusion of autolysosome with the nuclear envelope is involved in the nuclear ...
Keiichi Ikeda
wiley +1 more source
Orphanet Journal of Rare Diseases, 2022 Hereditary angioedema (HAE) is a rare autosomal dominant genetic disease characterized by repetitive subcutaneous or submucosal angioedema, activation of the kinin system, and increased vascular permeability.
Yinshi Guo +6 more
doaj +1 more source
Life expectancy in Italian patients with hereditary angioedema due to C1 inhibitor deficiency.
Journal of Allergy and Clinical Immunology: In Practice, 2020 Life expectancy in Italian patients with hereditary angioedema due to C1-inhibitor deficiency Francesca Perego, MD, Antonio Gidaro, MD, Andrea Zanichelli, MD, Mauro Cancian, MD, Francesco Arcoleo, MD, Riccardo Senter, MD, Maria Bova, MD, Tiziana De ...
F. Perego +12 more
semanticscholar +1 more source
3D Printing Innovations in Polymeric Porous and Patterned Architecture
Advanced Functional Materials, EarlyView.Polymeric foams occupy a unique structural space between dense solids and open networks, where engineered void fraction governs mechanical compliance, thermal resistance, and mass transport. Additive manufacturing now enables precise spatial control over cellular architecture, unlocking designer foam structures across applications spanning crash ...
Dhanush Patil +13 more
wiley +1 more source
Case Reports in UrologyAcquired angioedema with low C1-inhibitor (AAE-C1-INH) is a rare disorder characterized by an acquired deficiency in the C1 esterase inhibitor (C1-INH). This case report describes a 79-year-old patient presenting to the emergency department for painless ...
Meghan V. Matheny +2 more
doaj +1 more source
Advanced Functional Materials, EarlyView.This work developed a smart Janus wood membrane integrating asymmetric wettability with built‐in electrical sensing for oil‐water separation. The membrane achieved > 99.5% separation efficiency and high flux by leveraging wood's natural anisotropic pore structure.
Kaiwen Chen +10 more
wiley +1 more source
Advanced Functional Materials, EarlyView.A nanounit‐assembled hydrogel employing a “pull‐and‐push” strategy simultaneously scavenges pro‐inflammatory cell‐free DNA (cfDNA) and delivers regenerative therapeutics in response to burn‐induced hyperthermia. By repolarizing macrophages and promoting angiogenesis, this multifunctional platform accelerates burn wound healing, offering a blueprint for
Han‐Sem Kim +9 more
wiley +1 more source
Allergy, Asthma & Clinical Immunology, 2018 Background Hereditary angioedema due to C1 inhibitor deficiency (C1-INH-HAE) is a rare autosomal dominant disease characterized by episodes of acute subcutaneous swelling, and/or recurrent severe abdominal pain.
Anna Valerieva +3 more
doaj +1 more source