Results 21 to 30 of about 69,714 (253)
We present the case of PRKAG2 cardiac syndrome, a rare autosomal-dominant genetic disease characterized by peculiar clinical and electrophysiological abnormalities. We clearly show through the images the peculiar clinical features that should raise suspicion of a mutant PRKAG2 gene. Indeed, together with an accurate clinical and instrumental evaluation,
Fabris E +9 more
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Cardiac arrhythmias and conduction disturbances are accompanied by structural remodelling of the specialised cardiomyocytes known collectively as the cardiac conduction system.
Robert S. Stephenson +11 more
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Rapidly Progressive Cardiac Manifestation of Behçet's Disease Involving Conduction System and Aortic Valve [PDF]
Cardiac conduction system impairment is a rare clinical manifestation of Behçet's disease. We report a patient who showed 1st degree atrioventricular block at first presentation, and showed aggravated finding of 3rd degree atrioventricular block on five months later.
Yu, Jin Sok +9 more
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Predictive factors of atrioventricular conduction disorders [PDF]
Atrioventricular conduction disorders represent an alteration in the normal function of the heart’s electrical conduction system, a system that connects the atria and ventricles through the atrio-ventricular node and the His-Purkinje system. Consequently,
Carmen Marina Deutsch +2 more
doaj +1 more source
Left bundle branch–optimized cardiac resynchronization therapy: Pursuing the optimal resynchronization in severe (distal) conduction system disease [PDF]
Contains fulltext : 294265.pdf (Publisher’s version ) (Open Access)
Jesse Rijks +2 more
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An uncommon case of complete AV block
Background Granulomatosis with polyangiitis (GPA) is a rare systemic inflammatory disorder characterized by vasculitis of the small vessels, as well as necrotizing granulomatous lesions, affecting mainly upper and lower respiratory tracts, lungs and ...
Federica Valente +3 more
doaj +1 more source
Limited effects of long-term enzyme replacement therapy on the cardiac conduction system in Fabry disease [PDF]
The long-term effects of enzyme replacement therapy (ERT) on cardiac function and the conduction system in Fabry disease are not clearly understood. We report a case of a 48-year-old man with non-classical Fabry disease treated with ERT for 11 years.
Tomoya, Kaneda +10 more
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An unusual reason for complete atrioventricular block ; Kearn Sayre Syndrome
Kearn sayre syndrome (KSS) is a rare disease with a typical onset before 20 years and charactarized by triad of chronic progressive external ophthalmoplegia, retinitis pigmentosa and progressive cardiac conduction abnormalities.
Halil Atas, Fuad Samadov, Osman Yesildag
doaj +1 more source
Electrocardiographic Effects of Cholinesterase Inhibitors in Patients with Alzheimer’s Disease
Aim:Cholinesterase inhibitors (ChEIs), such as donepezil and rivastigmine, are used safely in the treatment of Alzheimer’s disease (AD). However, the effects of these drugs on the cardiac conduction system are not clear.
Ayşe ÇOLAK, Didem ÖZ
doaj +1 more source
An adjuvant therapy in cervical necrotising fasciitis: hyperbaric oxygen treatment
Kearn sayre syndrome (KSS) is a rare disease with a typical onset before 20 years and characterized by triad of chronic progressive external ophthalmoplegia, retinitis pigmentosa and progressive cardiac conduction abnormalities.
Nuray Ensari +5 more
doaj +1 more source

