Pancreatic, nutritional and clinical outcomes in children 0-5 years with cystic fibrosis during the first 2 years of CFTR modulator therapy (PaNC): a multicentre prospective observational study protocol. [PDF]
Miles C +18 more
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Kidney effects of triple CFTR modulator therapy in people with cystic fibrosis. [PDF]
Gabai P +7 more
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The effect of triple CFTR modulator therapy and azithromycin on ion channels and inflammation in cystic fibrosis. [PDF]
Bani Melhim S +4 more
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Type 2 inflammation in cystic fibrosis is a predictor of mortality and targeted with CFTR modulator therapy. [PDF]
Cook DP +5 more
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Changing profile of bacterial infection and microbiome in cystic fibrosis: when to use antibiotics in the era of CFTR-modulator therapy. [PDF]
Milczewska J +4 more
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Heightened mitochondrial respiration in CF cells is normalised by triple CFTR modulator therapy through mechanisms involving calcium. [PDF]
Jarosz-Griffiths HH +6 more
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Heterogeneity of CFTR modulator-induced sweat chloride concentrations in people with cystic fibrosis. [PDF]
Zemanick ET +10 more
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Organic Synthesis and Current Understanding of the Mechanisms of CFTR Modulator Drugs Ivacaftor, Tezacaftor, and Elexacaftor. [PDF]
Ferreira FC +2 more
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Considerations for the use of inhaled antibiotics for Pseudomonas aeruginosa in people with cystic fibrosis receiving CFTR modulator therapy. [PDF]
Burgel PR +10 more
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Laboratory Tools to Predict CFTR Modulator Therapy Effectiveness and to Monitor Disease Severity in Cystic Fibrosis. [PDF]
Bacalhau M, Camargo M, Lopes-Pacheco M.
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