Endogenous Viral Etiology of Prion Diseases [PDF]
, 2009 Transmissible spongiform encephalopathies (TSEs), or prion diseases, are a group of incurable neurodegenerative disorders, including Kuru and Creutzfeldt-Jakob disease in humans, “mad cow” disease in cattle, and scrapie in sheep. This paper
Claudiu I. Bandea
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Chinese Journal of Contemporary Neurology and Neurosurgery, 2013 Creutzfeldt⁃Jakob disease (CJD) is a degenerative central nervous system (CNS) disease caused by infection of prion protein (PrP), with clinical features including short course, rapid development and 100% mortality.
Lin WANG, Jian-rong LIU
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Complicated symptomatology and diagnosis of Creuzfeld-Jakob disease on a basis of clinical case
Quality in SportCreutzfeldt-Jakob disease (CJD) is a rare condition. In this study we describe the diagnosis of the disease in a 73-year old female, presenting dementia. Diagnostic tests unveiled characteristic features of CJD. The diagnosis of CJD was confirmed. It is
Marta Jurga +9 more
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MRI and clinical syndrome in dura materrelated Creutzfeldt-Jakob disease [PDF]
, 2018 Objective : Iatrogenic Creutzfeldt-Jakob disease (iCJD) is mainly associated with dura mater (DM) grafts and administration of human growth hormones (hGH). Data on disease course in DM-CJD are limited.
Barsic, B. +12 more
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Does Improvement in Case Ascertainment Explain the Increase in Sporadic Creutzfeldt-Jakob Disease Since 1970 in the United Kingdom? [PDF]
, 2017 The aim of this study was to quantify the improvements in case ascertainment which are considered to explain the rise in the incidence of sporadic Creutzfeldt-Jakob disease.
Cohen, Carine H.
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Arquivos de Neuro-Psiquiatria, 1976 É apresentado caso sugestivo de doença de Creutzfeldt-Jakob em adulto jovem. O estudo anátomo-patológico revelou alteração difusa no córtice cerebral, núcleos da base e medula, constituídas por degeneração neuronal, gliose, espongiose e infiltração ...
Osvaldo J. M. Nascimento +1 more
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A survey and a molecular dynamics study on the (central) hydrophobic region of prion proteins
, 2014 Prion diseases are invariably fatal neurodegenerative diseases that affect humans and animals. Unlike most other amyloid forming neurodegenerative diseases, these can be highly infectious. Prion diseases occur in a variety of species.
Wang, Feng, Zhang, Jiapu
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Neuroimagen estructural y funcional en las enfermedades priónicas humanas [PDF]
, 2011 INTRODUCTION: Prion diseases are neurodegenerative disorders resulting from the accumulation of a misfolded isoform of the cellular prion protein (PrPc). They can occur as acquired, sporadic or hereditary forms. Although prion diseases show a wide range
Arbizu, J. (Javier) +6 more
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Cellular distribution of the prion protein in palatine tonsils of mule deer (Odocoileus hemionus) and Rocky Mountain elk (Cervus elaphus nelsoni) [PDF]
, 2019 Chronic wasting disease (CWD) is a transmissible spongiform encephalopathy (TSE) that affects members of the Cervidae family, including deer (Odocoileus spp.), elk (Cervus Canadensis spp.), and moose (Alces alces spp.).
Belden, E. Lee +2 more
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A case of CreutzfeldtâJakob disease presenting with bilingual Gerstmann syndrome
Archives of Clinical Neuropsychology, 2000 openaire +1 more source