Results 101 to 110 of about 316,034 (278)

Cutaneous mastocytosis: Two pediatric cases treated with topical pimecrolimus. [PDF]

, 2010
Cutaneous mastocytosis is characterized by increased numbers of skin mast cells that release mediators causing pruritus, urticaria, and flushing. Most pediatric mastocytosis patients exhibit the pattern of urticaria pigmentosa, which typically appears ...
Azevedo, R, Correia, O, Delgado, L, Duarte, AF, Quirino, P   +4 more
core   +1 more source

Diagnosis, management and the burden of symptoms of mastocytosis from the physician's perspective: A nationwide study

British Journal of Haematology, Volume 207, Issue 5, Page 1973-1981, November 2025.
Summary Mastocytosis is categorized into cutaneous mastocytosis (CM), mast cell sarcoma and systemic mastocytosis (SM). Within SM, indolent SM (ISM) is the more frequent subtype. Adult patients with CM but without an extracutaneous biopsy are classified as having mastocytosis in the skin (MIS), a provisional diagnosis.
Julien Rossignol, Laurence Bouillet, Cristina Bulai‐Livideanu, Stéphane Barete, Julie Bruneau, Clément Gourguechon, Laura Polivka, Angèle Soria, Olivier Lortholary, Trevor Stanbury, Benoit Bouquillon, Cedric Sauvage, Rose Marie Javier, Olivier Hermine, Michel Arock, the CEREMAST Network   +15 more
wiley   +1 more source

Solitary mastocytoma presenting in an adult: report and literature review of adult-onset solitary cutaneous mastocytoma with recommendations for evaluation and treatment

Dermatology Practical & Conceptual, 2016
Background: Mastocytosis is either cutaneous (with skin-limited proliferation of mast cells) or systemic (with mast cells in extracutaneous sites). The onset of solitary mastocytoma in an adult is rare.
Philip R. Cohen
doaj   +1 more source

Diagnostic and therapeutic considerations in idiopathic hypereosinophilia with warm autoimmune hemolytic anemia. [PDF]

, 2015
Hypereosinophilic syndrome (HES) encompasses numerous diverse conditions resulting in peripheral hypereosinophilia that cannot be explained by hypersensitivity, infection, or atopy and that is not associated with known systemic diseases with specific ...
Brys, Adam K, Sheth, Milan R, Sohn, David D, Sweidan, Alexander J   +3 more
core   +1 more source

Italian pediatric experts' consensus statement on diagnosis and management of primary atopic disorders

Pediatric Allergy and Immunology, Volume 36, Issue 11, November 2025.
Abstract Background Primary Atopic Disorders (PAD) represent a recently recognized subset of inborn errors of immunity (IEI), characterized by severe atopy driven by genetic mutations leading to dysregulated type 2 immune responses, excessive mast cell activation, and hyper production of IgE.
Fabio Cardinale, Ivan Taietti, Mayla Sgrulletti, Lucia Pacillo, Viviana Moschese, Caterina Cancrini, Raffaele Badolato, Michele Miraglia del Giudice, Gian Luigi Marseglia, Elena Chiappini, Riccardo Castagnoli, Primary Atopic Disorders Working Group, on behalf of the Italian Society of Pediatric Allergy and Immunology (SIAIP), Salvatore Barberi, Anna Belloni Fortina, Roberto Berni Canani, Paolo Bottau, Carlo Caffarelli, Mauro Calvani, Antonella Cianferoni, Francesco Cinetto, Bianca Laura Cinicola, Emilia Cirillo, Francesca Conti, Laura Dotta, Marzia Duse, Silvia Federici, Alessandro Fiocchi, Elena Galli, Silvia Giliani, Giuliana Giardino, Cristiana Indolfi, Lucia Leonardi, Amelia Licari, Vassilios Lougaris, Sara Manti, Alberto Martelli, Domenico Minasi, Elio Novembre, Riccardo Papa, Claudio Pignata, Federica Pulvirenti, Maria Sangerardi, Annarosa Soresina, Mariangela Tosca, Alberto Giovanni Ugazio, Anna Maria Zicari   +46 more
wiley   +1 more source

A Perspective on the Use of NB-UVB Phototherapy vs. PUVA Photochemotherapy [PDF]

, 2018
Narrowband UVB (NB-UVB) phototherapy and psoralen-UVA (PUVA) photochemotherapy are widely used phototherapeutic modalities for a range of skin diseases.
Ahmad, Archier, Archier, Aslam, Atzmony, Aydogan, Behrens-Williams, Berroeta, Bhatnagar, Bhatnagar, Bilsland, Bilsland, Bishnoi, Boswell, Brazzelli, Bruynzeel, Calzavara-Pinton, Calzavara-Pinton, Cameron, Cameron, Carter, Chalmers, Chauhan, Chen, Clayton, Collins, Cunningham, Dawe, Dawe, Dawe, Dawe, De, Decock, Der-Petrossian, Diederen, El-Mofty, Engin, Farnaghi, Fernandez-Guarino, Foerster, Garritsen, George, Godt, Gordon, Grandi, Green, Grundmann-Kollmann, Halpern, Harrop, Healy, Hearn, Hindson, Hindson, Hofer, Holme, Hoot, Hudson-Peacock, Ibbotson, Ibbotson, Iraji, Karvonen, Kerscher, Khafagy, Knobler, Kolde, Larko, Lever, Lindelof, Ling, Man, Man, Man, Man, Markham, Mastalier, Mckenna, Menage, Messenger, Millington, Mobacken, Mohamed, Morgado-Carrasco, Murray, Norris, Olsen, Parrish, Pavlovsky, Radakovic, Robinson, Roelandts, Roelandts, Ros, Rosen, Rosen, Rosen, Salem, Sapam, Sevrain, Sezer, Sivaramakrishnan, Snellman, Solak, Stern, Stern, Stern, Stern, Stern, Stern, Tanew, Tanew, Taylor, Tegner, Tzaneva, Van, Van, Wackernagel, Warren, Westerhof, Yones, Yones   +119 more
core   +3 more sources

Next Generation Sequencing of Genes With Epigenetic Alterations in Mastocytosis

Clinical and Translational Allergy, Volume 15, Issue 10, October 2025.
ABSTRACT Aim Mastocytosis is a neoplastic disease of the bone marrow associated with the risk of frequent and severe allergic reactions. However, the genetic predisposition is not fully understood, and the crucial element in pathogenesis is the presence of the oncogenic KIT p. D816 V gene mutation.
Aleksandra Górska, Thierry van De Wetering, Marta Sobalska‐Kwapis, Bogusław Nedoszytko, Danuta Gutowska‐Owsiak, Marek Niedoszytko   +5 more
wiley   +1 more source

Childhood Pseudoxanthomatousmastocytosis; Report of two cases

Indian Journal of Dermatopathology and Diagnostic Dermatology, 2018
Cutaneous mastocytosis (CM) is a mast cell proliferative disorder that commonly affects pediatric population. It has various clinical forms such as urticaria pigmentosa, solitary mastocytoma, telangiectasia macularis eruptiva perstans, diffuse CM, and ...
Bhabani S. T. P. Singh, Tapaswini Tripathy, Bikash Ranjan Kar, Surabhi Singh   +3 more
doaj   +1 more source

Cutaneous Mastocytosis in Childhood. Retrospective Study of 32 Patients [PDF]

, 2012
Introdução: A designação de mastocitose engloba várias entidades clinicamente distintas caracterizadas pela acumulação tissular de mastócitos. A pele é o órgão mais frequentemente envolvido.
Amaro, C, Cardoso, J, Coelho Macias, V, Freitas, I, Vieira, R   +4 more
core  

Clinical Scoring of Cutaneous Mastocytosis

Acta Dermato-Venereologica, 2001
There are still many controversies in defining and evaluating mastocytosis. One of the aspects that is missing is a system for clinical evaluation of mastocytosis of the skin. A calculation based on a semi-quantitative analysis of three aspects of mastocytosis was designed. The method is called the scoring index of mastocytosis (SCORMA).
Heide, R., Middelkamp Hup, M. A., Mulder, P. G., Oranje, A. P.   +3 more
openaire   +3 more sources