Results 51 to 60 of about 5,000,249 (354)

The clinical spectrum of SMA‐PME and in vitro normalization of its cellular ceramide profile

Annals of Clinical and Translational Neurology, Volume 9, Issue 12, Page 1941-1952, December 2022., 2022
Abstract Objective The objectives of this study were to define the clinical and biochemical spectrum of spinal muscular atrophy with progressive myoclonic epilepsy (SMA‐PME) and to determine if aberrant cellular ceramide accumulation could be normalized by enzyme replacement.
Michelle M. Lee, Graeme S. V. McDowell, Darryl C. De Vivo, Daniel Friedman, Samuel F. Berkovic, Maria Spanou, Argirios Dinopoulos, Katheryn Grand, Pedro A. Sanchez‐Lara, Michelle Allen‐Sharpley, Jodi Warman‐Chardon, Alexander Solyom, Thierry Levade, Edward H. Schuchman, Steffany A. L. Bennett, David A. Dyment, Toni S. Pearson   +16 more
wiley   +1 more source

Evaluating time domain reflectometry and coaxial impedance sensors for soil observations by the U.S. Climate Reference Network

Vadose Zone Journal, 2020
The objective of this study was to evaluate the performance of two commercial‐grade electromagnetic sensors in measuring soil water content for the U.S. Climate Reference Network (USCRN). One sensor was a 50‐MHz coaxial impedance dielectric sensor (model
Timothy B. Wilson, Howard J. Diamond, John Kochendorfer, Tilden P. Meyers, Mark Hall, Nancy W. Casey, C. Bruce Baker, Ronald Leeper, Michael A. Palecki   +8 more
doaj   +1 more source

Brownian yet non-Gaussian diffusion: from superstatistics to subordination of diffusing diffusivities [PDF]

Phys. Rev. X 7, 021002 (2017), 2016
A growing number of biological, soft, and active matter systems are observed to exhibit normal diffusive dynamics with a linear growth of the mean squared displacement, yet with a non-Gaussian distribution of increments. Based on the Chubinsky-Slater idea of a diffusing diffusivity we here establish and analyze a minimal model framework of diffusion ...
arxiv   +1 more source

Brain magnetic resonance imaging predictors in anti‐N‐methyl‐D‐aspartate receptor encephalitis

Annals of Clinical and Translational Neurology, Volume 9, Issue 12, Page 1974-1984, December 2022., 2022
Abstract Objective Brain magnetic resonance imaging (MRI) findings in anti‐N‐methyl‐D‐aspartate receptor (NMDAR) encephalitis are nonspecific and rarely have obvious associations with clinical characteristics and outcomes. This study aimed to comprehensively describe the MRI features of patients with NMDAR encephalitis, examine their associations with ...
Ying‐Ying Zhao, Bing Han, Cui‐Hong Qin, Xue‐Xiu Shi, Wen‐Jing Yun, Meng Wang, Bo Yuan, Tong‐Wen Sun, Hai‐Xu Wang   +8 more
wiley   +1 more source

The effect of yeast-derived β-glucans in reducing the adverse outcome of Lawsonia intracellularis in finishing pigs

Frontiers in Animal Science, 2023
IntroductionChronic diarrhoea is one of the most recurrent health issues in pig herds. Among Q9 the causative agents of diarrhoea, Lawsonia intracellularis is quite frequent with worldwide distribution leading to detrimental economical losses, as a ...
Lamya Rhayat, Gaël Even, Gaël Even, Tadele G. Kiros, Géraldine Kuhn, Ségolène Lebrun-Ruer, Ségolène Lebrun-Ruer, Christophe Audebert, Christophe Audebert, Julie Schulthess   +9 more
doaj   +1 more source

Recognizing early MRI signs (or their absence) is crucial in diagnosing metachromatic leukodystrophy

Annals of Clinical and Translational Neurology, Volume 9, Issue 12, Page 1999-2009, December 2022., 2022
Abstract Objectives Metachromatic leukodystrophy (MLD) has characteristic white matter (WM) changes on brain MRI, which often trigger biochemical and genetic confirmation of the diagnosis. In early or pre‐symptomatic disease stages, these typical MRI changes might be absent, hampering early diagnosis.
Daphne H. Schoenmakers, Shanice Beerepoot, Ingeborg Krägeloh‐Mann, Saskia Elgün, Benjamin Bender, Marjo S. van der Knaap, Nicole I. Wolf, Samuel Groeschel   +7 more
wiley   +1 more source

BDHI: a French national database on historical floods

E3S Web of Conferences, 2016
The paper describes the various features of the BDHI database (objects, functions, content). This document database provides document sheets on historical floods from various sources: technical reports from water authorities, scientific accounts ...
Lang Michel, Coeur Denis, Audouard Alexandre, Villanova-Oliver Marlène, Pène Jean-Philippe   +4 more
doaj   +1 more source

Self-diffusion of polymers in cartilage as studied by pulsed field gradient NMR [PDF]

, 2002
Pulsed field gradient (PFG) nuclear magnetic resonance (NMR) was used to investigate the self-diffusion behaviour of polymers in cartilage. Polyethylene glycol and dextran with different molecular weights and in different concentrations were used as ...
Arnold, K., Kärger, J., Naji, L., Schiller, J., Stallmach, F., Trampel, R.   +5 more
core   +2 more sources

Properties of small molecular drug loading and diffusion in a fluorinated PEG hydrogel studied by ^1H molecular diffusion NMR and ^(19)F spin diffusion NMR [PDF]

, 2010
R_f-PEG (fluoroalkyl double-ended poly(ethylene glycol)) hydrogel is potentially useful as a drug delivery depot due to its advanced properties of sol–gel two-phase coexistence and low surface erosion.
A Abragam, A Prabhutendolkar, AM Weljie, B Balinov, B Jeong, B Xu, BC Joondeph, CH Klein-Douwel, CS Johnson Jr, CS Johnson Jr, DG Regan, EO Stejskal, EO Stejskal, Errol V. Mathias, EV Mathias, H Yu, HC Torrey, J Jenner, J Kríž, JE Tanner, JE Tanner, Julia A. Kornfield, Julia Aponte, KI Momot, MA Voda, ML Johns, MP Krafft, MS Blumenkranz, NG Kundu, O Söderman, O Söderman, P Cornillon, PS Belton, RJ Phillips, RK Gupta, RM Cotts, S Matsukawa, S Viel, T Garasanin, T Giyoong, T Giyoong, WS Price, X Liu, Y Liao, Y Yamane, Yong Ba   +45 more
core   +3 more sources

Natural Fibre-Reinforced Biofoams

International Journal of Polymer Science, 2011
Starches and polylactic acids (PLAs) represent the main biobased and biodegradable polymers with potential industrial availability in the next decades for “bio” foams applications.
Anne Bergeret, Jean Charles Benezet
doaj   +1 more source