Results 51 to 60 of about 6,668 (259)

Super‐Refractory Status Epilepticus (SRSE) in a Patient With Compound Heterozygous OPA1 Variants: Case Report and Literature Review

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Super‐Refractory Status Epilepticus (SRSE) is a rare, life‐threatening neurological emergency with unclear etiology in many cases. Mitochondrial dysfunction, often due to disease‐causing genetic variants, is increasingly recognized as a cause, with each gene producing distinct pathophysiological mechanisms.
Pouria Mohammadi, Lara Basovic, Christopher Michael McGraw   +2 more
wiley   +1 more source

Brainstem and Cerebellar Volume Loss and Associated Clinical Features in Progressive Supranuclear Palsy

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Introduction Progressive Supranuclear Palsy (PSP) is a neurodegenerative ‘tauopathy’ with predominating pathology in the basal ganglia and midbrain. Caudal tau spread frequently implicates the cerebellum; however, the pattern of atrophy remains equivocal.
Chloe Spiegel, Timothy P. Siejka, Cassandra Marotta, Josh J. Y. Lee, Kelly Bertram, Terence J. O'Brien, Meng Law, Lucy Vivash, Ian H. Harding   +8 more
wiley   +1 more source

The Effect of He on the Evolution of Radiation-Induced Dislocation Loops near W/Cu Interface

Metals
In the current work, the distribution behaviors of irradiation-induced dislocation loops near the W-Cu interface (contains a thin W2C transition layer) under self-interstitial atom diffusion-dominated conditions were investigated based on the comparative
Huaqing Sang, Yifan Zhang, Jing Wang
doaj   +1 more source

Early Clinical, Imaging, and Pathological Characteristics of SRPK3/TTN‐Digenic Myopathy

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective SRPK3/TTN‐digenic myopathy was recently established as a skeletal muscle myopathy caused by digenic inheritance. This study characterizes the early clinical presentation of SRPK3/TTN‐digenic myopathy in one previously reported and seven newly identified pediatric patients.
Rotem Orbach, Sandra Donkervoort, Carola Hedberg‐Oldfors, Giovanni Baranello, Dimah Saade, Precilla D'Souza, Ruchee Patel, Eva Michael, A. Reghan Foley, Diana Bharucha‐Goebel, S. Jin Haugland, Meghan McAnally, Omer Abdul Hamid, Katherine Chao, Ellen F. Macnamara, Alan H. Beggs, Anna Sarkozy, Juliane Mueller, Steven A. Moore, Richard S. Finkel, Cynthia J. Tifft, Francesco Muntoni, Anders Oldfors, Carsten G. Bönnemann   +23 more
wiley   +1 more source

Application of Improved PRD Algorithm Based on Burgers Vector Extraction and Analysis in Dislocation Loop Simulation

Yuanzineng kexue jishu, 2023
After neutron irradiation, RAFM steel will produce two types of interstitial dislocation loops (1/2〈111〉 loop and 〈100〉 loop), resulting in radiation hardening and embrittlement after long service.
XU Xincheng;NIE Ningming;WANG Jin;HE Xinfu;ZENG Yan;ZHANG Jilin;WANG Jue;WAN Jian
doaj  

Shearing dominated by the coupling of the interfacial misfit and atomic bonding at the FCC (111) semi-coherent interfaces

Materials & Design, 2020
Using atomistic simulations, we present a systematic investigation of the shear mechanisms of three {111} bimetal interfaces, focusing on the influence of the dislocation spacing and bonding scheme across the interface. The evolution of interface sliding
Hui Yang, Linggang Zhu, Ruifeng Zhang, Jian Zhou, Zhimei Sun   +4 more
doaj   +1 more source

Cracking the Code: Which Ocular Symptoms Predict Dry Eye Signs? Insights From a Large International Sicca Registry

Arthritis Care &Research, EarlyView.
Objective The study aimed to identify symptom‐based predictors of dry eye disease (DED) signs in the Sjögren's International Collaborative Clinical Alliance (SICCA) cohort. Methods We performed a retrospective analysis examining 16 ocular symptoms (most graded 0–4) and artificial tear (AT) use (graded 0–3) as predictors of DED signs (abnormal ocular ...
Pragnya R. Donthineni, Chloe Shields, Rohit Muralidhar, Shreya Bhatt, Alan Baer, Robert Fox, Sara S. McCoy, Anat Galor   +7 more
wiley   +1 more source

Molecular dynamics simulations of cascade overlap with Void/Helium bubble

Nuclear Materials and Energy, 2022
When tungsten (W) is used as a plasma-facing material in fusion reactors, it will suffer irradiation from the high-energy neutron and high-flux low-energy helium (He) plasma, affording voids and He bubbles with varying helium-to-vacancy ratios (He/V ...
Jiechao Cui, Qing Hou, Min Li, Mingjie Qiu   +3 more
doaj   +1 more source

Experimental Evaluation of 100Cr6 Steel Microindented Surfaces Under Lubricated Nonconformal Point Contacts

Advanced Engineering Materials, EarlyView.
The tribological behavior of 100Cr6 steel spheres textured via Vickers microindentation is evaluated under lubricated sliding by varying both dimple size and density. Fine and dense textures significantly reduce friction across all lubrication regimes, while large dimples increase it.
Farideh Davoodi, Pasquale Guglielmi, Gianfranco Palumbo, Giuseppe Carbone   +3 more
wiley   +1 more source

Trapping and de-trapping behavior of hydrogen isotopes in <100> interstitial dislocation loops of tungsten

Nuclear Fusion
In fusion reactors, plasma-facing materials (PFMs) work under a complex irradiation environment. A lot of irradiation defects will be generated in tungsten (W), primary candidate for PFMs, leading to a substantial amount of hydrogen fuel retention. Among
Fei Sun, Qihang Liu, Baichuan Xu, Xiao-Chun Li, Jipeng Zhu, Dahuan Zhu, Hai-Shan Zhou, Hongxiang Zong, Lai-Ma Luo, Yasuhisa Oya, Yucheng Wu   +10 more
doaj   +1 more source