Results 101 to 110 of about 64,509,941 (193)

Rare case of eosinophilic granulomatosis with polyangiitis in two patients with α-1-antitrypsin deficiency (PiSZ) [PDF]

, 2016
We present two cases of eosinophilic granulomatosis with polyangiitis occurring with α-1-antitrypsin deficiency, both PiSZ phenotype. The simultaneous occurrence of these two conditions has seldom been described in the literature, despite evidence of an ...
Moxey, Jordan Maureen, Low, Emma, Low, Emma Victoria, Moxey, Jordan, Turner, Alice, Turner, Alice Margaret   +5 more
core   +1 more source

Eosinophilic granulomatosis with polyangiitis across the eosinophilic spectrum: from molecular mechanisms to practical differential diagnosis and targeted therapy

Rheumatology
Introduction Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis defined by asthma, hypereosinophilia, and multiorgan involvement.
Aleksandra Hus, Małgorzata Wisłowska
doaj   +1 more source

ANCA-associated vasculitis in the United Arab Emirates: a 17-year case series with review from Gulf literature

Annals of Saudi Medicine
BACKGROUND: Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) is a rare and severe autoimmune disease characterized by pauci-immune necrotizing vasculitis.
Hala Shahrour, Neama Luqman, Fatima AlKindi, Mumtaz Khan, Shamma Ahmad Al Nokhatha   +4 more
doaj   +1 more source

Infectious complication or exacerbation of granulomatosis with polyangiitis?

, 2015
Granulomatosis with polyangiitis (GPA) is a primary, systemic small vessel vasculitis. The respiratory tract is typically involved in the course of the disease.
Małgorzata Struk-Panfill, Anna Masiak, Zbigniew Zdrojewski   +2 more
core   +1 more source

Pediatric antineutrophil cytoplasmic antibody-associated vasculitis: A review on pulmonary manifestations, management, and outcomes

Tungs’ Medical Journal
Antineutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a rare systemic autoimmune disorder characterized by necrotizing inflammation of blood vessels infiltrated by neutrophils.
Chien-Heng Lin, Chieh-Ho Chen, Wei-Ching Lin, Wen-Jue Soong, Syuan-Yu Hong   +4 more
doaj   +1 more source

Granulomatosis with polyangiitis: rapidly progressive necrotizing glomerulonephritis in a pediatric patient

, 2014
Mariana Luna,1 Victoria Bocanegra,3 Patricia G Vallés1,21Nephrology Division, Pediatric Department, Dr Humberto Notti Pediatric Hospital, Mendoza, Argentina; 2Pathophysiology Area, Pathology Department, School of Medicine, National Cuyo University,
Bocanegra V, Vallés PG, Luna M
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Genome-wide association study of eosinophilic granulomatosis with polyangiitis reveals genomic loci stratified by ANCA status

Nature Communications, 2019
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare inflammatory disorder characterised by asthma, eosinophilia and vasculitis. Here, the authors describe a genome-wide association study of EGPA that reveals clinical and genetic differences ...
Paul A Lyons, James E Peters, Federico Alberici, James Liley, Richard M. R. Coulson, William Astle, Chiara Baldini, Francesco Bonatti, Maria C Cid, Heather Elding, Giacomo Emmi, Jörg Epplen, Loïc Guillevin, David R. W. Jayne, Tao Jiang, Iva Gunnarsson, Peter Lamprecht, Stephen Leslie, Mark A. Little, Davide Martorana, Frank Moosig, Thomas Neumann, Sophie Ohlsson, Stefanie Quickert, Giuseppe A. Ramirez, Barbara Rewerska, Georg Schett, Renato A. Sinico, Wojciech Szczeklik, Vladimir Tesar, Damjan Vukcevic, The European Vasculitis Genetics Consortium, Benjamin Terrier, Richard A Watts, Augusto Vaglio, Julia U Holle, Chris Wallace, Kenneth G. C. Smith   +37 more
doaj   +1 more source

Concurrent CRAO with Arteritic AION in Eosinophilic Granulomatosis with Polyangiitis

, 2019
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare systemic necrotizing vasculitis characterized by peripheral neuropathy, pulmonary involvement, and eosinophilia. EGPA has been associated with a number of ocular conditions, including retinal
Anuchit Poonyathalang; Tanyatuth Padungkiatsagul; Kavin Vanikieti; Thitiporn Thongborisuth
core  

Head and Neck Manifestations of Eosinophilic Granulomatosis with Polyangiitis: A Systematic Review. [PDF]

, 2016
OBJECTIVE: To conduct the first and only systematic review of the existing literature on head and neck manifestations of eosinophilic granulomatosis with polyangiitis to guide clinical decision making for the otolaryngologist.
Basnyat, Shristi, Rosen, Marc R., Goldfarb, Jared M., Rabinowitz, Mindy R., Nyquist, Gurston G.   +4 more
core   +1 more source

Epidemiology of Vasculitides in Khorasan Province, Iran

Iranian Journal of Medical Sciences, 2015
Vasculitides are a heterogeneous group of more than 20 diseases defined by inflammation and destruction of blood vessels. We aimed to study the demographic characteristics of the primary vasculitides in the North East of Iran.
Mohammadhassan Jokar, Zahra Mirfeizi
doaj