Interstitial pneumonia with autoimmune features and undifferentiated connective tissue disease: Our interdisciplinary rheumatology-pneumology experience, and review of the literature [PDF]
, 2016 Background: Interstitial lung diseases (ILDs) are a heterogeneous group of disorders characterized by inflammation and/or fibrosis of the lungs, varying from idiopathic interstitial pneumonias to secondary variants, including the ILDs associated to ...
Cerri, Stefania +9 more
core +1 more source
Vasculitis of the upper airways1
Swiss Medical Weekly, 2012 Systemic vasculitides are rare and potentially life-threatening diseases. Granulomatosis with polyangiitis (GPA; formerly Wegener’s granulomatosis) and Churg Strauss syndrome (possibly to be renamed eosinophilic granulomatosis with polyangiitis ...
Christian Pagnoux, Nikolaus E Wolter
doaj +1 more source
A case of eosinophilic polyangiitis with granulomatosis that evolved to cardiac arrest due to advanced atrioventricular block [PDF]
, 2023 Cardiac manifestations are the major cause of mortality in patients with eosinophilic granulomatosis with polyangiitis (EGPA). Among these manifestations in EGPA patients, in the literature, there are fewer reports describing bradycardia in EGPA patients
Kaneko, Takeshi +9 more
core
Hypergammaglobulinemia in the pediatric population as a marker for underlying autoimmune disease: a retrospective cohort study [PDF]
, 2014 Background: The significance of hypergammaglobulinemia as a marker of immune activation is unknown, as a differential diagnosis for hypergammaglobulinemia in children has not been adequately established.
Lo, Mindy S +3 more
core +1 more source
Emerging concepts in the pathogenesis of antineutrophil cytoplasmic antibody-associated vasculitis. [PDF]
, 2015 PURPOSE OF REVIEW: Antineutrophil cytoplasmic antibodies (ANCAs) remain central to our current understanding of the pathogenesis of ANCA-associated vasculitis (AAV), and this review considers recent developments in the context of four key questions: are ...
Flint, Shaun M +2 more
core
Familial Eosinophilic Granulomatosis with Polyangiitis
Open Journal of Rheumatology and Autoimmune Diseases, 2017 Eosinophilic granulomatosis with polyangiitis (EGPA) is an uncommon ANCA associated vasculitic disorder characterized by systemic necrotizing vasculitis of small vessels occurring exclusively among patients with bronchial asthma and tissue eosinophilia. Familial EGPA is extremely rare. Only two case reports have been published so far.
Abdurhman S. Al Arfaj +4 more
openaire +2 more sources
Eosinophilic Granulomatosis with Polyangiitis: The Beginning of a New Era [PDF]
, 2019 Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare type of anti-neutrophil cytoplasm antibody-associated vasculitis (AAV) with unique features, such as involvement of eosinophils in the pathogenesis, which requires different therapies from ...
Blanco, Marta Corral +2 more
core +1 more source
Clinical Case ReportsThis case highlights the atypical presentation of eosinophilic granulomatosis with polyangiitis (EGPA) with neurological and cardiac complications, emphasizing the necessity of early recognition and aggressive treatment to prevent morbidity and mortality.
Mahshid Talebi‐Taher +3 more
doaj +1 more source
European Journal of Clinical InvestigationEosinophilic granulomatous polyangiitis (EGPA) is a rare autoimmune disease characterized by multisystemic inflammation, with eosinophils playing a central role in its pathogenesis.
Federico Spataro +4 more
semanticscholar +1 more source
Eosinophilic Granulomatosis With Polyangiitis [PDF]
Chest, 2020 Alvise Berti +6 more
openaire +2 more sources