Results 91 to 100 of about 10,140 (167)

ADAR1 Is Essential for Smooth Muscle Homeostasis and Vascular Integrity

Cells
Vascular smooth muscle cells (VSMCs) play a critical role in maintaining vascular integrity. VSMC dysfunction leads to numerous vascular diseases. Adenosine deaminases acting on RNA 1 (ADAR1), an RNA editing enzyme, has shown both RNA editing and non ...
Dunpeng Cai, Shi-You Chen
doaj   +1 more source

Acromicric dysplasia caused by a mutation of fibrillin 1 in a family: A case report. [PDF]

World J Clin Cases, 2023
Shen R, Feng JH, Yang SP.
europepmc   +1 more source

Fibrillin-1 mutation contributes to Marfan syndrome by inhibiting Cav1.2-mediated cell proliferation in vascular smooth muscle cells. [PDF]

Channels (Austin), 2023
Lin W, Xiong J, Jiang Y, Liu H, Bian J, Wang J, Shao Y, Ni B.   +7 more
europepmc   +1 more source

Nanoscale Structural Comparison of Fibrillin-1 Microfibrils Isolated from Marfan and Non-Marfan Syndrome Human Aorta. [PDF]

Int J Mol Sci, 2023
Șulea CM, Mártonfalvi Z, Csányi C, Haluszka D, Pólos M, Ágg B, Stengl R, Benke K, Szabolcs Z, Kellermayer MSZ.   +9 more
europepmc   +1 more source

Microenvironmental Regulation by Fibrillin-1

Microenvironmental Regulation by Fibrillin-1
Sengle G, Tsutsui K, Keene DR, Tufa SF, Carlson EJ, Charbonneau NL, et al. (2012) Microenvironmental Regulation by Fibrillin-1. PLoS Genet 8(1): e1002425. https://doi.org/10.1371/journal.pgen.1002425 Fibrillin-1 is a ubiquitous extracellular matrix molecule that sequesters latent growth factor complexes.
openaire  

Fibrillin-1 deficiency in the outer perichondrium causes longitudinal bone overgrowth in mice with Marfan syndrome. [PDF]

Hum Mol Genet, 2022
Sedes L, Wondimu E, Crockett B, Hansen J, Cantalupo A, Asano K, Iyengar R, Rifkin DB, Smaldone S, Ramirez F.   +9 more
europepmc   +1 more source

Fibrillin-1-regulated miR-122 has a critical role in thoracic aortic aneurysm formation. [PDF]

Cell Mol Life Sci, 2022
Zhang RM, Tiedemann K, Muthu ML, Dinesh NEH, Komarova S, Ramkhelawon B, Reinhardt DP.   +6 more
europepmc   +1 more source

Immunohistochemical expression of fibrillin-1 and fibrillin-2 during tooth development.

Immunohistochemical expression of fibrillin-1 and fibrillin-2 during tooth development.
BACKGROUND AND OBJECTIVE: Oxytalan fibers are categorized as a microfibril assembly without elastin deposition, and are unique components in the periodontal ligament (PDL). However, little is known about their formation during PDL development. To clarify the mechanisms of oxytalan fiber formation in developing PDL, we performed immunohistochemical ...
openaire  

Retraction: Fibrillin-1, induced by Aurora-A but inhibited by BRCA2, promotes ovarian cancer metastasis. [PDF]

Oncotarget
Wang Z, Liu Y, Lu L, Yang L, Yin S, Wang Y, Qi Z, Meng J, Zang R, Yang G.   +9 more
europepmc   +1 more source

New Studies of the Aberrant Alterations in Fibrillin-1 Methylation During Colorectal Cancer Development. [PDF]

Front Oncol, 2022
Lv L, Ma J, Wu L, Zhang C, Wang Y, Wang G.   +5 more
europepmc   +1 more source